Peritoneal pseudomyxoma arising from the urachus.
Pseudomyxoma peritonei (PMP) arising from urachal tumors is extremely rare. To our knowledge, natural history, tumor biological behaviour, morbidity, treatment, and prognosis of PMP arising from the urachus are determined by the associated PMP. Management of urachal tumors with associated PMP should be based on aggressive locorregional therapy with cytoreductive surgery and hyperthermic intraperitoneal chemotherapy, similar to PMP arising from other origins.
Martínez
Alejandra
A
Institut Claudius Regaud, Surgery, 20-24, Rue du Pont Saint Pierre, 31052 Toulouse, France. martinez_a.alejandra@claudiusregaud.fr
Ferron
Gwénael
G
Mery
Eliane
E
Gladieff
Laurance
L
Delord
Jean Pierre
JP
Querleu
Denis
D
D000230:Adenocarcinoma / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D000328:Adult; D018282:Cystadenocarcinoma, Mucinous / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D010534:Peritoneal Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D011553:Pseudomyxoma Peritonei / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D035583:Rare Diseases / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D019233:Retreatment; D014057:Tomography, X-Ray Computed; D001749:Urinary Bladder Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*