Diffuse supravalvular aortic stenosis: surgical repair in adulthood.
We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.
Ferlan
Giovanni
G
Department of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, Italy.
De Pasquale
Claudio
C
Losito
Concetta
C
Fiorella
Annalisa
A
Marraudino
Nicola
N
Tunzi
Francesco
F