A latent form of essential thrombocythemia presenting as portal cavernoma.
Essential thrombocythemia is frequently associated with abdominal thrombotic complications including portal cavernoma as a consequence of chronic portal vein thrombosis. Essential thrombocythemia in a latent form is difficult to identify at onset due to the absence of an overt disease phenotype. In the presented case report, the diagnosis of essential thrombocythemia was initially missed because the typical disease phenotype was masked by bleeding and hypersplenism. The correct diagnosis was only reached when the patient experienced persistent thrombocytosis and pseudohyperkalemia after a shunt operation.
Cai
Xiao-Yan
XY
Department of General Surgery, Sir Run Run Shaw Hospital, College of Medicine, Sir Run Run Shaw Institute of Clinical Medicine of Zhejiang University, Hangzhou 310016, Zhejiang Province, China.
Zhou
Wei
W
Hong
De-Fei
DF
Cai
Xiu-Jun
XJ
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D005343:Fibrinolytic Agents / Q000627:therapeutic use; D006392:Hemangioma, Cavernous / Q000150:complications / Q000473:pathology*; D006801:Humans; D010641:Phenotype; D011169:Portal Vein; D013156:Splenectomy; D013920:Thrombocythemia, Essential / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D014057:Tomography, X-Ray Computed / Q000009:adverse effects; D016896:Treatment Outcome; D019043:Vascular Neoplasms / Q000209:etiology*
D005343:Fibrinolytic Agents