[Carcinoid of the minor duodenal papilla associated with multiple jejunal leiomyomas in type 1 neurofibromatosis].
Duodenal endocrine tumors are rare and represent 2% of all gastrointestinal endocrine neoplasms. Carcinoids of the ampulla of Vater are the most rare primary ampullary tumors. There was noted a frequent association of the endocrine tumors with type 1 neurofibromatosis also known as von Recklinghausen disease. To the best of our knowledge there are only 8 cases of papilla duodenalis minor carcinoids described in the literature. Authors describe herein the first carcinoid of papilla duodenalis minor case associated with multiple synchronic jejunal leiomyomas and von Recklinghausen disease, manifested with proximal intestinal obstruction and resolved by pancreatoduodenectomy (Kausch-Whipple procedure).
Ghidirim
Gh
G
Catedra Chirurgie nr. 1 N. Anestiadi şi Laboratorul de Chirurgie Hepato-Bilio-Pancreatic8, Universitatea de Medicină şi Farmacie N. Testemitanu, Chişinău, Moldova.
Rojnoveanu
Gh
G
Mişin
I
I
Cernîi
A
A
Gurghiş
R
R
D014670:Ampulla of Vater / Q000473:pathology; D002276:Carcinoid Tumor / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D004379:Duodenal Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007580:Jejunal Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D007889:Leiomyoma / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D008297:Male; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D010183:Pancreatic Ducts / Q000473:pathology; D016577:Pancreaticoduodenectomy / Q000379:methods; D016896:Treatment Outcome