title: Pharmacological treatment of electrical storm in cathecolaminergic polymorphic ventricular tachycardia.
abstract: We present a case of a young boy who had an implantable cadrioverter defibrillator implanted for refractory syncope and cathecolaminergic polymorphic ventricular tachycardia (CPVT). The patient underwent an electrical storm with multiple shocks and serious compromise of quality of life and risk. The pharmacological options are discussed as well as the strategies of managing ventricular arrhythmias in CPVT.
authors.affiliation: Arrhythmia Service, Hospital Portugues da Bahia, Salvador-Bahia, Brazil. alexfagundes@cardiol.br
authors.forename: Alexsandro
authors.initials: A
authors.lastname: Fagundes
authors.forename: Luiz Pereira
authors.initials: LP
authors.lastname: DE Magalhaes
authors.forename: Marcelo
authors.initials: M
authors.lastname: Russo
authors.forename: Edvaldo
authors.initials: E
authors.lastname: Xavier
mesh_terms: D000293:Adolescent; D000889:Anti-Arrhythmia Agents / Q000627:therapeutic use*; D001262:Atenolol / Q000627:therapeutic use; D017147:Defibrillators, Implantable; D004359:Drug Therapy, Combination; D004562:Electrocardiography; D005080:Exercise Test; D006801:Humans; D008297:Male; D009248:Nadolol / Q000627:therapeutic use; D011788:Quality of Life; D013575:Syncope / Q000517:prevention & control; D017180:Tachycardia, Ventricular / Q000175:diagnosis / Q000188:drug therapy* / Q000517:prevention & control; D014700:Verapamil / Q000627:therapeutic use
chemical_list: D000889:Anti-Arrhythmia Agents; D009248:Nadolol; D001262:Atenolol; D014700:Verapamil