Unilateral ovarian dermoid cyst accompanied by an ipsilateral paratubal cyst in a girl with Proteus Syndrome discovered by laparoscopic surgery.
BACKGROUND
Proteus syndrome is a rare hamartomatous disorder characterized by the overgrowth of multiple tissues in a mosaic pattern. Tumors of genitourinary tract in Proteus syndrome are uncommon.


METHODS
We here report a 5-year-old girl with Proteus syndrome who developed a cystic mass in the pelvic cavity. The cyst was discovered by ultrasonographic examination and finally proved to be a unilateral ovarian dermoid cyst accompanied by an ipsilateral paratubal cyst by laparoscopic surgery.


CONCLUSIONS
Proteus syndrome accompanied by an ovarian cyst is rare in girls. The possibilities of underlying ovarian cyst required for surgical intervention should be considered in Proteus syndrome.
Hong
Jin Hwa
JH
Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul 152-703, Korea.
Lee
Jae Kwan
JK
Song
Seung Hun
SH
Hwang
Jong Ha
JH
So
Kyung A
KA
Shin
Bong Kyung
BK
Lee
Nak Woo
NW
Lee
Kyu Wan
KW
D002675:Child, Preschool; D003884:Dermoid Cyst / Q000150:complications* / Q000473:pathology / Q000601:surgery; D005260:Female; D006801:Humans; D033162:Incidental Findings; D010535:Laparoscopy; D010048:Ovarian Cysts / Q000150:complications* / Q000473:pathology / Q000601:surgery; D010310:Parovarian Cyst / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D016715:Proteus Syndrome / Q000150:complications; D013724:Teratoma / Q000150:complications* / Q000473:pathology / Q000601:surgery