Sympathetic dysfunction of systemic right ventricle in congenitally corrected transposition of the great arteries.
We evaluate the systemic right ventricle (SRV) failure of congenitally corrected transposition of the great arteries using the scintigraphic studies in a case with 32-year-old male who improved the heart failure by the use of beta-adrenergic blockers. The myocardial perfusion sympathetic nervous system activity mismatch with preserved coronary flow and wall thickness indicates a distinctive feature as SRV cardiomyopathy, suggesting the importance of recovery of SRV sympathetic dysfunction for improving the prognosis.
Akutsu
Yasushi
Y
Division of Cardiology, Department of Medicine, Showa University School of Medicine, 1-5-8 Hatanodai, Shinagawaku, Tokyo, 142-8666, Japan. hzn01233@s02.itscom.net
Kaneko
Kyouichi
K
Kodama
Yusuke
Y
Li
Hui-Ling
HL
Suyama
Jumpei
J
Gokan
Takehiko
T
Kobayashi
Youichi
Y
D000319:Adrenergic beta-Antagonists / Q000627:therapeutic use; D017023:Coronary Angiography; D003330:Coronary Vessel Anomalies / Q000175:diagnosis / Q000503:physiopathology*; D004232:Diuretics / Q000627:therapeutic use; D004452:Echocardiography; D006329:Heart Conduction System / Q000503:physiopathology*; D006333:Heart Failure / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology*; D006352:Heart Ventricles / Q000503:physiopathology*; D006801:Humans; D008297:Male; D013564:Sympathetic Nervous System / Q000503:physiopathology*; D015899:Tomography, Emission-Computed, Single-Photon; D014057:Tomography, X-Ray Computed; D014188:Transposition of Great Vessels / Q000175:diagnosis / Q000503:physiopathology*
D000319:Adrenergic beta-Antagonists; D004232:Diuretics