title: [Wegener granulomatosis - otologic, nasal, tracheobronchial and pulmonary involvement].
abstract: Wegener granulomatosis is a rare systemic idiopathic disease characterized by involvement of small vessels - medium and small arteries, venules, arterioles and ocasionally large arteries. This disease has predilection for the upper and lower respiratory tract and the kidney, with granulomatous inflamation and necrosis. Clinical manifestations and organ involvement of the disease vary widely. Early diagnosis and treatment may lead to a full recovery. Without treatment, Wegener's granulomatosis can be fatal. The authors present a case of a 33 year-old female, with severe disease, but with good outcome, after adequate diagnosis and treatment.
authors: Serviço de Pneumologia, Hospital de São João (EPE), Porto. sandrabugalho@iol.pt
authors: Sandra
authors: S
authors: Figueiredo
authors: Laurentino Mendes
authors: LM
authors: Leal
authors: António
authors: A
authors: Morais
authors: Adriana
authors: A
authors: Magalhães
authors: Teresa
authors: T
authors: Oliveira
authors: Venceslau
authors: V
authors: Hespanhol
authors: Carlos
authors: C
authors: Dias
authors: Gabriela
authors: G
authors: Fernandes
mesh_terms: D000328:Adult; D001982:Bronchial Diseases / Q000209:etiology; D004427:Ear Diseases / Q000209:etiology; D005260:Female; D014890:Granulomatosis with Polyangiitis / Q000150:complications*; D006801:Humans; D008171:Lung Diseases / Q000209:etiology; D009668:Nose Diseases / Q000209:etiology; D014133:Tracheal Diseases / Q000209:etiology