Embolization of congenital intrahepatic porto-systemic shunt by n-butyl cyanoacrylate.
Congenital intrahepatic portosystemic venous shunt (IHPSVS) is rare vascular anomaly. We present one case of a 14-month male child who presented with global developmental delay. Child had high ammonia levels with low glutamine and high bile salts on the previous investigations and had history of neonatal seizures since day 13 of life. On admission, serum ammonia levels were elevated to 112micromol/L. Other laboratory investigations including liver and renal function test, and electrolytes were normal. He was, diagnosed to have IHPSVS on the basis of Doppler and CT, and treated by embolization with n-butyl cyanoacrylate (glue). A brief review of diagnostic modalities and endovascular management for the IHPSVS is presented including the present case.
Gupta
Vivek
V
Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India. drvivekgupta.pgi@gmail.com
Kalra
Naveen
N
Vyas
Sameer
S
Sodhi
K S
KS
Thapa
B R
BR
Khandelwal
N
N
D004621:Embolization, Therapeutic / Q000379:methods*; D004659:Enbucrilate / Q000494:pharmacology*; D005500:Follow-Up Studies; D006503:Hepatic Veins / Q000002:abnormalities*; D006801:Humans; D022124:Hyperammonemia / Q000151:congenital / Q000175:diagnosis / Q000628:therapy; D007223:Infant; D018810:Magnetic Resonance Angiography; D008297:Male; D011169:Portal Vein / Q000002:abnormalities*; D018570:Risk Assessment; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D016157:Vascular Fistula / Q000151:congenital* / Q000000981:diagnostic imaging / Q000628:therapy*; D054079:Vascular Malformations / Q000000981:diagnostic imaging* / Q000503:physiopathology / Q000628:therapy*
D004659:Enbucrilate