title: Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report.
abstract: Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old German Caucasian male with Papillon-Lefèvre syndrome associated with recurrent squamous cell carcinoma. Treatment is symptomatic and not always satisfactory.
authors.affiliation: Department of Plastic and Reconstructive Surgery, Department of Hand Surgery, Soft Tissue Tumour Reference Centre, BG University Hospital Bergmannsheil, Ruhr University Bochum, Buerkle-de-la Camp-Platz 1, 44789 Bochum, Germany. sammy.al-benna@ruhr-uni-bochum.de
authors.forename: Sammy
authors.initials: S
authors.lastname: Al-Benna
authors.forename: Raphael
authors.initials: R
authors.lastname: Hasler
authors.forename: Ingo
authors.initials: I
authors.lastname: Stricker
authors.forename: Hans-Ulrich
authors.initials: HU
authors.lastname: Steinau
authors.forename: Lars
authors.initials: L
authors.lastname: Steinstraesser