Anomalous vasculature in Mayer-Rokitansky-Kuster-Hauser syndrome.
OBJECTIVE
To report a case of unique anomalous pelvic vasculature in a woman with Müllerian agenesis.


METHODS
Case report.


METHODS
University hospital.


METHODS
A 61-year-old woman with Müllerian agenesis and stage IIIc papillary serous ovarian cancer.


METHODS
Surgery was performed, including bilateral salpingo-oophorectomy, omentectomy, right terminal ileum and right ascending colon resection, ileoascending/transverse colon reanastomosis, and debulking of pelvic plaques along bilateral ureters. The patient had subsequent chemotherapy with taxane and platinum agents and at the time of writing was in remission.


METHODS
None.


RESULTS
Absence of the uterus was confirmed; rudimentary uterine horns and associated fallopian tubes and ovaries were noted bilaterally. The right ureter coursed below and behind the right common iliac artery, which did not bifurcate into external and internal arteries at the pelvic brim. Instead there was only an external iliac artery that gave off a pelvic branch just before the inguinal ligament. On the left, there was only an internal iliac artery that gave off an external branch after diving into the pelvis.


CONCLUSIONS
It is possible that the aberrant vasculature was partially responsible for the absence of the uterus. Preoperatively, it is important to recognize the possibility of abnormal pelvic vasculature in patients with Müllerian agenesis.
Bailey
Amelia P
AP
Department of Obstetrics & Gynecology, University of Virginia Health System, Charlottesville, Virginia 22903, USA. ameliabailey@virginia.edu
Young
Jennifer L
JL
Nigrini
Elisabeth
E
Modesitt
Susan C
SC
D005260:Female; D006801:Humans; D008875:Middle Aged; D009095:Mullerian Ducts / Q000002:abnormalities* / Q000098:blood supply* / Q000601:surgery; D010051:Ovarian Neoplasms / Q000175:diagnosis* / Q000601:surgery; D013577:Syndrome; D054079:Vascular Malformations / Q000175:diagnosis* / Q000601:surgery