A case of incidentally detected IgG4-related sclerosing disease involving inflammatory abdominal aortic aneurysm and autoimmune pancreatitis.
A 59-year-old asymptomatic man was incidentally found to have a periaortic mass and an elevated serum amylase level during his medical check-up. Additional findings, such as infiltration of immunoglobulin G4 (IgG4)-producing plasma cells in the mass lesion, elevation of serum IgG4 (1000 mg/dl), and pancreatic duct narrowing as evidenced on a magnetic resonance cholangiopancreatography scan, confirmed the diagnosis as retroperitoneal fibrosis complicated with autoimmune pancreatitis. The patient responded favorably to steroid treatment before the appearance of symptoms.
Matsuki
Yasunori
Y
Department of Medicine, Japan Self-Defense Force Central Hospital, 1-2-24 Ikejiri, Setagaya, Tokyo 154-8532, Japan. yasmatsuki@aol.com
Sato
Kimiya
K
Fujikawa
Akira
A
Kyoto
Yukishige
Y
Hashimoto
Hiroshi
H
Hakozaki
Yukiya
Y
D017544:Aortic Aneurysm, Abdominal / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D001327:Autoimmune Diseases / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D033162:Incidental Findings; D008297:Male; D008875:Middle Aged; D050500:Pancreatitis, Chronic / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D012185:Retroperitoneal Fibrosis / Q000150:complications / Q000175:diagnosis* / Q000276:immunology
D007074:Immunoglobulin G