Valve-sparing replacement of the aortic root for a 2-year-old child with Loeys-Dietz syndrome.
Loeys-Dietz syndrome is a newly recognized constellation that presents with aortic aneurysm or dissection similar to Marfan's syndrome. We describe successful surgical treatment in a 2-year-old with the syndrome in whom we performed a valve-sparing replacement of the aortic root because of significant dilation of the aortic root and the ascending aorta.
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, USA.
Yoshio
Y
Ootaki
Minhaz
M
Uddin
Ross M
RM
Ungerleider
D001013:Aorta, Thoracic / Q000000981:diagnostic imaging / Q000601:surgery*; D017545:Aortic Aneurysm, Thoracic / Q000000981:diagnostic imaging / Q000601:surgery*; D001021:Aortic Valve / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods*; D002675:Child, Preschool; D005500:Follow-Up Studies; D006801:Humans; D055947:Loeys-Dietz Syndrome / Q000000981:diagnostic imaging / Q000601:surgery*; D008297:Male; D016343:Monitoring, Intraoperative / Q000379:methods; D011856:Radiographic Image Enhancement; D018570:Risk Assessment; D014057:Tomography, X-Ray Computed / Q000379:methods; D016896:Treatment Outcome; D018608:Ultrasonography, Doppler; D014656:Vascular Surgical Procedures / Q000379:methods