Eisenmenger syndrome and juvenile rheumatoid arthritis--a case of double diagnosis.
An 8.5-year-old girl evaluated for central cyanosis, hypoxia and normocarbia was found to have aorticopulmonary window and pulmonary hypertension. The diagnosis of Eisenmenger syndrome (ES) was made and treatment with bosentan was started. Four months later she was diagnosed to have juvenile rheumatoid arthritis and naproxen treatment was started. The case was remarkable in that she showed clinical improvement with new generation treatment of ES although pulmonary arterial pressure did not decrease significantly and the diagnosis of juvenile rheumatoid arthritis was made during follow-up.
Ozdemir
Osman
O
Department of Paediatric Cardiology, Kecioren Training and Research Hospital, Ankara, Turkey. pedkard@gmail.com
Agras
Pinar Isik
PI
Hizli
Samil
S
Guveloglu
Mine
M
Kabakus
Nimet
N
D000894:Anti-Inflammatory Agents, Non-Steroidal / Q000627:therapeutic use; D000959:Antihypertensive Agents / Q000627:therapeutic use; D001171:Arthritis, Juvenile / Q000175:diagnosis* / Q000188:drug therapy / Q000209:etiology; D000077300:Bosentan; D002648:Child; D003937:Diagnosis, Differential; D004541:Eisenmenger Complex / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D005260:Female; D006801:Humans; D009288:Naproxen / Q000627:therapeutic use; D013449:Sulfonamides / Q000627:therapeutic use; D016896:Treatment Outcome
D000894:Anti-Inflammatory Agents, Non-Steroidal; D000959:Antihypertensive Agents; D013449:Sulfonamides; D009288:Naproxen; D000077300:Bosentan