Bilateral papillary cystadenoma of the mesosalpinx: a rare manifestation of Von Hippel-Lindau disease.
We report a rare case of a woman with bilateral papillary cystadenomata of the broad ligament with von Hippel-Lindau disease (VHL) (other manifestations: capillary hemangioblastomas of the spinal cord). Patient surveillance is important, because in the course of VHL-associated tumors malignant lesions may arise that are relevant for the prognosis.
Zanotelli
Diana Bätschmann
DB
Department of Obstetrics and Gynecology, University Hospital Basel, Spitalstrasse 21, Basel, Switzerland.
Bruder
Elisabeth
E
Wight
Edward
E
Troeger
Carolyn
C
D018292:Cystadenoma, Papillary / Q000209:etiology* / Q000235:genetics / Q000473:pathology; D005185:Fallopian Tube Neoplasms / Q000209:etiology* / Q000235:genetics / Q000473:pathology; D005260:Female; D018325:Hemangioblastoma / Q000209:etiology*; D006801:Humans; D017354:Point Mutation; D013120:Spinal Cord Neoplasms / Q000209:etiology*; D013904:Thoracic Vertebrae; D051794:Von Hippel-Lindau Tumor Suppressor Protein / Q000235:genetics; D055815:Young Adult; D006623:von Hippel-Lindau Disease / Q000150:complications* / Q000175:diagnosis* / Q000235:genetics
D051794:Von Hippel-Lindau Tumor Suppressor Protein; C497446:VHL protein, human