title: [Thoracic impairment from familial Mediterranean fever: review of the literature and a case study].
abstract: Familial Mediterranean fever (FMF) is a recessive autosomal disease, predominantly affecting the population around the Mediterranean. The main clinical signs consist of attacks of fever associated with abdominal, articular and thoracic pain. Based on a case report, the authors describe the main thoracic forms of this illness comprising pleural pain, pleural effusion and pulmonary amyloidosis. The authors also discuss the association of mesothelioma and FMF. Colchicine is successfully used in the treatment of FMF.
authors.affiliation: Service de Pneumologie, CHU de Strasbourg, 1, Place de l'Hôpital, 67000, Strasbourg, France. gilwirtz@hotmail.com
authors.forename: G
authors.initials: G
authors.lastname: Wirtz
authors.forename: E
authors.initials: E
authors.lastname: Andrès
authors.forename: R
authors.initials: R
authors.lastname: Kessler
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D000328:Adult; D000686:Amyloidosis / Q000175:diagnosis; D001168:Arthritis / Q000209:etiology; D003078:Colchicine / Q000627:therapeutic use; D003937:Diagnosis, Differential; D010505:Familial Mediterranean Fever / Q000150:complications* / Q000175:diagnosis* / Q000188:drug therapy / Q000235:genetics; D005260:Female; D005334:Fever / Q000209:etiology; D005838:Genotype; D006801:Humans; D008171:Lung Diseases / Q000175:diagnosis; D009154:Mutation; D010375:Pedigree; D010641:Phenotype; D010996:Pleural Effusion / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy / Q000235:genetics; D010998:Pleurisy / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy / Q000235:genetics; D016896:Treatment Outcome; D050257:Tubulin Modulators / Q000627:therapeutic use
chemical_list: D050257:Tubulin Modulators; D003078:Colchicine