Primary sarcoma of the right ventricle: surgical and adjuvant therapy.
We describe surgical and adjuvant therapeutic management of a right ventricular (RV) sarcoma and pulmonary artery occlusion. Echocardiographic evaluation of a 39-year-old man with exertional dyspnea revealed a tumor mass in the right ventricle, pulmonary trunk, and bilateral pulmonary arteries. The tumor was resected with concomitant pulmonary valvotomy, but the resection was incomplete. The RV outflow was reconstructed with an allograft patch, and a stentless valve was implanted for pulmonary valvular function. The pulmonary trunk and arteries were enlarged with allograft patches. The tumor was undifferentiated sarcoma and caused postoperative pulmonary artery restenosis. Radiotherapy improved pulmonary perfusion (reduction of RV pressure), but the patient died of brain metastasis. Undifferentiated cardiac sarcomas associated with pulmonary hypoperfusion should be resected even if incompletely, and radiation therapy could alleviate reduced pulmonary perfusion.
Yamamoto
Hiroshi
H
Department of Cardiovascular Surgery, Akita University School of Medicine, 1-1-1 Hondo, Akita, 010-8543, Japan.
Yamamoto
Fumio
F
Ishibashi
Kazuyuki
K
Matsukawa
Makoto
M
Liu
Ke-Xiang
KX
Hasegawa
Hitoshi
H
D000328:Adult; D001157:Arterial Occlusive Diseases / Q000209:etiology / Q000473:pathology / Q000601:surgery; D001706:Biopsy; D001932:Brain Neoplasms / Q000556:secondary; D006348:Cardiac Surgical Procedures; D003251:Constriction, Pathologic; D004417:Dyspnea / Q000209:etiology / Q000601:surgery; D015150:Echocardiography, Doppler; D017809:Fatal Outcome; D006338:Heart Neoplasms / Q000150:complications / Q000532:radiotherapy / Q000556:secondary / Q000601:surgery*; D019918:Heart Valve Prosthesis Implantation; D006352:Heart Ventricles / Q000601:surgery; D006801:Humans; D008297:Male; D011651:Pulmonary Artery / Q000473:pathology / Q000601:surgery; D011664:Pulmonary Valve / Q000601:surgery; D018714:Radiotherapy, Adjuvant; D012509:Sarcoma / Q000150:complications / Q000532:radiotherapy / Q000556:secondary / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome