Multimodal treatment of primary extraskeletal Ewing's sarcoma of the chest wall: report of 2 cases.
Extraskeletal Ewing's sarcoma (EES) is a type of Ewing's sarcoma that arises in soft tissue and is now regarded as a member of a family of small round cell neoplasms of bone and soft tissue, including primitive neuroectodermal tumors (PNETs). EES occurs predominantly in adolescents and young adults between the ages of 10 and 30 years. The disease follows an aggressive course with a high recurrence rate. The presence of a distant metastasis is also common. EES arises in the soft tissue of either the trunk or extremities. We recently experienced two cases of EES that occurred in the chest wall. The two patients underwent wide resection and combined radiochemotherapy. There was no evidence of disease 30 and 22 months, respectively, after surgery. Although extremely rare, EES should be considered in the differential diagnosis of chest wall tumors. We report two cases of EES with a brief review of the literature.
Lee
Woo Surng
WS
Department of Thoracic and Cardiovascular Surgery, School of Medicine, Konkuk University Chungju Hospital, Chungju, Korea.
Kim
Yo Han
YH
Chee
Hyun Keun
HK
Hwang
Jae Joon
JJ
Kim
Jun Seok
JS
Lee
Song Am
SA
Hwang
Eun Gu
EG
Cho
Yo Han
YH
Chon
Gyu Rak
GR
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