title: [Surgical management of congenital heart defects in adolescent and adult patients, between years 2001-2008].
abstract: The leading interventions due to congenital heart defects performed in adults are: (I) reconstructive operations, including: (a) newly diagnosed malformations, (b) previously adjudged to be inoperable defects, (c) so called "tardive" interventions due to pulmonary hypertension or right ventricle insufficiency. There is a growing number of (II) REDO operations, including: (a) correction of residual defects, (b) replacement of damaged or outgrown homografts, (c) recoarctation (aneurysm, dissection) of the aorta after surgical or catheter interventions, (d) Ross procedure, valve replacements due to previously performed aortic valvulotomy/valvuloplasty or corrections of different malformations (e.g. TGA).
  
  
  RESULTS
  166 of all 4496 operations were performed in adolescents and adults (age: 16-52 years, mean: 28 years) between years 2001-2008. The distribution of these interventions: Ia: 77, Ib: 15, Ic: 4, IIa: 11, IIb: 22, IIc: 9, IId: 28. Mortality rates were the following: 0 intraoperative, 4 early postoperative, 1 pulmonary hypertensive crisis, 1 malignant rhythm disturbances, 2 multi-organ failure.
  
  
  CONCLUSIONS
  The main risk factors are pulmonary hypertension and right ventricle failure. Complex surgical solutions do not mean extreme problems for a congenital cardiac surgeon, but earlier diagnosis and the use of ECMO during therapy may improve the results.
authors.affiliation: Gottsegen György Országos Kardiológiai Intézet Budapest Haller u. 29. 1096.
authors.forename: István
authors.initials: I
authors.lastname: Hartyánszky
authors.forename: Andrea
authors.initials: A
authors.lastname: Székely
authors.forename: László
authors.initials: L
authors.lastname: Király
authors.forename: Zsolt
authors.initials: Z
authors.lastname: Prodán
authors.forename: Sándor
authors.initials: S
authors.lastname: Mihályi
authors.forename: Gábor
authors.initials: G
authors.lastname: Bodor
authors.forename: Csaba
authors.initials: C
authors.lastname: Tamás
authors.forename: Imre
authors.initials: I
authors.lastname: Kassai
authors.forename: Levente
authors.initials: L
authors.lastname: Fazakas
authors.forename: András
authors.initials: A
authors.lastname: Temesvári
authors.forename: András
authors.initials: A
authors.lastname: Szatmári
mesh_terms: D000293:Adolescent; D000328:Adult; D006348:Cardiac Surgical Procedures / Q000379:methods; D003310:Cor Triatriatum / Q000601:surgery; D015199:Extracorporeal Membrane Oxygenation; D005260:Female; D006330:Heart Defects, Congenital / Q000601:surgery*; D006349:Heart Valve Diseases / Q000601:surgery; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D006814:Hungary; D008297:Male; D008875:Middle Aged; D011666:Pulmonary Valve Stenosis / Q000601:surgery; D012086:Reoperation; D012720:Severity of Illness Index; D013771:Tetralogy of Fallot / Q000601:surgery; D014188:Transposition of Great Vessels / Q000601:surgery; D055815:Young Adult