title: Autoimmune pancreatitis associated with various extrapancreatic lesions during a long-term clinical course successfully treated with azathioprine and corticosteroid maintenance therapy.
abstract: Autoimmune pancreatitis (AIP) is often associated with systemic extrapancreatic lesions, and the concept of IgG4-related autoimmune disease has been proposed. We report a 62-year-old woman with AIP associated with various extrapancreatic lesions during a long-term clinical course. These extrapancreatic lesions occurred after the withdrawal of steroid therapy. Sclerosing sialadenitis occurred before AIP, whereas autoimmune sensorineural hearing loss, allergic purpura and endocapillary proliferative glomerulonephritis occurred after AIP. However, no relapse was observed for 5 years after the start of maintenance therapy with prednisolone and azathioprine.
authors: Department of Gastroenterology and Metabolism, Nagoya City University Graduate School of Medical Sciences, Nagoya.
authors: Itaru
authors: I
authors: Naitoh
authors: Takahiro
authors: T
authors: Nakazawa
authors: Hirotaka
authors: H
authors: Ohara
authors: Hitoshi
authors: H
authors: Sano
authors: Tomoaki
authors: T
authors: Ando
authors: Kazuki
authors: K
authors: Hayashi
authors: Hajime
authors: H
authors: Tanaka
authors: Fumihiro
authors: F
authors: Okumura
authors: Katsuyuki
authors: K
authors: Miyabe
authors: Michihiro
authors: M
authors: Yoshida
authors: Satoru
authors: S
authors: Takahashi
authors: Takashi
authors: T
authors: Joh
mesh_terms: D000305:Adrenal Cortex Hormones / Q000008:administration & dosage*; D001327:Autoimmune Diseases / Q000188:drug therapy* / Q000276:immunology / Q000473:pathology; D001379:Azathioprine / Q000008:administration & dosage*; D004359:Drug Therapy, Combination; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000188:drug therapy / Q000276:immunology / Q000473:pathology; D006801:Humans; D011695:IgA Vasculitis / Q000188:drug therapy / Q000276:immunology / Q000473:pathology; D008875:Middle Aged; D010195:Pancreatitis / Q000188:drug therapy* / Q000276:immunology / Q000473:pathology; D012793:Sialadenitis / Q000188:drug therapy / Q000276:immunology / Q000473:pathology; D013997:Time Factors; D016896:Treatment Outcome
chemical_list: D000305:Adrenal Cortex Hormones; D001379:Azathioprine