Mixed epithelial and stromal renal tumour in a 12-year-old boy.
Mixed epithelial and stromal tumour of the kidney (MESTK) is a rare kidney neoplasm that occurs almost exclusively in perimenopausal women. Long-term oestrogen replacement appears to play a major role in its pathogenesis. Around 70 cases have been described in the international literature, none of which involve male children. Herein, we describe an atypical case of MESTK diagnosed in a 12-year-old prepubertal boy who presented with hematuria. Pathology and immunohistochemistry revealed a typical MESTK. The child was free of disease at 2-year follow up after a partial nephrectomy and tumour excision.
Teklali
Youssef
Y
Paediatric Surgery Department, CHU Grenoble, France. yteklali@chu-grenoble.fr
Piolat
Christian
C
Durand
Chantal
C
Boillot
Bernard
B
Pasquier
Dominique
D
Jacquier
Catherine
C
Dyon
Jean François
JF
D002648:Child; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D007680:Kidney Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D008297:Male; D018193:Neoplasms, Complex and Mixed / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D009375:Neoplasms, Glandular and Epithelial / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D009392:Nephrectomy; D014463:Ultrasonography