Successful staged neonatal repair of tetralogy of Fallot with long-segment hypoplasia of the aorta.
We describe an extremely rare combination of tetralogy of Fallot (TOF), right-sided cervical aortic arch with long-segment hypoplasia, and other vascular anomalies. A two-stage surgical approach included aortic arch reconstruction followed by right ventricular muscle bundle division and ventricular septal defect closure a few weeks later. The initial clinical presentation, perioperative course, and imaging studies are presented along with a review of the relevant literature. This is the first report of successful neonatal repair of TOF with long-segment hypoplasia of the aorta.
Congenital Heart Center, University of Michigan, Ann Arbor, MI 48109-5204, USA. jimmyl@umich.edu
Jimmy C
JC
Lu
Sanket S
SS
Shah
Sonal T
ST
Owens
Adam L
AL
Dorfman
Ameeth
A
Vedre
Monica M
MM
Goble
Jennifer C
JC
Hirsch
John R
JR
Charpie
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D001017:Aortic Coarctation / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods; D004452:Echocardiography; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D013771:Tetralogy of Fallot / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D054079:Vascular Malformations / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*