title: Purpura-associated congenital lymphedema.
abstract: An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.
authors.affiliation: Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24, 50132 Florence, Italy. bertis@masternet.it
authors.forename: Samantha
authors.initials: S
authors.lastname: Berti
authors.forename: Alessandro
authors.initials: A
authors.lastname: Pieri
authors.forename: Torello
authors.initials: T
authors.lastname: Lotti
authors.forename: Alberto
authors.initials: A
authors.lastname: Duranti
authors.forename: John
authors.initials: J
authors.lastname: Panelos
authors.forename: Maurizio
authors.initials: M
authors.lastname: De Martino
authors.forename: Silvia
authors.initials: S
authors.lastname: Moretti
mesh_terms: D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007717:Knee / Q000473:pathology; D008209:Lymphedema / Q000150:complications* / Q000151:congenital* / Q000175:diagnosis / Q000628:therapy; D011693:Purpura / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D012501:Saphenous Vein / Q000473:pathology / Q000601:surgery; D017444:Skin Diseases, Papulosquamous / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D053828:Stockings, Compression; D013576:Syndactyly / Q000150:complications; D013577:Syndrome; D013848:Thigh / Q000473:pathology; D014034:Toes / Q000002:abnormalities; D016896:Treatment Outcome
chemical_list: D005938:Glucocorticoids