Rectal bleeding in Klippel-Trénaunay syndrome: treatment with laparoscopic ultralow anterior resection with intersphincteric dissection.
Klippel-Trénaunay syndrome is a rare congenital vascular disorder characterized by varicose veins, hypertrophy of the soft tissues and bones, and hemangiomas. Although colorectal angiomatosis is uncommon, this association can lead to life-threatening complications because of acute or chronic bleeding. We report a patient with Klippel-Trénaunay syndrome who presented with transfusion-dependent anemia secondary to chronic rectal bleeding. Endoscopy and image studies revealed venous angiomata involving the rectum and distal sigmoid colon. We performed a laparoscopic ultralow anterior resection with intersphincteric dissection, obtaining good results. After a follow-up of 20 months the patient did not present hematochezia and maintained fecal continence.
Rotholtz
Nicolas
N
Hospital Alemán de Buenos Aires, Argentina.
Bun
Maximiliano E
ME
Laporte
Mariano
M
Sandra
Lencinas
L
Carlos
Peczan
P
Mezzadri
Norberto
N
D000328:Adult; D001003:Anal Canal / Q000473:pathology / Q000601:surgery; D000714:Anastomosis, Surgical / Q000379:methods; D003113:Colonoscopy / Q000379:methods*; D006471:Gastrointestinal Hemorrhage / Q000209:etiology* / Q000601:surgery; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D010535:Laparoscopy / Q000379:methods*; D008297:Male; D011351:Proctoscopy / Q000379:methods*; D012002:Rectal Diseases / Q000209:etiology* / Q000601:surgery; D012007:Rectum / Q000473:pathology / Q000601:surgery; D012307:Risk Factors