title: Primary primitive neuroectodermal tumor of the orbit.
abstract: Primitive neuroectodermal tumor (PNET) is a small round cell malignant tumor of neuroectodermal origin. Most of the PNETs occur in the central nervous system (CNS). PNETs recognized outside of CNS are diagnosed as peripheral PNET (pPNET). This tumor which expresses MIC-2 gene (CD99) seems to be least aggressive after complete tumor resection. We describe a rare case of PNET in a young girl.
authors.affiliation: Department of Ocular Pathology & Uveitis Services, Sri Sankaradeva Nethralaya, Beltola, Guwahati, Assam, India. dr_dasdipankar@yahoo.com
authors.forename: Dipankar
authors.initials: D
authors.lastname: Das
authors.forename: Ganesh Chandra
authors.initials: GC
authors.lastname: Kuri
authors.forename: Panna
authors.initials: P
authors.lastname: Deka
authors.forename: Kasturi
authors.initials: K
authors.lastname: Bhattacharjee
authors.forename: Harsha
authors.initials: H
authors.lastname: Bhattacharjee
authors.forename: Akshay C
authors.initials: AC
authors.lastname: Deka
mesh_terms: D001706:Biopsy; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis* / Q000601:surgery; D013508:Ophthalmologic Surgical Procedures / Q000379:methods; D009918:Orbital Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014057:Tomography, X-Ray Computed
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