[Pedigree analysis and prosthodontic treatment of patients with dentinogenesis imperfecta type II].
OBJECTIVE
To study the heritable character and explore the prosthodontic treatment of opalescent dentin, also known as dentinogenesis imperfecta type II(DGI-II).


METHODS
Pedigree analysis was performed in the family members of patients with DGI-II found in Shanghai. The proband was treated with ceramometal restorations and investigated the treatment status of the DGI-II affected individuals in the family.


RESULTS
Five sequential generations with DGI-II were found in this family. The prevalence of later generation was approximately 50%. The rate of prosthodontic treatment was 90% nearly, including ceramometal restorations in the most of the patients and removable partial dentures in the others. The esthetic and mastication functions of the patients were good after treatment.


CONCLUSIONS
DGI-II showed a autosomal dominant pattern of inheritance. Ceramaometal restorations can prevent the affected teeth from abrasive and fracture, and also can help rehabilitate the esthetic and mastication functions of the teeth.
Gan
Hong
H
Department of Prosthodontics, Ninth People's Hospital, College of Stomatology, Shanghai Jiao Tong University School of Medicine, Shanghai Key Laboratory of Stomatology, Shanghai 200011, China. gan_honggh@126.com
Zhang
Xiu-yin
XY
Xu
Xiao-cen
XC
D002681:China; D003811:Dentinogenesis Imperfecta; D016326:Extracellular Matrix Proteins; D006801:Humans; D010375:Pedigree; D010750:Phosphoproteins; D011476:Prosthodontics
D016326:Extracellular Matrix Proteins; D010750:Phosphoproteins