title: A composite pheochromocytoma/ganglioneuroblastoma of the adrenal gland.
abstract: A 9-year-old female presented with a large abdominal mass. At surgery, the mass was noted to arise from the right adrenal gland. As the mass was manipulated, the patient developed severe hypertension. The final diagnosis was a cystic composite-pheochromocytoma/ganglioneuroblastoma. This compound adrenal tumor is only the fourth case reported in a child. Because composite pheochromocytomas are rare in the pediatric population, the management, optimal surveillance schedule and outcomes have not been characterized.
authors.affiliation: Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin 53226, USA. ecarroll@mcw.edu
authors.forename: Elizabeth Lee
authors.initials: EL
authors.lastname: Thiel
authors.forename: Beth A
authors.initials: BA
authors.lastname: Trost
authors.forename: Richard L
authors.initials: RL
authors.lastname: Tower
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery; D002648:Child; D005260:Female; D018305:Ganglioneuroblastoma / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007150:Immunohistochemistry; D009378:Neoplasms, Multiple Primary / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery; D010673:Pheochromocytoma / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery