Primary cutaneous Ewing's sarcoma/primitive neuroectodermal tumor manifesting numerous small and huge ulcerated masses: its complete remission by chemotherapy and magnetic resonance imaging findings.
Extraskeletal Ewing's sarcoma (ES) and primitive neuroectodermal tumor (PNET) are widely regarded as clinically and histologically identical tumors which consist of small blue round cells. Extraskeletal ESs/PNETs usually occur in the deep soft tissues of the paraspinal region, chest wall, or lower extremities. However, superficially located cases, so-called cutaneous ESs/PNETs, are exceedingly rare, and the vast majority of the reported cases present as a single small mass. We present magnetic resonance imaging (MRI) findings and clinical course of a unique case of primary cutaneous ES/PNET presenting as numerous huge masses with severe ulceration on them.
Bahk
Won-Jong
WJ
Department of Orthopedic Surgery, Uijeongbu St Mary's Hospital, The Catholic University of Korea, Uijeongbu, Korea. wjbahk@catholic.ac.kr
Chang
Eun-Deok
ED
Bae
Jung Min
JM
Chun
Kyung-Ah
KA
Lee
An-Hee
AH
Rho
Sang-Young
SY
Kim
Jin Woo
JW
D000970:Antineoplastic Agents / Q000008:administration & dosage*; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods*; D008297:Male; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D017599:Neuroectodermal Tumors / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D012512:Sarcoma, Ewing / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D012878:Skin Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D016896:Treatment Outcome; D014456:Ulcer / Q000175:diagnosis* / Q000209:etiology / Q000517:prevention & control
D000970:Antineoplastic Agents