Clinical improvement after banding of a pulmonary branch artery in a symptomatic patient with Osler-Rendu-Weber syndrome.
We report a symptomatic newborn with Osler-Rendu-Weber syndrome, multiple and diffuse pulmonary arteriovenous malformations, and right-to-left shunting in the left lung. Right-to-left shunting was significantly decreased by selectively banding the left pulmonary branch artery and clipping one large feeding vessel so that total resection of the left lung could be avoided.
Department of Pediatric Cardiology and Congenital Heart Disease, Deutsches Herzzentrum München, Technische Universität München, Munich, Germany. ruf-bettina@t-online.de
Bettina
B
Ruf
Andreas
A
Eicken
Christian
C
Schreiber
John
J
Hess
D001165:Arteriovenous Malformations / Q000000981:diagnostic imaging / Q000601:surgery*; D017023:Coronary Angiography; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000601:surgery*