[Sjögren-associated MALT-type lymphoma of labial salivary glands: rare constellation with amyloidosis and IgM-paraproteinemia].
We report a complex and rare combination of clinical and histological findings in a 59-year-old female patient: severe sicca-syndrome due to M. Sjögren, marginal zone B-cell lymphoma (MALT-type) in labial salivary glands with localized amyloid deposition, IgM-paraproteinemia, and Bence-Jones proteinuria. The causal association of these findings could only be elucidated by intense interdisciplinary correlation of all findings.
Flaig
M J
MJ
Klinik und Poliklinik für Dermatologie und Allergologie, Klinikum Innenstadt, Ludwig-Maximilians-Universität München, Frauenlobstr 9-11, 80337 München. Michael.Flaig@med.uni-muenchen.de
Ihrler
S
S
D000686:Amyloidosis / Q000175:diagnosis* / Q000473:pathology*; D001536:Bence Jones Protein / Q000032:analysis; D001706:Biopsy; D003299:Cooperative Behavior; D005260:Female; D006801:Humans; D007075:Immunoglobulin M / Q000032:analysis*; D033183:Interdisciplinary Communication; D008047:Lip Diseases / Q000175:diagnosis* / Q000473:pathology*; D008048:Lip Neoplasms / Q000175:diagnosis* / Q000473:pathology* / Q000601:surgery; D018442:Lymphoma, B-Cell, Marginal Zone / Q000175:diagnosis* / Q000473:pathology*; D008279:Magnetic Resonance Imaging; D008545:Melanoma / Q000601:surgery; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000601:surgery; D010265:Paraproteinemias / Q000175:diagnosis* / Q000473:pathology*; D010348:Patient Care Team; D011183:Postoperative Complications / Q000175:diagnosis / Q000473:pathology; D012468:Salivary Gland Neoplasms / Q000175:diagnosis* / Q000473:pathology*; D012470:Salivary Glands, Minor / Q000473:pathology*; D012859:Sjogren's Syndrome / Q000175:diagnosis* / Q000473:pathology*
D007075:Immunoglobulin M; D001536:Bence Jones Protein