Primary primitive neuroectodermal tumor of the orbit.
Primitive neuroectodermal tumor (PNET) is a small round cell malignant tumor of neuroectodermal origin. Most of the PNETs occur in the central nervous system (CNS). PNETs recognized outside of CNS are diagnosed as peripheral PNET (pPNET). This tumor which expresses MIC-2 gene (CD99) seems to be least aggressive after complete tumor resection. We describe a rare case of PNET in a young girl.
Das
Dipankar
D
Department of Ocular Pathology & Uveitis Services, Sri Sankaradeva Nethralaya, Beltola, Guwahati, Assam, India. dr_dasdipankar@yahoo.com
Kuri
Ganesh Chandra
GC
Deka
Panna
P
Bhattacharjee
Kasturi
K
Bhattacharjee
Harsha
H
Deka
Akshay C
AC
D001706:Biopsy; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis* / Q000601:surgery; D013508:Ophthalmologic Surgical Procedures / Q000379:methods; D009918:Orbital Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014057:Tomography, X-Ray Computed
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