title: Hepatobiliary scan in Alagille syndrome; arteriohepatic dysplasia.
abstract: Arteriohepatic dysplasia or congenital paucity of interlobular bile ducts - Alagille Syndrome, is a well defined syndrome characterized by five major features, including chronic cholestasis, posterior embryotoxon, butterfly-like vertebral arch defects, peripheral pulmonary artery hypoplasia or stenosis and facial dysmorphy. The disease is very rare. Only three cases have been reported in Greece and none with renal involvement. Hepatobiliary scan was a fundamental tool in the patients diagnosis and therefore we present the following case.
authors.affiliation: Nuclear Medicine Department, Medical School University of Alexandroupolis, Thrace, Greece. azissim@yahoo.gr
authors.forename: Athanassios
authors.initials: A
authors.lastname: Zissimopoulos
authors.forename: Dimitrios
authors.initials: D
authors.lastname: Cassimos
authors.forename: Savas
authors.initials: S
authors.lastname: Deftereos
authors.forename: Panos
authors.initials: P
authors.lastname: Prassopoulos
authors.forename: Ioannis
authors.initials: I
authors.lastname: Xinias
authors.forename: Christina
authors.initials: C
authors.lastname: Pavlidou
authors.forename: Antigone
authors.initials: A
authors.lastname: Mavroudi
authors.forename: Olga
authors.initials: O
authors.lastname: Vrani
authors.forename: Athanassios
authors.initials: A
authors.lastname: Chatzimichael
mesh_terms: D016738:Alagille Syndrome / Q000000981:diagnostic imaging* / Q000473:pathology*; D001659:Biliary Tract / Q000000981:diagnostic imaging* / Q000473:pathology*; D006801:Humans; D007223:Infant; D008099:Liver / Q000000981:diagnostic imaging* / Q000473:pathology*; D008297:Male; D011877:Radionuclide Imaging