Isolated left ventricular noncompaction cardiomyopathy accompanied by severe mitral regurgitation.
Isolated left ventricular noncompaction cardiomyopathy (IVNC) is a cardiomyopathy thought to be caused by arrest of normal embryogenesis of the endocardium and myocardium. This abnormality is often associated with other congenital cardiac defects. A 21-year-old man presented to the emergency department with worsening exertional dyspnea during the previous 2 months. Two-dimensional and Doppler echocardiography revealed an enlarged left atrium (LA) and a markedly dilated left ventricle (LV) with preserved LV systolic function, severe mitral valve regurgitation, and prolapse due to chordae rupture. The myocardium of the LV and right ventricle (RV) had excessively prominent trabeculations and deep intertrabecular recesses. He is the first patient in Korea who has undergone mitral valve replacement surgery because of severe mitral valve regurgitation and prolapse due to chordae rupture accompanied by IVNC.
Chung
Jong Won
JW
Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea, St. Mary's Hospital, Seoul, Korea.
Lee
Sung Jin
SJ
Lee
Jae Hak
JH
Chin
Jung Yeon
JY
Lee
Hyo Jin
HJ
Lee
Chang Jung
CJ
Choi
Yun Seok
YS
Shim
Sung Bo
SB
Youn
Ho-Joong
HJ
Lee
Sun Hee
SH