title: Hearing evaluation in newborns with congenital aural malformation.
abstract: OBJECTIVE
  Over 5 years, 68,472 newborns were screened through a newly implemented universal newborn hearing screening program. In 15 cases, atresia of the external ear canal was found. The aim of this study was to estimate the hearing status of these newborns using transiently evoked otoacoustic emissions (TEOAEs) and auditory brainstem responses (ABRs).
  
  
  METHODS
  TEOAEs were performed during the first days after birth in the normal ears of all newborns. Diagnostic ABR audiometry was performed in 10 newborns.
  
  
  RESULTS
  Unilateral involvement occurred in all newborns studied. TEOAEs were present in all the contralateral ears. Normal ABRs were recorded from the healthy ear, whereas a conductive hearing loss, of approximately 50-60 dB, was found in the involved ear. In long-term follow-up, a satisfactory level of hearing, language, and speech development was found in 9 of the newborns; it was too early to come to definite conclusions in 4 newborns and 2 newborns were lost in follow-up.
  
  
  CONCLUSIONS
  In this study, all newborns with aural atresia had normal function in the contralateral ear. Yet, a comprehensive assessment of hearing is essential as early intervention is necessary in the rare case of bilateral hearing impairment.
authors: ENT Department of Athens National University, Hippokration Hospital, Athens, Greece.
authors: S G
authors: SG
authors: Korres
authors: D G
authors: DG
authors: Balatsouras
authors: C P
authors: CP
authors: Lyra
authors: G S
authors: GS
authors: Korres
authors: I
authors: I
authors: Kantas
authors: C E
authors: CE
authors: Papadakis
mesh_terms: D001300:Audiometry, Evoked Response; D016022:Case-Control Studies; D015331:Cohort Studies; D054644:Ear Auricle / Q000002:abnormalities*; D004432:Ear, Middle / Q000002:abnormalities*; D016057:Evoked Potentials, Auditory, Brain Stem; D005260:Female; D034381:Hearing Loss / Q000151:congenital / Q000175:diagnosis* / Q000453:epidemiology*; D006801:Humans; D007231:Infant, Newborn; D007804:Language Development; D008297:Male; D015997:Neonatal Screening; D017084:Otoacoustic Emissions, Spontaneous; D015995:Prevalence