Hereditary multiple exostoses of the hip.
OBJECTIVE
To assess the radiographic features of 36 hips with hereditary multiple exostoses (HME).


METHODS
Hip parameters of 12 males and 6 females (36 hips) aged 2 to 28 years with HME were assessed using anteroposterior radiographs. The recorded features included the sites of osteochondromas, the femoral head/neck ratio, the Reimer's migration percentage, Sharp's acetabular angle, the centre edge angle, the femoral neck-shaft angle, and degenerative changes.


RESULTS
15 of the 18 patients were asymptomatic; 3 complained of pain (2 underwent excision or bone biopsy); no lesion was malignant. Osteochondromas were most commonly located in the femur followed by the ilium; only one was intra-articular. 32 hips had coxa valga; 26 had an abnormal Reimer's migration percentage; 17 had an abnormal Sharp's acetabular angle; 12 had an abnormal centre edge angle; 32 had an abnormal femoral neck-shaft angle; and 6 had degenerative changes. Acetabular and femoral dysplasia as well as subluxation are common in patients with HME.


CONCLUSIONS
Borderline subluxated hips and those with marked coxa valga and/or acetabular dysplasia should be closely monitored to determine the need for surgery in the future. Subluxated hips should be operated on early, particularly in children and symptomatic adults.
El-Fiky
Tarek A M
TA
El-Hadra University Hospital, Alexandria, Egypt.
Chow
Wang
W
Li
Yun Hoi
YH
To
Michael
M
D000293:Adolescent; D000328:Adult; D001706:Biopsy; D001859:Bone Neoplasms / Q000151:congenital* / Q000000981:diagnostic imaging* / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D005097:Exostoses, Multiple Hereditary / Q000000981:diagnostic imaging* / Q000601:surgery; D005260:Female; D006618:Hip Dislocation, Congenital / Q000000981:diagnostic imaging* / Q000601:surgery; D006621:Hip Joint / Q000002:abnormalities* / Q000000981:diagnostic imaging* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D011859:Radiography