[Febrile ulceronecrotic Mucha-Habermann disease with exuberant mucosal involvement: case report].
Pityriasis lichenoides is a rare idiopathic cutaneous disorder, with a clinical-histopathological spectrum comprising the acute varioliform form (Mucha-Habermann's disease), its febrile ulceronecrotic variant, and its chronic form. Systemic manifestations may occur in the febrile ulceronecrotic variant, with reports of adult mortality. The case of a young male patient with clinical and histopathological diagnosis of Mucha-Habermann's disease, febrile ulceronecrotic variant, with severe mucosal involvement - an occasional incidence even in the most severe forms of pityriasis lichenoides - is presented. In addition to the atypical clinical aspect, an excellent therapeutic result is shown with the association of prednisone and methotrexate.
Cumming
Moema Mignac
MM
FMRP, USP, Ribeirão Preto, SP, Brasil.
Salathiel
Adriana S
AS
Paino
Mário Alberto S
MA
Delort
Sérgio
S
Roselino
Ana Maria
AM
D005334:Fever / Q000209:etiology; D006801:Humans; D008297:Male; D009059:Mouth Diseases / Q000209:etiology* / Q000473:pathology; D009092:Mucous Membrane / Q000473:pathology; D009336:Necrosis; D010409:Penile Diseases / Q000209:etiology* / Q000473:pathology; D017514:Pityriasis Lichenoides / Q000150:complications* / Q000473:pathology; D012883:Skin Ulcer / Q000209:etiology; D055815:Young Adult