A composite pheochromocytoma/ganglioneuroblastoma of the adrenal gland.
A 9-year-old female presented with a large abdominal mass. At surgery, the mass was noted to arise from the right adrenal gland. As the mass was manipulated, the patient developed severe hypertension. The final diagnosis was a cystic composite-pheochromocytoma/ganglioneuroblastoma. This compound adrenal tumor is only the fourth case reported in a child. Because composite pheochromocytomas are rare in the pediatric population, the management, optimal surveillance schedule and outcomes have not been characterized.
Thiel
Elizabeth Lee
EL
Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin 53226, USA. ecarroll@mcw.edu
Trost
Beth A
BA
Tower
Richard L
RL
D000310:Adrenal Gland Neoplasms / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery; D002648:Child; D005260:Female; D018305:Ganglioneuroblastoma / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007150:Immunohistochemistry; D009378:Neoplasms, Multiple Primary / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery; D010673:Pheochromocytoma / Q000473:pathology* / Q000503:physiopathology / Q000601:surgery