A difficult airway in a patient with nephrogenic sclerosing fibrosis.
Nephrogenic sclerosing fibrosis (dermopathy) is a relatively rare complication of long-term renal dialysis. The syndrome includes marked thickening of the skin and diffuse fibrosis of fascia, muscle, heart, and lungs, leading to contractures of the joints and limbs and cardiopulmonary compromise. We present the case of a 29-year-old woman who required emergent intubation because of respiratory compromise, and who had had normal airway examinations and intubations before the onset of nephrogenic sclerosing fibrosis symptoms.
Gist
Richard S
RS
Department of Anesthesiology, Section of Critical Care Medicine, Naval Medical Center Portsmouth, Portsmouth, Virginia 23708, USA. richard.gist@med.navy.mi
Miller
David W
DW
Warren
Ty
T
D000328:Adult; D004630:Emergencies; D005260:Female; D005355:Fibrosis; D006801:Humans; D007442:Intubation, Intratracheal; D017214:Laryngeal Masks; D007830:Larynx / Q000473:pathology*; D054989:Nephrogenic Fibrosing Dermopathy / Q000473:pathology*; D012121:Respiration, Artificial; D014139:Tracheostomy