title: Acute adrenal crisis mimicking familial Mediterranean fever attack in a renal transplant FMF patient with amyloid goiter.
abstract: The most devastating complication of familial Mediterranean fever (FMF) is amyloidosis which is capable of resulting in chronic renal failure. Although amyloid deposits are frequent in adrenal glands based on the autopsies of FMF patients however; to our knowledge, symptomatic adrenal insufficiency has not been reported yet. We describe a 21-year-old-FMF amyloidosis case with a well-functioning allograft who presented to the emergency clinic with the complaints of abdominal pain, vomiting and diarrhea mimicking FMF attack. adrenocorticotrophic hormone stimulation test was performed due to resistant hyponatremia and disclosed Addison disease. In countries with a high prevalence of FMF, adrenal crisis should be borne in mind in long standing FMF patients.
authors.affiliation: Gazi University, Ankara, Turkey. hcemeksiz@gmail.com
authors.forename: Hamdi
authors.initials: H
authors.lastname: Emeksiz
authors.forename: Sevcan
authors.initials: S
authors.lastname: Bakkaloglu
authors.forename: Orhun
authors.initials: O
authors.lastname: Camurdan
authors.forename: Mehmet
authors.initials: M
authors.lastname: Boyraz
authors.forename: Oguz
authors.initials: O
authors.lastname: Soylemezoglu
authors.forename: Enver
authors.initials: E
authors.lastname: Hasanoglu
authors.forename: Necla
authors.initials: N
authors.lastname: Buyan
mesh_terms: D000208:Acute Disease; D000224:Addison Disease / Q000097:blood / Q000150:complications / Q000175:diagnosis*; D000309:Adrenal Insufficiency / Q000097:blood / Q000175:diagnosis* / Q000209:etiology; D000324:Adrenocorticotropic Hormone / Q000097:blood; D000682:Amyloid / Q000378:metabolism; D000686:Amyloidosis / Q000150:complications / Q000378:metabolism / Q000473:pathology*; D003937:Diagnosis, Differential; D010505:Familial Mediterranean Fever / Q000150:complications / Q000175:diagnosis* / Q000378:metabolism; D006042:Goiter / Q000150:complications / Q000378:metabolism / Q000473:pathology*; D006801:Humans; D007010:Hyponatremia / Q000150:complications / Q000378:metabolism / Q000473:pathology; D016030:Kidney Transplantation; D008297:Male; D055815:Young Adult
chemical_list: D000682:Amyloid; D000324:Adrenocorticotropic Hormone