Double lumbosacral lipomas of the dorsal and filar types associated with OEIS complex: case report.
A female baby was born at 37 weeks and 6 days gestation by vaginal delivery with omphalocele, exstrophy of the cloaca, and imperforate anus, indicating the presence of OEIS complex, a rare combination of defects consisting of omphalocele (O), exstrophy of the cloaca (E), imperforate anus (I), and spinal deformity (S), associated with lumbosacral lipoma. The most common associated spinal deformity is terminal myelocystocele, and spinal lipoma is rare. Constructive interference in steady-state magnetic resonance imaging clearly revealed double lipomas, a dorsal-type lipoma, located dorsal to the low-lying conus medullaris, and a filar-type lipoma, revealed by a thickened and fatty filum terminale. After recovery from abdominogenital repairs, debulking of the dorsal-type lipoma and untethering of the spinal cord by sectioning of the filar-type lipoma were performed at the age of 14 months. Neurosurgical treatment for occult spinal dysraphism should be undertaken after recovery from the initial series of major abdominogenital procedures.
Department of Neurosurgery, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan. tokunaga_so@yahoo.co.jp
So
S
Tokunaga
Takato
T
Morioka
Kimiaki
K
Hashiguchi
Kazuhiro
K
Samura
Fumiaki
F
Yoshida
Yasushi
Y
Miyagi
Takashi
T
Yoshiura
Takeshi
T
Yamanouchi
Tomio
T
Sasaki
D001006:Anus, Imperforate / Q000150:complications; D001746:Bladder Exstrophy / Q000150:complications; D002420:Cauda Equina / Q000002:abnormalities / Q000601:surgery; D002988:Cloaca / Q000002:abnormalities; D005260:Female; D006801:Humans; D007223:Infant; D007796:Laminectomy; D008067:Lipoma / Q000150:complications* / Q000473:pathology / Q000601:surgery*; D008159:Lumbar Vertebrae / Q000002:abnormalities / Q000601:surgery; D008279:Magnetic Resonance Imaging; D019651:Plastic Surgery Procedures; D012447:Sacrum / Q000002:abnormalities / Q000601:surgery; D013116:Spinal Cord / Q000002:abnormalities / Q000601:surgery; D013117:Spinal Cord Compression / Q000150:complications / Q000473:pathology / Q000601:surgery; D016135:Spinal Dysraphism / Q000150:complications* / Q000473:pathology / Q000601:surgery*; D013125:Spinal Neoplasms / Q000150:complications* / Q000473:pathology / Q000601:surgery*; D013577:Syndrome; D016896:Treatment Outcome