[Malignant form of familial hypertrophic cardiomyopathy complicated with ventricular fibrillation in siblings. Electrocardiogram in hypertrophic cardiomyopathy - a review].
A family with hypertrophic cardiomyopathy (HCM) (15-year-old boy, his 17-year-old sister and 45-year-old father) is described. The first sign of HCM was cardiac arrest (CA) due to ventricular fibrillation (VF) in a boy. A few months later sister of proband had the episode of CA due to VF. Both had implanted cardioverter-defibrillator (ICD). Echocardiography revealed HCM in both cases and in a father, who also received prophylactic ICD. During 24-month follow-up fast VT was observed in sister of proband. We review electrocardiographic changes in HCM and their correlation with magnetic resonance.
Kukla
Piotr
P
Oddział Chorób Wewnetrznych, Szpital Specjalistyczny, Gorlice. kukla_piotr@poczta.onet.pl
Petkow-Dimitrow
Paweł
P
Jastrzebski
Marek
M
Bednarek
Jacek
J
Lelakowski
Jacek
J
Bryniarski
Leszek
L
D000293:Adolescent; D000368:Aged; D024741:Cardiomyopathy, Hypertrophic, Familial / Q000150:complications* / Q000175:diagnosis / Q000235:genetics / Q000628:therapy; D017147:Defibrillators, Implantable; D004562:Electrocardiography; D005260:Female; D006323:Heart Arrest / Q000175:diagnosis / Q000209:etiology* / Q000235:genetics / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D035781:Siblings; D014693:Ventricular Fibrillation / Q000175:diagnosis* / Q000209:etiology* / Q000235:genetics / Q000628:therapy