Odontogenic myxofibroma synchronous with primary angiosarcoma of the spleen.
Odontogenic myxofibroma of the temporomandibular joint (TMJ) is a rare tumour; moreover, primary splenic angiosarcoma (PAS) in paediatric patients is extremely rare. We report on a 15-year-old boy who presented with right TMJ swelling and subsequently developed epigastric and right upper quadrant pain. The TMJ swelling proved to be odontogenic myxofibroma and the abdominal pain was a result of primary splenic angiosarcoma with hepatic metastasis. We report for the first time the synchronous presentation of PAS and odontogenic myxofibroma in a paediatric patient, and we describe the radiological features along with the histological diagnosis and clinical outcome. Uptake in (18)F-2-fluoro-2-deoxy-D-glucose positron emission tomography is also described for the first time for both these tumours.
Hadidy
A
A
Department of Radiology and Nuclear Medicine, Jordan University Hospital, Amman, Jordan. ahadidy@ju.edu.jo
Alsharif
A
A
Sheikh-Ali
R
R
Abukhalaf
M
M
Awidi
A
A
Abukaraki
A
A
Nimri
C
C
Omari
A
A
D000293:Adolescent; D001859:Bone Neoplasms / Q000556:secondary; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005350:Fibroma / Q000175:diagnosis* / Q000473:pathology; D006394:Hemangiosarcoma / Q000175:diagnosis*; D006801:Humans; D008113:Liver Neoplasms / Q000556:secondary; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis*; D009808:Odontogenic Tumors / Q000175:diagnosis* / Q000473:pathology; D013160:Splenic Neoplasms / Q000175:diagnosis*; D013705:Temporomandibular Joint Disorders / Q000175:diagnosis* / Q000473:pathology