title: Diffuse supravalvular aortic stenosis: surgical repair in adulthood.
abstract: We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.
authors.affiliation: Department of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, Italy.
authors.forename: Giovanni
authors.initials: G
authors.lastname: Ferlan
authors.forename: Claudio
authors.initials: C
authors.lastname: De Pasquale
authors.forename: Concetta
authors.initials: C
authors.lastname: Losito
authors.forename: Annalisa
authors.initials: A
authors.lastname: Fiorella
authors.forename: Nicola
authors.initials: N
authors.lastname: Marraudino
authors.forename: Francesco
authors.initials: F
authors.lastname: Tunzi