[Intraocular medulloepithelioma - series of 10 cases and review of the literature].
Intraocular medulloepithelioma is an extremely rare unilateral intraocular tumor arising from the nonpigmented ciliary epithelium. Medulloepitheliomas may be classified as benign and malignant and as teratoid and nonteratoid tumors. As a rule a long latency period occurs after first symptoms until the final diagnosis of a medulloepithelioma is made. Differential diagnosis includes in particular unilateral retinoblastoma. Intraocular medulloepithelioma may occur as masquerade-syndrome simulating uveitis. We present 10 patients with intraocular medulloepithelioma. In 7 of these patients the eye had to be enucleated. Metastasis did not occur, but epiretinal tumor seeding did occur in one patient. In one of the 3 not enucleated eyes, ruthenium-106 brachytherapy could salvage the tumor containing eye.
Holdt
M
M
Zentrum für Augenheilkunde, Universitätsklinikum Essen. markus.holdt@uk-essen.de
Jurklies
C
C
Schueler
A
A
Otterbach
F
F
Bornfeld
N
N
D001918:Brachytherapy / Q000379:methods*; D015353:Eye Enucleation / Q000379:methods*; D005134:Eye Neoplasms / Q000628:therapy*; D005260:Female; D006801:Humans; D008297:Male; D018242:Neuroectodermal Tumors, Primitive / Q000628:therapy*; D016896:Treatment Outcome