title: A case of desmoplastic small round cell tumor diagnosed in a young female patient.
abstract: Desmoplastic small round cell tumor is a very rare malignancy. We report the case of a 26-year-old woman who suffered from dyspepsia and abdominal pain for 2 months. We performed an endoscopic biopsy of the duodenal mass and diagnosed her disease as desmoplastic small round cell tumor using immunohistochemical staining, fluorescence in situ hybridization, and reverse transcriptase polymerase chain reaction. Because the mass invaded the pancreas and superior mesenteric vein as well as duodenum and the disease was disseminated to liver and peritoneum, she received palliative chemotherapy using vincristine, doxorubicin, cyclophosphamide, ifosfamide, and etoposide. The maximal response to chemotherapy was stable disease. The patient expired 9 months after diagnosis.
authors.affiliation: Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.
authors.forename: Ji-Won
authors.initials: JW
authors.lastname: Kim
authors.forename: Jin Hyun
authors.initials: JH
authors.lastname: Park
authors.forename: Hyeon Jin
authors.initials: HJ
authors.lastname: Cho
authors.forename: Ji-Hyun
authors.initials: JH
authors.lastname: Kwon
authors.forename: Youngil
authors.initials: Y
authors.lastname: Koh
authors.forename: Su-Jung
authors.initials: SJ
authors.lastname: Kim
authors.forename: Se Hyung
authors.initials: SH
authors.lastname: Kim
authors.forename: Se-Hoon
authors.initials: SH
authors.lastname: Lee
authors.forename: Seock-Ah
authors.initials: SA
authors.lastname: Im
authors.forename: Yong-Tae
authors.initials: YT
authors.lastname: Kim
authors.forename: Woo Ho
authors.initials: WH
authors.lastname: Kim