title: Perioperative management of a child with von Willebrand disease undergoing surgical repair of craniosynostosis: looking at unusual targets.
abstract: We report the successful management of a craniosynostosis repair in a child with severe Type I von Willebrand disease diagnosed during the preoperative assessment and treated by coagulation factor VIII and ristocetin cofactor. Collaboration among the anesthesiologist, the neurosurgeon, the clinical pathologist, and the pediatric hematologist is important for successful management.
authors.affiliation: University Department of Anesthesia and ICM, CHR Citadelle, Liege, Belgium.
authors.forename: Isabelle
authors.initials: I
authors.lastname: Maquoi
authors.forename: Vincent
authors.initials: V
authors.lastname: Bonhomme
authors.forename: Jacques Daniel
authors.initials: JD
authors.lastname: Born
authors.forename: Marie-Françoise
authors.initials: MF
authors.lastname: Dresse
authors.forename: Elisabeth
authors.initials: E
authors.lastname: Ronge-Collard
authors.forename: Jean-Marc
authors.initials: JM
authors.lastname: Minon
authors.forename: Pol
authors.initials: P
authors.lastname: Hans
mesh_terms: D000244:Adenosine Diphosphate / Q000378:metabolism; D000776:Anesthesiology / Q000379:methods; D003094:Collagen / Q000378:metabolism; D003398:Craniosynostoses / Q000150:complications* / Q000601:surgery*; D004837:Epinephrine / Q000378:metabolism; D006487:Hemostasis; D006801:Humans; D007223:Infant; D008297:Male; D011184:Postoperative Period; D013514:Surgical Procedures, Operative / Q000379:methods; D016896:Treatment Outcome; D014842:von Willebrand Diseases / Q000150:complications* / Q000628:therapy*
chemical_list: D000244:Adenosine Diphosphate; D003094:Collagen; D004837:Epinephrine