title: [Intraocular medulloepithelioma - series of 10 cases and review of the literature].
abstract: Intraocular medulloepithelioma is an extremely rare unilateral intraocular tumor arising from the nonpigmented ciliary epithelium. Medulloepitheliomas may be classified as benign and malignant and as teratoid and nonteratoid tumors. As a rule a long latency period occurs after first symptoms until the final diagnosis of a medulloepithelioma is made. Differential diagnosis includes in particular unilateral retinoblastoma. Intraocular medulloepithelioma may occur as masquerade-syndrome simulating uveitis. We present 10 patients with intraocular medulloepithelioma. In 7 of these patients the eye had to be enucleated. Metastasis did not occur, but epiretinal tumor seeding did occur in one patient. In one of the 3 not enucleated eyes, ruthenium-106 brachytherapy could salvage the tumor containing eye.
authors.affiliation: Zentrum für Augenheilkunde, Universitätsklinikum Essen. markus.holdt@uk-essen.de
authors.forename: M
authors.initials: M
authors.lastname: Holdt
authors.forename: C
authors.initials: C
authors.lastname: Jurklies
authors.forename: A
authors.initials: A
authors.lastname: Schueler
authors.forename: F
authors.initials: F
authors.lastname: Otterbach
authors.forename: N
authors.initials: N
authors.lastname: Bornfeld
mesh_terms: D001918:Brachytherapy / Q000379:methods*; D015353:Eye Enucleation / Q000379:methods*; D005134:Eye Neoplasms / Q000628:therapy*; D005260:Female; D006801:Humans; D008297:Male; D018242:Neuroectodermal Tumors, Primitive / Q000628:therapy*; D016896:Treatment Outcome