Dental management of a patient with factor X deficiency.
Factor X deficiency (also known as Stuart-Prower factor deficiency) is an extremely rare hereditary hematologic disorder, affecting 1 person in 2 million. The gene causing this condition is autosomal recessive; thus, only those inheriting from both parents exhibit clinical symptoms, such as moderate bleeding, easy bruising and subcutaneous bleeding from mucous membranes. Patients with marked deficiency may have severe posttraumatic or spontaneous internal or external bleeding, leading to such complications as hemarthrosis or hemorrhagic strokes. This case report describes the dental management of a patient with severe factor X deficiency whose development was delayed due to multiple episodes of intracranial hemorrhage in early childhood. It also highlights the importance of timely interdisciplinary communication and consultation to promote a successful outcome.
Adewumi
Abi
A
Department of Pediatric Dentistry, Health Science Centre, P.O. Box 100426, University of Florida, Gainesville, FL 32610, USA. aadewumi@dental.ufl.edu
Sakhalkar
Vishwas
V
D000293:Adolescent; D000768:Anesthesia, General; D017742:Dental Care for Chronically Ill; D005171:Factor X Deficiency / Q000150:complications*; D006801:Humans; D008297:Male; D010347:Patient Care Planning