title: An atypical presentation of a blastic plasmacytoid dendritic cell tumors.
abstract: Blastic plasmacytoid dendritic cell tumor is a rare lymphoma, which has been included as an independent entity in the World Health Organization (WHO) 2008 classification for cutaneous lymphomas. This neoplasm usually affects middle-aged or elderly patients with predominant skin or soft tissues involvement. Although it usually has a good initial response to chemotherapy, relapses are the rule and they occur rapidly. We report a new case of an 81-year-old woman with a blastic plasmacytoid dendritic cell tumors with an unusual presentation.
authors.affiliation: Department of Dermatology, Hospital Clínico Universitario de Valencia, Valencia, Spain. veronical_c@hotmail.com
authors.forename: Verónica
authors.initials: V
authors.lastname: López
authors.forename: Nuria
authors.initials: N
authors.lastname: Martí
authors.forename: Antonio
authors.initials: A
authors.lastname: Ferrández
authors.forename: Jose María
authors.initials: JM
authors.lastname: Martin
authors.forename: Esperanza
authors.initials: E
authors.lastname: Jordá
mesh_terms: D000369:Aged, 80 and over; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D014408:Biomarkers, Tumor / Q000378:metabolism; D001707:Biopsy, Needle; D001854:Bone Marrow Cells / Q000378:metabolism / Q000473:pathology; D003520:Cyclophosphamide / Q000627:therapeutic use; D003713:Dendritic Cells / Q000378:metabolism / Q000473:pathology*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D008223:Lymphoma / Q000175:diagnosis* / Q000188:drug therapy / Q000378:metabolism; D011241:Prednisone / Q000627:therapeutic use; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000378:metabolism; D014750:Vincristine / Q000627:therapeutic use
chemical_list: D014408:Biomarkers, Tumor; D014750:Vincristine; D003520:Cyclophosphamide; D011241:Prednisone