Imaging findings of chronic subluxation of the os odontoideum and cervical myelopathy in a child with Beare-Stevenson cutis gyrata syndrome after surgery to the head and neck.
BACKGROUND
Although uncommon, fractures of the os odontoideum are known to occur in children under 7 years old, following acute trauma.


METHODS
We report a case of chronic subluxation of the os odontoideum resulting in cervical myelopathy in a child with Beare-Stevenson cutis gyrata syndrome after surgery to the head and neck.


RESULTS
The patient was initially put in a Halo vest, following which occipital cervical fusion was performed.


CONCLUSIONS
Subluxations and fractures at the odontoid synchondrosis are rare but should be anticipated in young children with risk factors for instability of the cervical spine.
Too
Chow Wei
CW
Department of Diagnostic Imaging, KK Women's and Children's Hospital, Singapore.
Tang
Phua Hwee
PH
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000052:Acanthosis Nigricans / Q000151:congenital; D002574:Cervical Vertebrae / Q000000981:diagnostic imaging; D002648:Child; D019465:Craniofacial Abnormalities / Q000000981:diagnostic imaging*; D005260:Female; D050723:Fractures, Bone / Q000601:surgery; D006801:Humans; D009333:Neck / Q000601:surgery; D009777:Occipital Bone / Q000601:surgery; D009809:Odontoid Process / Q000000981:diagnostic imaging / Q000473:pathology*; D012868:Skin Abnormalities / Q000000981:diagnostic imaging*; D013514:Surgical Procedures, Operative; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D014609:Uvula / Q000002:abnormalities