title: Rosai-Dorfman disease presenting as a pulmonary artery mass.
abstract: Rosai-Dorfman disease is rare and typically presents with cervical lymphadenopathy, but may manifest as extranodal disease. This disease is generally indolent and self-limited, but it carries a poor or fatal prognosis when it is advanced or when it involves and compresses vital structures. We present a case of Rosai-Dorfman disease affecting the pulmonary arteries in a 22-year-old woman with severe, symptomatic right heart failure.
authors.affiliation: Department of Surgery, University of Virginia, Charlottesville, Virginia 22908, USA. dmw7f@virginia.edu
authors.forename: Dustin M
authors.initials: DM
authors.lastname: Walters
authors.forename: Gansevoort H
authors.initials: GH
authors.lastname: Dunnington
authors.forename: Simone M
authors.initials: SM
authors.lastname: Dustin
authors.forename: Henry F
authors.initials: HF
authors.lastname: Frierson
authors.forename: Benjamin B
authors.initials: BB
authors.lastname: Peeler
authors.forename: Benjamin D
authors.initials: BD
authors.lastname: Kozower
authors.forename: Gorav
authors.initials: G
authors.lastname: Ailawadi
authors.forename: David R
authors.initials: DR
authors.lastname: Jones
authors.forename: Christine L
authors.initials: CL
authors.lastname: Lau
mesh_terms: D001706:Biopsy; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D015618:Histiocytosis, Sinus / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D011651:Pulmonary Artery; D015899:Tomography, Emission-Computed, Single-Photon; D014057:Tomography, X-Ray Computed; D014652:Vascular Diseases / Q000175:diagnosis* / Q000601:surgery; D014656:Vascular Surgical Procedures / Q000379:methods*; D055815:Young Adult