Rosette-forming glioneuronal tumor (RGNT) of the fourth ventricle: Case report and review of literature.
Rosette-forming glioneuronal tumor (RGNT) of the fourth ventricle has been identified as a novel and distinctive type of primary central nervous system neoplasm. In this report, we present a case with RGNT arising from the right cerebellar hemisphere. A 30-year-old female patient complained of headache for a five-year duration. Preoperative MRI revealed a well-circumscribed, cystic-solid lesion with hypo-intensity on T1-weighted image, hyper-intensity on T2-weighted image, and significant dot-like enhancement after IV contrast. Gross total resection was achieved in this case via suboccipital retro-sigmoidal approach, and RGNT was confirmed in the final histopathological diagnosis. RGNT of the fourth ventricle is a rare, benign tumor with an excellent prognosis. Operation is recommended as the prior protocol of treatment, and the follow-up MRI is necessary to evaluate the long-term prognostic effects. Currently, only one case of progression or recurrence has been reported in the postoperative course.
Department of Neurosurgery, Huashan Hospital affiliated to Fudan University, Shanghai Neurosurgical Center, The 3rd ward, 12 Middle Wulumuqi Road, Shanghai 200040, PR China.
ShiHai
S
Luan
DongXiao
D
Zhuang
LinLin
L
Sun
Feng-Ping
FP
Huang
D000328:Adult; D002528:Cerebellar Neoplasms / Q000473:pathology; D002531:Cerebellum / Q000473:pathology; D002551:Cerebral Ventricle Neoplasms / Q000473:pathology* / Q000601:surgery; D005260:Female; D020546:Fourth Ventricle / Q000473:pathology* / Q000601:surgery; D005910:Glioma / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D019635:Neurosurgical Procedures; D012397:Rosette Formation; D016896:Treatment Outcome