title: Pulmonary hypertensive necrotizing arteritis: an unusual case of unilateral involvement in an infant with congenital heart disease.
abstract: Pulmonary hypertension is clinically defined as a pulmonary arterial pressure greater than 25 mmHg at rest or greater than 30 mmHg during exercise. We report a unique case of an infant with congenital heart disease causing pulmonary hypertension and necrotizing pulmonary arteritis but affecting only one lung. In conclusion, in pulmonary valve atresia, the lungs may be supplied via aortopulmonary collaterals. Necrotizing pulmonary arteritis is a severe lesion seen in irreversible pulmonary hypertension.
authors.affiliation: The Fingerland Department of Pathology, Charles University, Faculty of Medicine and Faculty Hospital, Hradec Králové, Czech Republic. steiner@lfhk.cuni.cz
authors.forename: Ivo
authors.initials: I
authors.lastname: Steiner
authors.forename: Viera
authors.initials: V
authors.lastname: Bolosová
authors.forename: Sona
authors.initials: S
authors.lastname: Fejtová
mesh_terms: D000015:Abnormalities, Multiple / Q000473:pathology; D002972:Cleft Palate; D005260:Female; D007839:Functional Laterality; D006330:Heart Defects, Congenital / Q000150:complications*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D007231:Infant, Newborn; D008168:Lung / Q000098:blood supply / Q000473:pathology*; D010488:Polyarteritis Nodosa / Q000209:etiology* / Q000473:pathology*