title: Early infantile epileptic encephalopathy with unusual favourable outcome.
abstract: The authors report the case of an infant suffered from early infantile epileptic encephalopathy with suppression-burst, or Ohtahara syndrome, a severe form of epilepsy in early childhood. The patient was treated with vigabatrin causing a favourable response. This unusual outcome may be related with the normality of neuroimaging and metabolic studies, as happens with idiopathic West syndrome cases.
authors.affiliation: Neuropediatric Unit, Puerta de Hierro Majadahonda Hospital, Madrid, Spain. rcazorlac@hotmail.com
authors.forename: María Rosario
authors.initials: MR
authors.lastname: Cazorla
authors.forename: Alfonso
authors.initials: A
authors.lastname: Verdú
authors.forename: Carmen
authors.initials: C
authors.lastname: Montes
authors.forename: Fernando
authors.initials: F
authors.lastname: Ayuga
mesh_terms: D000927:Anticonvulsants / Q000627:therapeutic use*; D001927:Brain Diseases / Q000188:drug therapy / Q000503:physiopathology; D004569:Electroencephalography; D004827:Epilepsy / Q000188:drug therapy / Q000503:physiopathology; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D011247:Pregnancy; D013036:Spasms, Infantile / Q000503:physiopathology; D013577:Syndrome; D016896:Treatment Outcome; D020888:Vigabatrin / Q000627:therapeutic use*
chemical_list: D000927:Anticonvulsants; D020888:Vigabatrin