title: Primary intracranial extra-axial and supratentorial atypical rhabdoid tumor.
abstract: An atypical teratoid/rhabdoid tumor of the central nervous system is an aggressive infantile embryonal neoplasm, usually presenting as an infratentorial and intraparenchymatous lesion. We report on magnetic resonance imaging findings of a 22-month-old boy with a biopsy-proven primary rhabdoid tumor, presenting as a single intracranial supratentorial extra-axial mass. Based on the patient's age and imaging features (perfusion, diffusion magnetic resonance imaging, and magnetic resonance spectroscopy), a diagnosis of atypical teratoid/rhabdoid tumor was more accurate than diagnoses of meningioma and primitive neuroectodermal tumor. Although this entity is relatively rare, it should be considered in the differential diagnosis of dural-based, space-occupying central nervous system lesions.
authors.affiliation: Neuroradiology Unit, University Hospital of Grenoble, 38700 Grenoble Cedex 09, France. fbing@chu-grenoble.fr
authors.forename: Fabrice
authors.initials: F
authors.lastname: Bing
authors.forename: Frédérique
authors.initials: F
authors.lastname: Nugues
authors.forename: Sylvie
authors.initials: S
authors.lastname: Grand
authors.forename: Pierre
authors.initials: P
authors.lastname: Bessou
authors.forename: Caroline
authors.initials: C
authors.lastname: Salon
mesh_terms: D001921:Brain / Q000378:metabolism / Q000473:pathology / Q000601:surgery; D001929:Brain Edema / Q000473:pathology; D001932:Brain Neoplasms / Q000175:diagnosis* / Q000473:pathology* / Q000628:therapy; D003937:Diagnosis, Differential; D038524:Diffusion Magnetic Resonance Imaging; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D009682:Magnetic Resonance Spectroscopy; D008297:Male; D009364:Neoplasm Recurrence, Local; D018335:Rhabdoid Tumor / Q000175:diagnosis* / Q000473:pathology* / Q000628:therapy; D015173:Supratentorial Neoplasms / Q000175:diagnosis* / Q000473:pathology* / Q000628:therapy; D016896:Treatment Outcome