title: Lessons from a case of osteopetrosis oxycephaly and Chiari type I malformation: a case report.
abstract: We report a child with osteopetrosis, oxycephaly and Chiari type I malformation who presented with raised intracranial pressure. During cranial expansion surgery the patient developed sudden cardiac arrest which we believe was probably related to the Chiari malformation. The case highlights a previously unrecognized association between osteopetrosis, craniosynostosis and a persistently open fontanelle at age 4 years. In addition it supports the existing literature in emphasizing the need for careful preoperative work up, choice of approach and operative technique in children with complex craniosynostosis and Chiari malformation.
authors.affiliation: University of Nottingham, Faculty of Medicine and Health Sciences, Medical School, Queen's Medical Centre, Nottingham NG7 2UH, UK. mzyyaaj@nottingham.ac.uk
authors.forename: Aimun Ab
authors.initials: AA
authors.lastname: Jamjoom
authors.forename: Bakur A
authors.initials: BA
authors.lastname: Jamjoom
authors.forename: Abrar R
authors.initials: AR
authors.lastname: Waliuddin
authors.forename: Abdulhakim B
authors.initials: AB
authors.lastname: Jamjoom