Aortopexy for tracheomalacia with dextrocardia, pulmonary artery sling, and congenital tracheal stenosis.
We report a rare case of coexisting pulmonary artery sling, congenital tracheal stenosis, and dextrocardia caused by right lung hypoplasia. Successful treatment of severe postoperative tracheomalacia was achieved by aortopexy, aiming displacement of the aortic arch across orthogonally in front of the trachea due to dextrocardia. The aim of this surgery was different from the usual aortopexy for tracheomalacia, which lifts the tracheal wall with the aorta. The three-dimensional evaluation considering the patient's associated malformations led to a successful result.
Lee
Kwang-Jong
KJ
Department of Surgery, Tokyo Metropolitan Kiyose Children's Hospital, Tokyo, Japan. kwangjong@xrh.biglobe.ne.jp
Kamagata
Shoichiro
S
Hirobe
Seiichi
S
Toma
Miki
M
Furukawa
Takuo
T
Fukushima
Naoki
N
Inomata
Yukihiro
Y
D000015:Abnormalities, Multiple; D001013:Aorta, Thoracic / Q000601:surgery*; D001999:Bronchoscopy; D003914:Dextrocardia / Q000175:diagnosis / Q000601:surgery*; D003937:Diagnosis, Differential; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D013902:Radiography, Thoracic; D014057:Tomography, X-Ray Computed; D014135:Tracheal Stenosis / Q000151:congenital / Q000175:diagnosis / Q000601:surgery*; D055090:Tracheomalacia / Q000175:diagnosis / Q000601:surgery*; D054079:Vascular Malformations / Q000175:diagnosis / Q000601:surgery*; D014656:Vascular Surgical Procedures / Q000379:methods*