Purpura-associated congenital lymphedema.
An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.
Berti
Samantha
S
Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24, 50132 Florence, Italy. bertis@masternet.it
Pieri
Alessandro
A
Lotti
Torello
T
Duranti
Alberto
A
Panelos
John
J
De Martino
Maurizio
M
Moretti
Silvia
S
D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007717:Knee / Q000473:pathology; D008209:Lymphedema / Q000150:complications* / Q000151:congenital* / Q000175:diagnosis / Q000628:therapy; D011693:Purpura / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D012501:Saphenous Vein / Q000473:pathology / Q000601:surgery; D017444:Skin Diseases, Papulosquamous / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D053828:Stockings, Compression; D013576:Syndactyly / Q000150:complications; D013577:Syndrome; D013848:Thigh / Q000473:pathology; D014034:Toes / Q000002:abnormalities; D016896:Treatment Outcome
D005938:Glucocorticoids