Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report.
Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old German Caucasian male with Papillon-Lefèvre syndrome associated with recurrent squamous cell carcinoma. Treatment is symptomatic and not always satisfactory.
Al-Benna
Sammy
S
Department of Plastic and Reconstructive Surgery, Department of Hand Surgery, Soft Tissue Tumour Reference Centre, BG University Hospital Bergmannsheil, Ruhr University Bochum, Buerkle-de-la Camp-Platz 1, 44789 Bochum, Germany. sammy.al-benna@ruhr-uni-bochum.de
Hasler
Raphael
R
Stricker
Ingo
I
Steinau
Hans-Ulrich
HU
Steinstraesser
Lars
L