Right ventricular hypertrabeculation associated with double-outlet left ventricle: exaggeration of a normal pattern or right ventricular cardiomyopathy?
We describe a rare case of double-outlet left ventricle, ventricular septal defect, and subpulmonary valve stenosis surgically corrected by Rastelli procedure, developing severe homograft obstruction with right ventricular dilation and extensive hypertrabeculation/noncompaction during follow-up. We briefly discuss the cause diagnosis, and clinical significance of right ventricular hypertrabeculation/noncompaction.
Limongelli
Giuseppe
G
Department of Cardiology, Monaldi Hospital, Second University of Naples, Naples, Italy. limongelligiuseppe@libero.it
Pacileo
Giuseppe
G
Calabro'
Paolo
P
Rea
Alessandra
A
Masarone
Daniele
D
Di Salvo
Giovanni
G
D'Andrea
Antonello
A
Vatta
Matteo
M
Elliott
Perry M
PM
Calabro
Raffaele
R
D000015:Abnormalities, Multiple; D000293:Adolescent; D019917:Blood Vessel Prosthesis Implantation / Q000009:adverse effects*; D006328:Cardiac Catheterization; D009202:Cardiomyopathies / Q000175:diagnosis* / Q000209:etiology; D004108:Dilatation, Pathologic; D004310:Double Outlet Right Ventricle / Q000150:complications / Q000601:surgery*; D018618:Echocardiography, Doppler, Color; D019918:Heart Valve Prosthesis Implantation / Q000009:adverse effects*; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000150:complications / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D008297:Male; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000601:surgery*