Primary intestinal lymphangiectasia.
Primary intestinal lymphangiectasia (PIL) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites, and protein losing enteropathy. We report a series of 4 children from Chennai, India presenting with anasarca, recurrent diarrhea, hypoproteinemia and confirmatory features of PIL on endoscopy and histopathology.
Suresh
N
N
Departments of Pediatrics and Gastroenterology, Kanchi Kamakoti CHILDS Trust Hospital, Nungambakkam, Chennai, Tamil Nadu, India. drsuresh30@rediffmail.com
Ganesh
R
R
Sankar
Janani
J
Sathiyasekaran
Malathi
M
D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D007421:Intestine, Small / Q000473:pathology; D008201:Lymphangiectasis, Intestinal / Q000473:pathology* / Q000628:therapy; D008297:Male