title: [Febrile ulceronecrotic Mucha-Habermann disease with exuberant mucosal involvement: case report].
abstract: Pityriasis lichenoides is a rare idiopathic cutaneous disorder, with a clinical-histopathological spectrum comprising the acute varioliform form (Mucha-Habermann's disease), its febrile ulceronecrotic variant, and its chronic form. Systemic manifestations may occur in the febrile ulceronecrotic variant, with reports of adult mortality. The case of a young male patient with clinical and histopathological diagnosis of Mucha-Habermann's disease, febrile ulceronecrotic variant, with severe mucosal involvement - an occasional incidence even in the most severe forms of pityriasis lichenoides - is presented. In addition to the atypical clinical aspect, an excellent therapeutic result is shown with the association of prednisone and methotrexate.
authors.affiliation: FMRP, USP, Ribeirão Preto, SP, Brasil.
authors.forename: Moema Mignac
authors.initials: MM
authors.lastname: Cumming
authors.forename: Adriana S
authors.initials: AS
authors.lastname: Salathiel
authors.forename: Mário Alberto S
authors.initials: MA
authors.lastname: Paino
authors.forename: Sérgio
authors.initials: S
authors.lastname: Delort
authors.forename: Ana Maria
authors.initials: AM
authors.lastname: Roselino
mesh_terms: D005334:Fever / Q000209:etiology; D006801:Humans; D008297:Male; D009059:Mouth Diseases / Q000209:etiology* / Q000473:pathology; D009092:Mucous Membrane / Q000473:pathology; D009336:Necrosis; D010409:Penile Diseases / Q000209:etiology* / Q000473:pathology; D017514:Pityriasis Lichenoides / Q000150:complications* / Q000473:pathology; D012883:Skin Ulcer / Q000209:etiology; D055815:Young Adult