title: Peritoneal pseudomyxoma arising from the urachus.
abstract: Pseudomyxoma peritonei (PMP) arising from urachal tumors is extremely rare. To our knowledge, natural history, tumor biological behaviour, morbidity, treatment, and prognosis of PMP arising from the urachus are determined by the associated PMP. Management of urachal tumors with associated PMP should be based on aggressive locorregional therapy with cytoreductive surgery and hyperthermic intraperitoneal chemotherapy, similar to PMP arising from other origins.
authors.affiliation: Institut Claudius Regaud, Surgery, 20-24, Rue du Pont Saint Pierre, 31052 Toulouse, France. martinez_a.alejandra@claudiusregaud.fr
authors.forename: Alejandra
authors.initials: A
authors.lastname: Martínez
authors.forename: Gwénael
authors.initials: G
authors.lastname: Ferron
authors.forename: Eliane
authors.initials: E
authors.lastname: Mery
authors.forename: Laurance
authors.initials: L
authors.lastname: Gladieff
authors.forename: Jean Pierre
authors.initials: JP
authors.lastname: Delord
authors.forename: Denis
authors.initials: D
authors.lastname: Querleu
mesh_terms: D000230:Adenocarcinoma / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D000328:Adult; D018282:Cystadenocarcinoma, Mucinous / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D010534:Peritoneal Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D011553:Pseudomyxoma Peritonei / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D035583:Rare Diseases / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*; D019233:Retreatment; D014057:Tomography, X-Ray Computed; D001749:Urinary Bladder Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery*