Mayer-Rokitansky-Kuster-Hauser syndrome with H-type anovestibular fistula.
Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by Mullerian duct structures agenesis. Anorectal malformations are uncommonly associated with MRKH syndrome, and among them, rectovestibular fistula and cloacal malformations have been commonly described. H-type of anovestibular fistula associated with MRKH syndrome has not been reported previously. One such case along with its treatment is reported.
Mahajan
Jai Kumar
JK
Department of Pediatric Surgery, Advanced Pediatric Center, Postgraduate Institute of Medical Education and Research, Chandigarh 160012, India. jkmahajanjk@sify.com
Venkatesh
M A
MA
Bawa
Monika
M
Rao
Katargadda L N
KL
D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000601:surgery; D002648:Child; D005260:Female; D006801:Humans; D009095:Mullerian Ducts / Q000002:abnormalities*; D012003:Rectal Fistula / Q000175:diagnosis* / Q000601:surgery; D013577:Syndrome; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities*