[Behçet disease with isolated ACTH deficiency].
We report a case of a patient with longstanding Behçet disease, with neurological symptoms predominantly, who became hospitalized for adrenal insufficiency, caused by isolated deficiency of corticotropin (DAACTH). DAACTH is a typical characteristic of hypophysitis, reported in association with many autoimmune diseases. Nevertheless, hypothalamic-pituitary injury in Behçet disease is exceptional. We review the literature and possible mechanisms of this association until now not reported.
Sánchez Sobrino
Paula
P
Servicio de Endocrinología y Nutrición, Hospital Xeral, Complexo Hospitalario Universitario de Vigo (CHUVI), Vigo, Pontevedra, España. paula.sanchez.sobrino.82@gmail.com
Páramo Fernández
Concepción
C
Lamas Ferreiro
José Luis
JL
Mantiñán Gil
Beatriz
B
Palmeiro Carballeira
Regina
R
García-Mayor
Ricardo Víctor
RV
D000324:Adrenocorticotropic Hormone / Q000172:deficiency*; D000368:Aged; D001528:Behcet Syndrome / Q000209:etiology*; D006801:Humans; D008297:Male
D000324:Adrenocorticotropic Hormone