Unilateral optic atrophy preceding Coats disease in a girl with Parry-Romberg syndrome.
OBJECTIVE
Parry-Romberg syndrome (PRS) is a rare disease of unknown etiology and pathogenesis, characterized by progressive hemifacial atrophy. Diverse ocular manifestations were reported in association with PRS, including enophthalmos, lid retraction, blepharoptosis, restrictive strabismus, ocular motor nerve dysfunction, Horner syndrome, reduced corneal sensitivity, band keratopathy, episcleritis, uveitis, neuroretinitis, and retinal vasculitis.


METHODS
Descriptive case report.


RESULTS
We report on the development of unilateral optic atrophy followed by ipsilateral Coats disease exudation and shallow retinal detachment in the posterior pole and inferior retina.


CONCLUSIONS
Optic atrophy was not previously described in association with PRS. We describe the development of unilateral optic atrophy with subsequent CD, 5 years later , in a girl with PRS.
Nasser
Orwa
O
Department of Ophthamology, Hadassah University Hospital, Jerusalem, Israel.
Greiner
Kathrin
K
Amer
Radgonde
R
D000293:Adolescent; D005122:Exudates and Transudates; D005150:Facial Hemiatrophy / Q000150:complications*; D005260:Female; D006801:Humans; D009896:Optic Atrophy / Q000209:etiology*; D012173:Retinitis / Q000175:diagnosis / Q000209:etiology*