title: Oral findings and dental treatment in a child with West syndrome.
abstract: West syndrome (WS) is a rare, severe form of epilepsy that typically manifests early in infancy. It is considered a malignant condition that combines episodes of spasms that occur in clusters (infantile spasm), hypsarrhythmia on the electroencephalogram, and neuropsychomotor delay. Although WS has been widely investigated from a medical standpoint, few reports have focused on the oral findings in patients with this syndrome. This article reports the case history of a 7-year-old child diagnosed with WS. The major clinical features were generalized tooth wear and gingival enlargement, altered chronology and sequence of dental eruption, primary canine cusp-to-cusp relationship, ectopic dental eruption, and mildly arched palate. Multiple white spot lesions were also observed, possibly associated with poor oral hygiene, due to a fermentable carbohydrate-rich diet, and continuous use of sugar-containing medications. Dental care management of patients with special needs is discussed and the dental treatment for this child with WS is described.
authors.affiliation: Department of Dental Materials and Prosthodontics, Preventive and Community Dentistry, School of Dentistry of Ribeirão Preto, University of São Paulo, Ribeirão Preto, São Paulo, Brazil.
authors.forename: Rômulo Rocha
authors.initials: RR
authors.lastname: Regis
authors.forename: Cristiane Tomaz
authors.initials: CT
authors.lastname: Rocha
authors.forename: Carolina Paes
authors.initials: CP
authors.lastname: Torres
authors.forename: Ivna Fernandes
authors.initials: IF
authors.lastname: Queiroz
authors.forename: Alexandra Mussolino
authors.initials: AM
authors.lastname: de Queiroz
mesh_terms: D002648:Child; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries / Q000517:prevention & control; D003793:Dental Restoration, Permanent; D005260:Female; D019214:Gingival Overgrowth / Q000209:etiology; D006801:Humans; D007223:Infant; D013036:Spasms, Infantile / Q000150:complications; D013577:Syndrome; D014078:Tooth Eruption; D014079:Tooth Eruption, Ectopic / Q000209:etiology; D057085:Tooth Wear / Q000209:etiology