[Idiopathic retroperitoneal fibrosis:clinical characteristics of 61 cases and literature review.].
OBJECTIVE
We reviewed the data of 61 cases with idiopathic retroperitoneal fibrosis (IRF). The purpose was to understand the feature of the disease in order to improve its diagnosis and treatment.


METHODS
The clinical data of 61 cases discharged from our hospital were analyzed retrospectively.


RESULTS
IRF was seen in male higher than in female (3.7:1), the mean age was 55.7 years. One case was complicated with polymyositis, two cases had family history. Back pain and abdominal pain were most commonly onset symptoms. 34 patients were treated with surgery, 10 patients treated with corticosteroid or combined with immunosuppressive agents or tamoxifen, 4 patients treated with surgery combined with corticosteroid. Two patients were died, other patients responded well to managements.


CONCLUSIONS
Each of the three different therapeutic approaches were effective. Long-term low dose steroids therapy could prevent recurrence.
Li
Kun-Peng
KP
Department of Rheumatology, Chinese PLA General Hospital, Beijing 100853, China.
Zhu
Jian
J
Zhang
Jiang-Lin
JL
Huang
Feng
F
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D017285:Polymyositis; D012185:Retroperitoneal Fibrosis; D016896:Treatment Outcome
D000305:Adrenal Cortex Hormones; D007166:Immunosuppressive Agents