[Left ventricular non-compaction in an infant with congenital heart defect].
Non-compaction of the left ventricle (NCLV) was categorised as unclassified cardiomyopathy by the World Health Organization in 1995. Over the last decade this condition has been identified as a distinct form of cardiomyopathy and a genetically heterogeneous disorder. Clinically, this may be coupled with the loss of contractility, arrhythmia, and thromboembolism. The prognosis in a symptomatic patient is generally poor, with progression to chronic heart failure and death, including sudden death. We report a case of a child with NCLV and coexisting hemodynamic significant ventricular septal defect.
Klinika Kardiologii Dzieciecej i Wad Wrodzonych Serca, Gdański Uniwersytet Medyczny, 80-211 Gdańsk. joannak@amg.gda.pl
Joanna
J
Kwiatkowska
Janina
J
Aleszewicz-Baranowska
Jan
J
Ereciński
D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000628:therapy; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000175:diagnosis* / Q000628:therapy; D006801:Humans; D007223:Infant; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis* / Q000628:therapy; D011379:Prognosis