[Proliferative sickle cell retinopathy revealing Glanzmann thrombasthenia].
Glanzmann thrombasthenia is a rare qualitative platelet abnormality of autosomal recessive transmission caused by absence of GP IIb/IIIa and resulting in disturbance of platelet aggregation and bleeding time extension. We report the case of a 16-year-old female suffering from SC sickle cell disease and presenting with bilateral vitreous hemorrhage revealing Glanzmann thrombasthenia. Despite vitrectomy, the functional prognosis was poor. Indeed, association of a severe hemorrhagic disease and sickle cell retinopathy makes surgical management difficult.
Odoulami-Yehouessi
L
L
Clinique Ophtalmologique, Centre National Hospitalier et Universitaire Hubert Koutoukou Maga, Cotonou, Bénin. drodoulis@yahoo.fr
Sounouvou
I
I
Anani
L
L
Tachabi
S
S
Doutentien
C
C
Latoundji
S
S
D000293:Adolescent; D000755:Anemia, Sickle Cell / Q000150:complications*; D005260:Female; D006801:Humans; D012164:Retinal Diseases / Q000209:etiology*; D013915:Thrombasthenia / Q000150:complications* / Q000175:diagnosis