Epithelioid hemangioendothelioma of the liver with metastatic coeliac lymph nodes in an 11-year-old boy.
Epithelioid hemangioendothelioma of the liver is a very rare vascular tumour in children with intermediate malignant potential. We present a case in which the typical imaging appearances of coalescent peripheral hepatic masses with capsular retraction contributed to the diagnosis. A positron emission tomography-CT (PET-CT) procedure was performed in staging the disease with a strong suspicion of coeliac nodal involvement confirmed after laparotomy and histological analysis. Our case is unique because of the rarity of the disease, the young age of the child, and proven nodal metastases at initial diagnosis. The use of PET-CT allows better staging at initial diagnosis and thus better management with improved follow-up in these patients.
Da Ines
David
D
Service de Radiologie et Imagerie Médicale, Hôtel Dieu, CHU Clermont-Ferrand, Bd Léon Malfreyt, Clermont-Ferrand 63058, France. ddaines@chu-clermontferrand.fr
Petitcolin
Virginie
V
Joubert-Zakeyh
Juliette
J
Demeocq
Francois
F
Garcier
Jean-Marc
JM
D000005:Abdomen / Q000000981:diagnostic imaging; D002648:Child; D018323:Hemangioendothelioma, Epithelioid / Q000175:diagnosis* / Q000556:secondary*; D006801:Humans; D008113:Liver Neoplasms / Q000175:diagnosis*; D008207:Lymphatic Metastasis; D008297:Male; D049268:Positron-Emission Tomography; D011860:Radiography, Abdominal; D013382:Subtraction Technique; D014057:Tomography, X-Ray Computed