Two-Stage Total Aortic Replacement for Loeys-Dietz Syndrome.
Abstract Loeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.(J Card Surg ****;**:**-**).
Williams
Matthew L
ML
Division of Thoracic and Cardiovascular Surgery, Department of Surgery, Duke University, Durham, North Carolina.
Wechsler
Stephanie Burns
SB
Hughes
G Chad
GC