title: Nutrition management of pediatric patients who have cystic fibrosis.
abstract: Since the identification of cystic fibrosis (CF) in the 1940s, nutrition care of patients who have CF has been a challenge. Through optimal caloric intake and careful management of malabsorption, patients are expected to meet genetic potential for growth. Yet factors beyond malabsorption, including nutrient activity at the cellular level, may influence growth and health. This article reviews nutrition topics frequently discussed in relationship to CF and presents intriguing new information describing nutrients currently being studied for their impact on overall health of patients who have CF.
authors.affiliation: Department of Clinical Nutrition, The Children's Hospital of Philadelphia, University of Pennsylvania School of Medicine, 34th Street and Civic Center Boulevard, 9NW, Room 82, Philadelphia, PA 19104-4399, USA. michelsu@email.chop.edu
authors.forename: Suzanne H
authors.initials: SH
authors.lastname: Michel
authors.forename: Asim
authors.initials: A
authors.lastname: Maqbool
authors.forename: Maria D
authors.initials: MD
authors.lastname: Hanna
authors.forename: Maria
authors.initials: M
authors.lastname: Mascarenhas
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D002794:Choline / Q000008:administration & dosage; D003550:Cystic Fibrosis / Q000150:complications / Q000178:diet therapy / Q000378:metabolism; D004044:Dietary Proteins / Q000008:administration & dosage*; D002149:Energy Intake; D005228:Fatty Acids, Essential / Q000008:administration & dosage; D005978:Glutathione / Q000008:administration & dosage; D006801:Humans; D007223:Infant; D008286:Malabsorption Syndromes / Q000175:diagnosis / Q000209:etiology / Q000628:therapy*; D018977:Micronutrients / Q000008:administration & dosage*; D008903:Minerals / Q000008:administration & dosage; D014131:Trace Elements / Q000008:administration & dosage; D014451:Ubiquinone / Q000008:administration & dosage / Q000031:analogs & derivatives; D014815:Vitamins / Q000008:administration & dosage; D055815:Young Adult
chemical_list: D004044:Dietary Proteins; D005228:Fatty Acids, Essential; D018977:Micronutrients; D008903:Minerals; D014131:Trace Elements; D014815:Vitamins; D014451:Ubiquinone; C024989:coenzyme Q10; D005978:Glutathione; D002794:Choline