Oral findings and dental treatment in a child with West syndrome.
West syndrome (WS) is a rare, severe form of epilepsy that typically manifests early in infancy. It is considered a malignant condition that combines episodes of spasms that occur in clusters (infantile spasm), hypsarrhythmia on the electroencephalogram, and neuropsychomotor delay. Although WS has been widely investigated from a medical standpoint, few reports have focused on the oral findings in patients with this syndrome. This article reports the case history of a 7-year-old child diagnosed with WS. The major clinical features were generalized tooth wear and gingival enlargement, altered chronology and sequence of dental eruption, primary canine cusp-to-cusp relationship, ectopic dental eruption, and mildly arched palate. Multiple white spot lesions were also observed, possibly associated with poor oral hygiene, due to a fermentable carbohydrate-rich diet, and continuous use of sugar-containing medications. Dental care management of patients with special needs is discussed and the dental treatment for this child with WS is described.
Regis
Rômulo Rocha
RR
Department of Dental Materials and Prosthodontics, Preventive and Community Dentistry, School of Dentistry of Ribeirão Preto, University of São Paulo, Ribeirão Preto, São Paulo, Brazil.
Rocha
Cristiane Tomaz
CT
Torres
Carolina Paes
CP
Queiroz
Ivna Fernandes
IF
de Queiroz
Alexandra Mussolino
AM
D002648:Child; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries / Q000517:prevention & control; D003793:Dental Restoration, Permanent; D005260:Female; D019214:Gingival Overgrowth / Q000209:etiology; D006801:Humans; D007223:Infant; D013036:Spasms, Infantile / Q000150:complications; D013577:Syndrome; D014078:Tooth Eruption; D014079:Tooth Eruption, Ectopic / Q000209:etiology; D057085:Tooth Wear / Q000209:etiology