Rosai-Dorfman disease presenting as a pulmonary artery mass.
Rosai-Dorfman disease is rare and typically presents with cervical lymphadenopathy, but may manifest as extranodal disease. This disease is generally indolent and self-limited, but it carries a poor or fatal prognosis when it is advanced or when it involves and compresses vital structures. We present a case of Rosai-Dorfman disease affecting the pulmonary arteries in a 22-year-old woman with severe, symptomatic right heart failure.
Walters
Dustin M
DM
Department of Surgery, University of Virginia, Charlottesville, Virginia 22908, USA. dmw7f@virginia.edu
Dunnington
Gansevoort H
GH
Dustin
Simone M
SM
Frierson
Henry F
HF
Peeler
Benjamin B
BB
Kozower
Benjamin D
BD
Ailawadi
Gorav
G
Jones
David R
DR
Lau
Christine L
CL
D001706:Biopsy; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D015618:Histiocytosis, Sinus / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D011651:Pulmonary Artery; D015899:Tomography, Emission-Computed, Single-Photon; D014057:Tomography, X-Ray Computed; D014652:Vascular Diseases / Q000175:diagnosis* / Q000601:surgery; D014656:Vascular Surgical Procedures / Q000379:methods*; D055815:Young Adult