[Hereditary pigmentary hepatoses (functional hyperbilirubinemias)].
Reviewed in this paper are bilirubin metabolism, definition and classification of hereditary pigmentary hepatoses, their pathogenesis and forms of inheritance, clinical picture, laboratory, instrumental and differential diagnosis, morphological changes in the hepatic tissue, and therapeutic strategies.
Tsimmerman
Ia S
IaS
D006801:Humans; D006933:Hyperbilirubinemia, Hereditary / Q000175:diagnosis / Q000503:physiopathology / Q000628:therapy