title: Primary pulmonary rhabdomyosarcoma in an adult with neurofibromatosis-1.
abstract: Rhabdomyosarcomas arising in various tissues associated with neurofibromatosis type 1 have been sporadically described in children and young adults. We report a unique case of primary pulmonary rhabdomyosarcoma in an adult with neurofibromatosis type 1. A right lower lobectomy was performed. The Intergroup Rhabdomyosarcoma Study IV postsurgical grouping classification was 1A. The patient is scheduled for chemotherapy without adjuvant radiation therapy as per standard pediatric protocol.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Dongguk University Hospital, Goyang, Korea.
authors.forename: Jae-Sung
authors.initials: JS
authors.lastname: Choi
authors.forename: Jong Sun
authors.initials: JS
authors.lastname: Choi
authors.forename: Eung-Joong
authors.initials: EJ
authors.lastname: Kim
mesh_terms: D000328:Adult; D001707:Biopsy, Needle; D003937:Diagnosis, Differential; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D011013:Pneumonectomy / Q000379:methods; D012208:Rhabdomyosarcoma / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D014057:Tomography, X-Ray Computed