title: Choledochal cyst associated with duodenal atresia: case report and review of the literature.
abstract: We report a rare case of choledochal cyst (CC) associated with congenital duodenal atresia (DA) and annular pancreas (AP). A girl was born at 37 weeks of gestation weighing 2,974 g with a prenatal diagnosis of DA. She underwent a duodenoduodenostomy for type III DA with an AP 1 day after birth. At 4 years of age, she was admitted for evaluation of cholangitis and pancreatitis. Radiological studies demonstrated a fusiform-type CC with pancreaticobiliary maljunction (PBMJ). Excision of the CC and hepaticojejunostomy were performed. The patient was discharged without complications. Despite the fact that CC, DA, and AP are embryologically closely related entities, to the best of our knowledge, only eight such cases have been documented. We must be aware of the possible combination of CC in the follow-up of the patients with DA associated with AP.
authors.affiliation: Division of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Hirakata, Osaka, Japan.
authors.forename: A
authors.initials: A
authors.lastname: Iwai
authors.forename: Yoshinori
authors.initials: Y
authors.lastname: Hamada
authors.forename: K
authors.initials: K
authors.lastname: Takada
authors.forename: N
authors.initials: N
authors.lastname: Inagaki
authors.forename: R
authors.initials: R
authors.lastname: Nakatake
authors.forename: H
authors.initials: H
authors.lastname: Yanai
authors.forename: H
authors.initials: H
authors.lastname: Miki
authors.forename: Y
authors.initials: Y
authors.lastname: Araki
authors.forename: M
authors.initials: M
authors.lastname: Sato
authors.forename: S
authors.initials: S
authors.lastname: Ono
authors.forename: N
authors.initials: N
authors.lastname: Iwai
authors.forename: A-Hon
authors.initials: AH
authors.lastname: Kwon
mesh_terms: D002675:Child, Preschool; D015529:Choledochal Cyst / Q000150:complications* / Q000175:diagnosis; D004386:Duodenum / Q000002:abnormalities*; D005260:Female; D006801:Humans; D007409:Intestinal Atresia / Q000150:complications* / Q000175:diagnosis
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