A late presentation of Dandy-Walker malformation and aortic coarctation.
The Dandy-Walker malformation is a rare anomaly of the posterior cranial fossa. Concomitant brain or systemic malformations are frequent and can influence the outcome. Associated cardiac congenital defects usually induce a poor prognosis. We report a case of a 58-yearold man with hydrocephalus, in whom Dandy-Walker malformation was diagnosed, for the first time, after the demonstration of aortic coarctation. This association is very rare and only a few cases have been described; moreover, to our knowledge, this is the first description of this incidence in a middle-aged patient. The characteristic of diseases and physiopathologic features are discussed, focusing attention on the rare and late clinical manifestations.
Venturini
Elio
E
aDepartment of Cardiology, Civic Hospital Cecina, Cecina bDepartment of Neurology, Civic Hospital Piombino, Piombino, Italy.
Magni
Lucia
L
Pucci
Giovanna
G
Mazzinghi
Fabio
F
D000800:Angioplasty, Balloon / Q000295:instrumentation; D001017:Aortic Coarctation / Q000150:complications* / Q000000981:diagnostic imaging / Q000628:therapy; D003616:Dandy-Walker Syndrome / Q000150:complications* / Q000000981:diagnostic imaging / Q000628:therapy; D006801:Humans; D018810:Magnetic Resonance Angiography; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D015607:Stents; D016896:Treatment Outcome