Orbital compression syndrome in sickle cell crisis.
This article is about a 9-year-old boy with known homozygous sickle cell disease who developed unilateral exophthalmia and eyelid swelling during a sickle cell crisis. The symptoms were due to a vaso-occlusive event in the orbital bones,known as orbital compression syndrome, which is a rare complication of sickle cell disease.
Mueller
E B
EB
Klinikum Esslingen, Paediatric Hospital, Esslingen, Germany. e.mueller@klinikum-esslingen.de
Niethammer
K
K
Rees
D
D
Partsch
C J
CJ
D000755:Anemia, Sickle Cell / Q000175:diagnosis* / Q000628:therapy; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D001157:Arterial Occlusive Diseases / Q000175:diagnosis* / Q000628:therapy; D001803:Blood Transfusion; D002648:Child; D003937:Diagnosis, Differential; D004359:Drug Therapy, Combination; D004487:Edema / Q000175:diagnosis; D005094:Exophthalmos / Q000175:diagnosis* / Q000628:therapy; D005271:Femur Head Necrosis / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009915:Orbit / Q000098:blood supply / Q000473:pathology; D009916:Orbital Diseases / Q000175:diagnosis* / Q000628:therapy
D000900:Anti-Bacterial Agents