Modified primary sutureless repair of total anomalous pulmonary venous connection in heterotaxy.
Early and late mortality remain high after palliative open heart surgery in low-weight neonates. In addition, the need for neonatal repair and the presence of pulmonary venous obstruction are risk factors for mortality in right isomerism. We describe a modified primary sutureless repair of infracardiac total anomalous pulmonary venous connection in a 1,600 g neonate with heterotaxy. Endarterectomy of intimal hyperplasia localized to the anastomotic site was required at bilateral bidirectional cavopulmonary connection 6 months after the initial repair. The patient underwent a successful fenestrated Fontan procedure using an extracardiac conduit at the age of 2 years.
Oshima
Yoshihiro
Y
Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan. ooshima_kch@hp.pref.hyogo.jp
Yoshida
Masahiro
M
Maruo
Ayako
A
Shimazu
Chikashi
C
Higuma
Tomonori
T
Inoue
Takeshi
T
D000015:Abnormalities, Multiple; D003937:Diagnosis, Differential; D015150:Echocardiography, Doppler; D005260:Female; D005500:Follow-Up Studies; D018729:Fontan Procedure / Q000379:methods*; D006801:Humans; D007231:Infant, Newborn; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery; D013536:Suture Techniques; D054079:Vascular Malformations / Q000175:diagnosis / Q000601:surgery*; D014781:Viscera / Q000002:abnormalities*