Case series: Treatment considerations in x-linked hypohidrotic ectodermal dysplasia.
OBJECTIVE
To describe our treatment considerations obtained from the dental care of several boys affected with X-linked hypohidrotic ectodermal dysplasia (HED) and to discuss the different problems that may arise in connection with these kinds of treatments.


METHODS
The subject group included 10 males affected with X-linked HED, treated at the department of Paediatric Dentistry and Clinical Genetics, Copenhagen School of Dentistry. All patients were treated, after a period of adaptation, with removable prostheses and whenever necessary, composite restoration of the conical crown morphology of the maxillary incisors. Furthermore, some of the patients received an orthodontic treatment for closure/reduction of the medial diastema.


RESULTS
The mean number of appointments at the department was 32 with a range from 7 to 59 appointments. In 7 out of 10 patients, the treatment was a success according to the patient, parents and dentist. In 3 out of 10 patients the treatment was not a success from the dentist's point of view: primarily due to lack of cooperation between the patient, parents and dentist. In half of the patients the deviated maxillary incisors morphology was restored and 5 out of 10 patients received orthodontic treatment for closure of the medial diastema in the maxilla.


CONCLUSIONS
It is of utmost importance to take the motivation of the patient and parents as well as the patient's acceptance for dental treatment into consideration. Furthermore, the treatment is rather time-consuming and should involve different areas of specialisation. Finally it is vital to remember that the parents may also have undergone a prolonged dental treatment, which might reduce their patience regarding their children's treatments.
Department of Paediatric Dentistry and Clinical Genetics, School of Dentistry, University of Copenhagen, Norre Alle 20, 2200 Copenhagen N, Denmark. mol@odont.ku.dk
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D000848:Anodontia / Q000628:therapy; D001071:Appointments and Schedules; D002648:Child; D002675:Child, Preschool; D003188:Composite Resins; D017742:Dental Care for Chronically Ill; D017266:Dental Prosthesis; D003793:Dental Restoration, Permanent; D003970:Diastema / Q000628:therapy; D053358:Ectodermal Dysplasia 1, Anhidrotic / Q000150:complications; D004955:Esthetics, Dental; D006801:Humans; D007180:Incisor / Q000002:abnormalities; D007223:Infant; D008297:Male; D009042:Motivation; D009971:Orthodontics, Corrective; D010290:Parents; D010347:Patient Care Planning; D010349:Patient Compliance; D017060:Patient Satisfaction; D011368:Professional-Family Relations; D014071:Tooth Abnormalities / Q000628:therapy*; D014094:Tooth, Deciduous / Q000002:abnormalities; D016896:Treatment Outcome
D003188:Composite Resins