Biochemical efficacy of N-carbamylglutamate in neonatal severe hyperammonaemia due to propionic acidaemia.
Schwahn
Bernd C
BC
Pieterse
Louisa
L
Bisset
W Michael
WM
Galloway
Peter G
PG
Robinson
Peter H
PH
D000641:Ammonia / Q000097:blood; D004305:Dose-Response Relationship, Drug; D005260:Female; D005500:Follow-Up Studies; D005971:Glutamates / Q000008:administration & dosage / Q000627:therapeutic use*; D006801:Humans; D022124:Hyperammonemia / Q000097:blood / Q000209:etiology / Q000628:therapy*; D007231:Infant, Newborn; D056693:Propionic Acidemia / Q000097:blood / Q000150:complications* / Q000628:therapy; D006435:Renal Dialysis; D012720:Severity of Illness Index
D005971:Glutamates; C006895:N-carbamylglutamate; D000641:Ammonia
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