Valve-sparing replacement of the aortic root for a 2-year-old child with Loeys-Dietz syndrome.
Loeys-Dietz syndrome is a newly recognized constellation that presents with aortic aneurysm or dissection similar to Marfan's syndrome. We describe successful surgical treatment in a 2-year-old with the syndrome in whom we performed a valve-sparing replacement of the aortic root because of significant dilation of the aortic root and the ascending aorta.
Ootaki
Yoshio
Y
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, USA.
Uddin
Minhaz
M
Ungerleider
Ross M
RM
D001013:Aorta, Thoracic / Q000000981:diagnostic imaging / Q000601:surgery*; D017545:Aortic Aneurysm, Thoracic / Q000000981:diagnostic imaging / Q000601:surgery*; D001021:Aortic Valve / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods*; D002675:Child, Preschool; D005500:Follow-Up Studies; D006801:Humans; D055947:Loeys-Dietz Syndrome / Q000000981:diagnostic imaging / Q000601:surgery*; D008297:Male; D016343:Monitoring, Intraoperative / Q000379:methods; D011856:Radiographic Image Enhancement; D018570:Risk Assessment; D014057:Tomography, X-Ray Computed / Q000379:methods; D016896:Treatment Outcome; D018608:Ultrasonography, Doppler; D014656:Vascular Surgical Procedures / Q000379:methods