Exstrophy-epispadias complex associated with complete urethral duplication: preoperative diagnosis is a must.
We report a rare association of complete urethral duplication and exstrophy-epispadias complex in a totally incontinent boy. A voiding cystourethrography was performed and revealed a dorsal epispadiac urethra, a normal ventral urethra, and a good bladder capacity. Urethrocystoscopy showed a normal ventral urethra with verumontanum, normal bladder neck, and a large opening of the dorsal urethra. Dorsal urethral excision and bladder closure were enough to achieve complete continence because of the normal ventral urethra.
Zeidan
Smart
S
Department of Pediatric Surgery and Urology, AP-HP, Robert Debré University Hospital, University of Paris VII, Paris, France. smartzeidan@gmail.com
El-Ghoneimi
Alaa
A
D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000601:surgery; D001746:Bladder Exstrophy / Q000175:diagnosis* / Q000601:surgery; D004842:Epispadias / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011300:Preoperative Care; D014521:Urethra / Q000002:abnormalities* / Q000601:surgery