Tracheal chondrosarcoma--a rare complication in Maffucci syndrome.
Maffucci syndrome is a rare congenital non-hereditary disease characterised by subcutaneous haemangiomata and multiple enchondromata. We present a case of an intermediate grade myxoid chondrosarcoma of the tracheal cartilage in a 34-year-old man with a history of Maffucci syndrome. Chondrosarcoma of the trachea are extremely rare tumours. A review of the radiological literature reveals approximately 15 previously published cases. No case was found with a history of Maffucci syndrome.
Wagnetz
U
U
Department of Medical Imaging, Toronto General Hospital, 200 Elizabeth Street, Toronto, Ontario M5G 2C4, Canada. Ute.Wagnetz@uhn.on.ca
Patsios
D
D
Darling
G
G
Las Heras
F
F
Hwang
D
D
D000328:Adult; D001859:Bone Neoplasms / Q000000981:diagnostic imaging* / Q000209:etiology / Q000473:pathology; D001999:Bronchoscopy; D002813:Chondrosarcoma / Q000000981:diagnostic imaging* / Q000209:etiology / Q000473:pathology; D003287:Contrast Media; D004687:Enchondromatosis / Q000150:complications*; D006801:Humans; D008297:Male; D036542:Tomography, Spiral Computed / Q000379:methods; D014134:Tracheal Neoplasms / Q000000981:diagnostic imaging* / Q000209:etiology / Q000473:pathology
D003287:Contrast Media