title: Sympathetic dysfunction of systemic right ventricle in congenitally corrected transposition of the great arteries.
abstract: We evaluate the systemic right ventricle (SRV) failure of congenitally corrected transposition of the great arteries using the scintigraphic studies in a case with 32-year-old male who improved the heart failure by the use of beta-adrenergic blockers. The myocardial perfusion sympathetic nervous system activity mismatch with preserved coronary flow and wall thickness indicates a distinctive feature as SRV cardiomyopathy, suggesting the importance of recovery of SRV sympathetic dysfunction for improving the prognosis.
authors.affiliation: Division of Cardiology, Department of Medicine, Showa University School of Medicine, 1-5-8 Hatanodai, Shinagawaku, Tokyo, 142-8666, Japan. hzn01233@s02.itscom.net
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Akutsu
authors.forename: Kyouichi
authors.initials: K
authors.lastname: Kaneko
authors.forename: Yusuke
authors.initials: Y
authors.lastname: Kodama
authors.forename: Hui-Ling
authors.initials: HL
authors.lastname: Li
authors.forename: Jumpei
authors.initials: J
authors.lastname: Suyama
authors.forename: Takehiko
authors.initials: T
authors.lastname: Gokan
authors.forename: Youichi
authors.initials: Y
authors.lastname: Kobayashi
mesh_terms: D000319:Adrenergic beta-Antagonists / Q000627:therapeutic use; D017023:Coronary Angiography; D003330:Coronary Vessel Anomalies / Q000175:diagnosis / Q000503:physiopathology*; D004232:Diuretics / Q000627:therapeutic use; D004452:Echocardiography; D006329:Heart Conduction System / Q000503:physiopathology*; D006333:Heart Failure / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology*; D006352:Heart Ventricles / Q000503:physiopathology*; D006801:Humans; D008297:Male; D013564:Sympathetic Nervous System / Q000503:physiopathology*; D015899:Tomography, Emission-Computed, Single-Photon; D014057:Tomography, X-Ray Computed; D014188:Transposition of Great Vessels / Q000175:diagnosis / Q000503:physiopathology*
chemical_list: D000319:Adrenergic beta-Antagonists; D004232:Diuretics