Bilateral renal inflammatory pseudotumour effectively treated with corticosteroid.
Inflammatory pseudotumour (IPT) is a rare disease of unknown cause that most commonly involves the lung but can occur in almost any site in the body. Occurrence in the kidneys is very rare and bilateral renal involvement even rarer. There are 34 previously reported cases in the English-language medical literature between 1966 and 2008. Herein we report a case of IPT infiltrating both kidneys. We have also reviewed the clinical features, radiological findings, treatment and outcome of renal IPT. Clinical features at presentation are commonly non-specific. Features on imaging are inadequate to make a diagnosis of IPT or to clearly distinguish it from malignancy. Consequently diagnosis has frequently been made after nephrectomy and on a few occasions with the aid of percutaneous or open biopsies. The majority of renal IPT (83%) have been treated with nephrectomy and those cases with bilateral IPT have received corticosteroids.
Li
Jordan Yuanzhi
JY
Department of Nephrology, Flinders Medical Centre, Flinders University, Bedford Park, Adelaide, SA 5042, Australia. jordan.li@health.sa.gov.au
Yong
Tuck Y
TY
Coleman
Mark
M
Astill
David
D
Passaris
George
G
Juneja
Rajiv
R
Siddins
Mark
M
Barbara
Jeffrey A J
JA
D006104:Granuloma, Plasma Cell / Q000175:diagnosis / Q000188:drug therapy* / Q000473:pathology; D006801:Humans; D007668:Kidney / Q000473:pathology; D007674:Kidney Diseases / Q000175:diagnosis / Q000188:drug therapy* / Q000473:pathology; D008297:Male; D008875:Middle Aged; D011239:Prednisolone / Q000627:therapeutic use*; D016896:Treatment Outcome
D011239:Prednisolone