Need for comprehensive vascular assessment before surgical repair of aortic coarctation in PHACES syndrome.
Children with PHACES syndrome commonly present with aortic coarctation and abnormalities of the supra-aortic and intracranial arteries. We describe a case of complex aortic coarctation in the context of PHACES syndrome, where preoperative detection of abnormalities in supra-aortic and intracranial arteries led to modification of the surgical technique adopted, in order to avoid potential neurological damage.
Giardini
Alessandro
A
Cardiorespiratory Unit, Great Ormond Street Hospital for Children, London WC1N 3JH, UK. alessandro5574@iol.it
Gholam
Caroline
C
Khambadkone
Sachin
S
Kostolny
Martin
M
D000015:Abnormalities, Multiple / Q000473:pathology*; D001017:Aortic Coarctation / Q000473:pathology* / Q000601:surgery*; D001921:Brain / Q000098:blood supply*; D020785:Central Nervous System Vascular Malformations / Q000473:pathology* / Q000601:surgery; D005153:Facial Neoplasms; D006391:Hemangioma; D006801:Humans; D007223:Infant; D018810:Magnetic Resonance Angiography; D011300:Preoperative Care; D013577:Syndrome