title: Stromal tumor of the ampulla of vater: report of a case and systematic review of reported cases.
abstract: BACKGROUND
  Gastrointestinal stromal tumours are a large category of primary no epithelial neoplasms of the digestive tract. The localization of stromal tumours in the ampulla of Vater (STAV) is very rare.
  
  
  OBJECTIVE
  The aim of this study was to describe clinical, endoscopic and therapeutic particularities of STAV.
  
  
  METHODS
  We reported a new case and we carried out an extensive electronic search for the relevant literature using Medline. Key words used were "ampulla of Vater" and "Gastrointestinal stromal tumor" and "CD 117". With our case, we collected seven other cases in the literature.
  
  
  RESULTS
  The analysis of the sample of these eight cases leads us to propose the following conclusions. STAV is a tumor of adult after the age of fifty. There is no specific symptomatology. Gastroduodenal endoscopy with biopsies and immunoassaying allows positive preoperative diagnosis in the 5 cases. Treatment should be duodenopancreatectomy since the tumor is often malignant (5 cases).
authors.affiliation: Surgical unit A, Charles Nicolle Hospital, Tunis, Tunisia.
authors.forename: Hichem
authors.initials: H
authors.lastname: Jerraya
authors.forename: Riadh
authors.initials: R
authors.lastname: Bel Haj Salah
authors.forename: Khalil
authors.initials: K
authors.lastname: Ben Mena
authors.forename: Karim
authors.initials: K
authors.lastname: Haouet
authors.forename: Abdeljelil
authors.initials: A
authors.lastname: Zaouche
mesh_terms: D000328:Adult; D000367:Age Factors; D000368:Aged; D014670:Ampulla of Vater / Q000000981:diagnostic imaging / Q000473:pathology; D001706:Biopsy; D016099:Endoscopy, Gastrointestinal; D005260:Female; D046152:Gastrointestinal Stromal Tumors / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D007118:Immunoassay; D008297:Male; D008875:Middle Aged; D016577:Pancreaticoduodenectomy; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography