Spontaneous hematomyelia in a child with hemophilia A: a case report.
Hemorrhagic complications in patients with hemophilia have been occasionally reported in the spinal column and the spinal cord. Treatment is based on prompt replacement therapy as the occurrence and development of neurologic dysfunction are related to the length of time between the onset of symptoms and the factor replacement. We report case of a 7-year-old hemophilic boy who presented with flaccid paraparesis resulting from thoracic hematomyelia. The patient showed gradual improvement on medical management with cryoprecipitate infusions. This case calls attention to the need for prompt diagnosis of rarely reported spinal hematomyelia based on clinical manifestations and radiologic features and highlights its management options in patients with hemophilia.
Aulakh
Roosy
R
Hemato-Oncology and Genetics Units, Department of Pediatrics, Advanced Pediatric Center, Post Graduate Institute of Medical Education and Research, Chandigarh, Punjab, India.
Panigrahi
Inusha
I
Naranje
Kirti
K
Sharda
Sheetal
S
Marwaha
Ram K
RK
D002648:Child; D005169:Factor VIII / Q000627:therapeutic use; D005340:Fibrinogen / Q000627:therapeutic use; D006395:Hemarthrosis; D006467:Hemophilia A / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D020758:Spinal Cord Vascular Diseases / Q000209:etiology*; D016896:Treatment Outcome
C026912:cryoprecipitate coagulum; D005169:Factor VIII; D005340:Fibrinogen