A case of desmoplastic small round cell tumor diagnosed in a young female patient.
Desmoplastic small round cell tumor is a very rare malignancy. We report the case of a 26-year-old woman who suffered from dyspepsia and abdominal pain for 2 months. We performed an endoscopic biopsy of the duodenal mass and diagnosed her disease as desmoplastic small round cell tumor using immunohistochemical staining, fluorescence in situ hybridization, and reverse transcriptase polymerase chain reaction. Because the mass invaded the pancreas and superior mesenteric vein as well as duodenum and the disease was disseminated to liver and peritoneum, she received palliative chemotherapy using vincristine, doxorubicin, cyclophosphamide, ifosfamide, and etoposide. The maximal response to chemotherapy was stable disease. The patient expired 9 months after diagnosis.
Kim
Ji-Won
JW
Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.
Park
Jin Hyun
JH
Cho
Hyeon Jin
HJ
Kwon
Ji-Hyun
JH
Koh
Youngil
Y
Kim
Su-Jung
SJ
Kim
Se Hyung
SH
Lee
Se-Hoon
SH
Im
Seock-Ah
SA
Kim
Yong-Tae
YT
Kim
Woo Ho
WH