Successful surgical treatment of atrial fibrillation, mitral regurgitation, and aortic root aneurysm in a patient with classical type Ehlers-Danlos syndrome.
Herein, we present an unusual case of a 48-year-old patient with Ehlers-Danlos syndrome (classic type) with multiple cardiovascular pathologies, including mitral regurgitation, a dilated aortic root, and chronic atrial fibrillation. A complex mitral valve repair, modified cryo-Maze procedure, and aortic valve-sparing operation (reimplantation) were performed, which were further complicated by the patient's fragile tissues. The patient was discharged on postoperative day 10 in good health with normal mitral and aortic valve function. We believe that this is the first report of such an extensive cardiac procedure in a patient with Ehlers-Danlos syndrome.
Sauer
Matthias
M
Department of Cardiac Surgery, Heart Center Leipzig, University of Leipzig, Leipzig, Germany. matthiassauer@yahoo.de
Borger
Michael A
MA
Seeburger
Joerg
J
Mohr
Friedrich W
FW
D017545:Aortic Aneurysm, Thoracic / Q000209:etiology / Q000601:surgery*; D001281:Atrial Fibrillation / Q000209:etiology / Q000601:surgery*; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005500:Follow-Up Studies; D006801:Humans; D008875:Middle Aged; D008944:Mitral Valve Insufficiency / Q000209:etiology / Q000601:surgery*