Primary pulmonary rhabdomyosarcoma in an adult with neurofibromatosis-1.
Rhabdomyosarcomas arising in various tissues associated with neurofibromatosis type 1 have been sporadically described in children and young adults. We report a unique case of primary pulmonary rhabdomyosarcoma in an adult with neurofibromatosis type 1. A right lower lobectomy was performed. The Intergroup Rhabdomyosarcoma Study IV postsurgical grouping classification was 1A. The patient is scheduled for chemotherapy without adjuvant radiation therapy as per standard pediatric protocol.
Choi
Jae-Sung
JS
Department of Thoracic and Cardiovascular Surgery, Dongguk University Hospital, Goyang, Korea.
Choi
Jong Sun
JS
Kim
Eung-Joong
EJ
D000328:Adult; D001707:Biopsy, Needle; D003937:Diagnosis, Differential; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D011013:Pneumonectomy / Q000379:methods; D012208:Rhabdomyosarcoma / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D014057:Tomography, X-Ray Computed