Isolated ventricular non-compaction: an underdiagnosed cause of congestive heart failure.
Isolated ventricular non-compaction is a frequently underdiagnosed rare congenital cardiomyopathy. The importance of diagnosing this cardiomyopathy lies especially in asymptomatic patients, screening relatives of index cases in order to focus on their follow-up, and searching for criteria warranting prophylactic anticoagulation, implantable cardioverter defibrillator and anti-remodeling drugs such as angiotensin-converting inhibitors. We present the clinical and imaging characteristics of this entity and discuss some of the therapeutic dilemmas involving these patients.
Schwartzenberg
Shmuel
S
Department of Cardiology, Tel Aviv Sourasky Medical Center, Tel Aviv, Israel. sschwartzenberg@gmail.com
Sherez
Jack
J
Wexler
Dov
D
Aviram
Galit
G
Keren
Gad
G
D009202:Cardiomyopathies / Q000151:congenital / Q000000981:diagnostic imaging / Q000473:pathology*; D017023:Coronary Angiography; D006333:Heart Failure / Q000209:etiology* / Q000473:pathology; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000473:pathology*; D006801:Humans; D009206:Myocardium / Q000473:pathology*; D011379:Prognosis; D018615:Ultrasonography, Doppler, Color