Early infantile epileptic encephalopathy with unusual favourable outcome.
The authors report the case of an infant suffered from early infantile epileptic encephalopathy with suppression-burst, or Ohtahara syndrome, a severe form of epilepsy in early childhood. The patient was treated with vigabatrin causing a favourable response. This unusual outcome may be related with the normality of neuroimaging and metabolic studies, as happens with idiopathic West syndrome cases.
Cazorla
María Rosario
MR
Neuropediatric Unit, Puerta de Hierro Majadahonda Hospital, Madrid, Spain. rcazorlac@hotmail.com
Verdú
Alfonso
A
Montes
Carmen
C
Ayuga
Fernando
F
D000927:Anticonvulsants / Q000627:therapeutic use*; D001927:Brain Diseases / Q000188:drug therapy / Q000503:physiopathology; D004569:Electroencephalography; D004827:Epilepsy / Q000188:drug therapy / Q000503:physiopathology; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D011247:Pregnancy; D013036:Spasms, Infantile / Q000503:physiopathology; D013577:Syndrome; D016896:Treatment Outcome; D020888:Vigabatrin / Q000627:therapeutic use*
D000927:Anticonvulsants; D020888:Vigabatrin