title: [Pulmonary lymphangiomatosis revealed by an interstitial syndrome in a young adult].
abstract: BACKGROUND
  Diffuse pulmonary lymphangiomatosis is an extremely rare congenital lesion affecting the lymphatic pulmonary system. It is carcterized by a multifocal proliferation and a pulmonary lymphatic vessels dilatation. It is essentially observed in newborns and infants. The diagnosis is based on histological findings.
  
  
  OBJECTIVE
  The purpose of this article is to describe the main clinical and pathological features of this rare entity difficult to diagnose.
  
  
  METHODS
  We report a case of a 19-year old girl who presented with a 2-month standing dyspnea. Radiographic findings consisted in a soft tissue infiltration and thickening in the two lobes. Based on histological and immunohistochemical findings, the diagnosis of diffuse pulmonary lymphangiomatosis was retained.
  
  
  CONCLUSIONS
  Diffuse pulmonary lymphangiomatosis is a difficult diagnosis which can be confused with lymphangioleiomyomatosis. Its worse prognosis could be improved by an early diagnosis enabling the use of interferon alpha 2B at the proper time.
authors.affiliation: Service d'Anatomie Pathologique, Hôpital A. Mami de L'Ariana, Tunisie.
authors.forename: Aïda
authors.initials: A
authors.lastname: Ayadi-Kaddour
authors.forename: Jouda
authors.initials: J
authors.lastname: Cherif
authors.forename: Mona
authors.initials: M
authors.lastname: Mlika
authors.forename: Maged
authors.initials: M
authors.lastname: Béji
authors.forename: Faouzi
authors.initials: F
authors.lastname: El Mezni
mesh_terms: D000328:Adult; D004417:Dyspnea / Q000209:etiology*; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis*; D008202:Lymphangioma / Q000175:diagnosis*