title: Peripheral neuroectodermal tumor of the vulva: a case report.
abstract: BACKGROUND
  Peripheral neuroectodermal tumors arising from vulva are extremely rare; only 12 cases have been reported so far. These tumors belong to the Ewing sarcoma family of tumors. They occur in bones and variety of soft tissues of chest wall, pelvis, paravertebral region, and lower extremities. Being aggressive tumors, they have poor prognosis.
  
  
  METHODS
  We report a case of a 20-year-old woman who presented with a 20 x 15 x 10-cm pedunculated mass arising from the right labium majus. Judicious use of a panel of markers led to diagnosis of peripheral neuroectodermal tumor. The patient died of metastatic disease.
  
  
  CONCLUSIONS
  Judicious use of a panel of markers and a molecular test, if necessary, helps in confirming the diagnosis. Surgery followed by chemotherapy with or without radiation is the treatment of choice.
authors.affiliation: Department of Obstetrics & Gynaecology, All India Institute of Medical Sciences Ansari Nagar, New Delhi, India. vatslad@hotmail.com
authors.forename: Vatsla
authors.initials: V
authors.lastname: Dadhwal
authors.forename: Anupama
authors.initials: A
authors.lastname: Bahadur
authors.forename: Ruchika
authors.initials: R
authors.lastname: Gupta
authors.forename: Saloni
authors.initials: S
authors.lastname: Bansal
authors.forename: Suneeta
authors.initials: S
authors.lastname: Mittal
mesh_terms: D017809:Fatal Outcome; D005260:Female; D006801:Humans; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000175:diagnosis* / Q000473:pathology* / Q000556:secondary; D014846:Vulvar Neoplasms / Q000175:diagnosis* / Q000473:pathology*; D055815:Young Adult