Extraosseous Ewing's sarcoma / primitive neuroectodermal tumor of the sacral nerve plexus.
We report an unusual case of Ewing's sarcoma / primitive neuroectodermal tumor (PNET) of the sacral nerve plexus in a 9-year-old boy who presented with a soft tissue swelling and severe piercing pain in the lower back region. MRI of the lumbosacral spine showed a lobulated soft tissue mass with clubbed finger-like projections along the path of the sacral nerves, which had caused widening of the spinal canal and the sacral foramina (S2-S4 level). There was presacral extension and posterior scalloping of the sacral vertebrae. Histopathology of the lesion confirmed Ewing's sarcoma / PNET of the sacral spinal nerve plexus. The patient responded favorably to chemotherapy and radiotherapy, showing clinical and radiological improvement.
Narula
M K
MK
Department of Radiodiagnosis, Lady Hardinge Medical College, and Associated Smt. Sucheta Kriplani and Kalawati Saran Children Hospital, New Delhi-110 001, India.
Gupta
Nishant
N
Anand
Rama
R
Kapoor
Sudhir
S