Successful staged Fontan completion for truncus arteriosus with hypoplastic left ventricle.
We report a case of truncus arteriosus type II with a large outlet ventricular septal defect and a hypoplastic left ventricle. The first-stage palliation was the removal of both branch pulmonary arteries from the ascending aorta, patch augmentation of the pulmonary artery confluence, and modified Blalock-Taussig shunt at age 1 month. The second stage palliation was a bidirectional Glenn at 6 months. The final stage was an extracardiac Fontan at age 3 years. Eight years later, the patient is doing well, with an unobstructed Fontan pathway and mild-to-moderate truncal valve insufficiency.
Hoashi
Takaya
T
Division of Pediatric Cardiovascular Surgery, Department of Surgery, University of Michigan Medical School, Ann Arbor, Michigan, USA.
Bove
Edward L
EL
Ohye
Richard G
RG
D019917:Blood Vessel Prosthesis Implantation; D002648:Child; D002675:Child, Preschool; D002932:Cineangiography; D004452:Echocardiography; D015150:Echocardiography, Doppler; D005500:Follow-Up Studies; D018729:Fontan Procedure / Q000379:methods*; D006344:Heart Septal Defects, Atrial / Q000175:diagnosis / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000175:diagnosis / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis / Q000601:surgery*; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D010166:Palliative Care; D011138:Polytetrafluoroethylene; D011183:Postoperative Complications / Q000175:diagnosis; D011651:Pulmonary Artery / Q000601:surgery; D012086:Reoperation; D014339:Truncus Arteriosus, Persistent / Q000175:diagnosis / Q000601:surgery*; D014683:Vena Cava, Superior / Q000601:surgery
D011138:Polytetrafluoroethylene