Congenitally unguarded tricuspid valve orifice with multiple other defects in a child with refractory heart failure.
Congenitally unguarded tricuspid valve orifice, a variant of tricuspid valve dysplasia, is a rare malformation with protean manifestations. This report describes a 5-year old child with refractory heart failure who, on echocardiography, was found to have unguarded tricuspid valve orifice with severe tricuspid regurgitation, pulmonary valve dysplasia with severe pulmonary regurgitation , cor triatriatum dexter , myxomatous mitral valve , perimembranous ventricular septal defect and a diverticulum of the right ventricular outflow tract. The management options for this child are discussed.
Mohan
Jagdish C
JC
Department of Cardiology, Ridge Heart Centre, Sunder Lal Jain Hospital, Ashok Vihar-III, Delhi, India. jcmohan@vsnl.com
Tomar
Deepak
D
Shekhar
Chandra
C
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D002675:Child, Preschool; D004452:Echocardiography; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis*; D006333:Heart Failure / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging*