title: Klippel-Trénaunay syndrome: treatment of lower extremity pain with a spinal cord stimulator.
abstract: A young adult man with Klippel-Trénaunay syndrome presented to our pain management service with complaints of severe lower extremity neuropathic pain (pain scale 8 of 10 on the left and 4 of 10 on the right). The pain in his left leg was so severe that he wanted to undergo a left lower extremity amputation. The patient declined chronic use of narcotic medications for pain relief, believing that this would interfere with his educational and lifestyle pursuits. After a complete evaluation for possible sources of pain, we performed a trial placement of a spinal cord stimulator at the T9 level, which relieved his pain. We then placed a stimulator at the T10 level. At 1 year postimplantation, he was pain free (pain scale 1 of 10 bilaterally) and was able to function normally without narcotic support. We believe this to be the first use of a spinal cord stimulator for lower extremity pain resulting from Klippel-Trénaunay syndrome. We also discuss the clinical evaluation and treatment of a Klippel-Trénaunay syndrome patient with chronic pain.
authors.affiliation: Vascular and Vein Center, Grand Medical Center, Columbus, OH 43325, USA. RFranz2@ohiohealth.com
authors.forename: Randall W
authors.initials: RW
authors.lastname: Franz
authors.forename: Aleksey
authors.initials: A
authors.lastname: Prok
mesh_terms: D004599:Electric Stimulation Therapy / Q000295:instrumentation / Q000379:methods*; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000628:therapy*; D035002:Lower Extremity / Q000098:blood supply; D018810:Magnetic Resonance Angiography; D008297:Male; D010146:Pain / Q000209:etiology; D059408:Pain Management; D013116:Spinal Cord; D055815:Young Adult