Congenital erythropoietic porphyria: anesthetic implications.
Congenital erythropoietic porphyria is a rare error of heme metabolism. Derangement of heme metabolism leads to disfiguration, phototoxicity, and the precipitation of porphyric crises. This case report discusses the myriad perioperative considerations in a patient with congenital erythropoietic porphyria.
Kumar
Mritunjay
M
Department of Anesthesiology and Intensive Care, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, India.
Bose
Somnath
S
Darlong
Vanlal
V
Punj
Jyotsna
J
D000328:Adult; D000768:Anesthesia, General; D001766:Blindness / Q000209:etiology / Q000601:surgery*; D017484:Dermatitis, Phototoxic / Q000209:etiology; D009877:Endophthalmitis / Q000601:surgery; D006227:Hand Deformities, Acquired / Q000150:complications; D006418:Heme / Q000378:metabolism; D006801:Humans; D008297:Male; D013508:Ophthalmologic Surgical Procedures; D010149:Postoperative Pain / Q000188:drug therapy; D019990:Perioperative Care; D017092:Porphyria, Erythropoietic / Q000150:complications* / Q000473:pathology; D011183:Postoperative Complications / Q000209:etiology / Q000628:therapy
D006418:Heme