A case of incidentally detected IgG4-related sclerosing disease involving inflammatory abdominal aortic aneurysm and autoimmune pancreatitis.
A 59-year-old asymptomatic man was incidentally found to have a periaortic mass and an elevated serum amylase level during his medical check-up. Additional findings, such as infiltration of immunoglobulin G4 (IgG4)-producing plasma cells in the mass lesion, elevation of serum IgG4 (1000 mg/dl), and pancreatic duct narrowing as evidenced on a magnetic resonance cholangiopancreatography scan, confirmed the diagnosis as retroperitoneal fibrosis complicated with autoimmune pancreatitis. The patient responded favorably to steroid treatment before the appearance of symptoms.
Department of Medicine, Japan Self-Defense Force Central Hospital, 1-2-24 Ikejiri, Setagaya, Tokyo 154-8532, Japan. yasmatsuki@aol.com
Yasunori
Y
Matsuki
Kimiya
K
Sato
Akira
A
Fujikawa
Yukishige
Y
Kyoto
Hiroshi
H
Hashimoto
Yukiya
Y
Hakozaki
D017544:Aortic Aneurysm, Abdominal / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D001327:Autoimmune Diseases / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D033162:Incidental Findings; D008297:Male; D008875:Middle Aged; D050500:Pancreatitis, Chronic / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D012185:Retroperitoneal Fibrosis / Q000150:complications / Q000175:diagnosis* / Q000276:immunology
D007074:Immunoglobulin G