title: Bilateral implantation in children with cochleovestibular nerve hypoplasia.
abstract: To report on the outcomes of sequential bilateral cochlear implantation (CI) in children with inner ear malformation. The study design is a retrospective case study. The setting is a tertiary reference center. Two children presenting a profound bilateral congenital hearing loss with bilateral hypoplasia of the cochleovestibular nerves and hypoplasic external semicircular canal had a cochlear implant at respectively 16 months and 33 months. A second implant was proposed at respectively 17 and 20 months after the first implant. The main outcome measures are audiometry, perceptive results in closed and open set words (CSW and OSW) and oral production at follow-up. The first cochlear implant gave respectively mean thresholds at 60 dB and 70 dB. Bilateral CI showed mean threshold at respectively 40 dB and 55 dB. In case 1, perceptive assessment was 83% and 70% in respectively CSW and OSW with oral production and comprehension of sentences after 1 year follow-up. In case 2, the perceptive assessment showed no perceptive or linguistic evolution at 6 months follow-up. In cochleovestibular nerve hypoplasia, bilateral implantation could be discussed in cases of limited result after unilateral implant.
authors: ENT Department, Armand Trousseau Children's Hospital, 75012 Paris, France. n.oker@hotmail.fr
authors: N
authors: N
authors: Oker
authors: N
authors: N
authors: Loundon
authors: S
authors: S
authors: Marlin
authors: I
authors: I
authors: Rouillon
authors: N
authors: N
authors: Leboulanger
authors: E N
authors: EN
authors: Garabédian
mesh_terms: D001299:Audiometry / Q000379:methods; D019929:Cochlear Implantation / Q000379:methods*; D003054:Cochlear Implants; D000013:Congenital Abnormalities / Q000175:diagnosis / Q000601:surgery; D003638:Deafness / Q000151:congenital / Q000601:surgery; D005260:Female; D005500:Follow-Up Studies; D006319:Hearing Loss, Sensorineural / Q000151:congenital / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D018570:Risk Assessment; D012494:Sampling Studies; D013067:Speech Perception; D016896:Treatment Outcome; D000159:Vestibulocochlear Nerve / Q000002:abnormalities*