Kawashima procedure after staged unifocalizations in asplenia with major aortopulmonary collateral arteries.
We report a Kawashima procedure (total cavopulmonary shunt) successfully carried out for asplenia syndrome, pulmonary atresia, and major aortopulmonary collateral arteries. At the age of 8, the patient underwent staged bilateral unifocalizations using confluent central pulmonary arteries concomitant with bilateral modified Blalock-Taussig shunts. As the result of an interrupted inferior vena cava with azygous continuation, the patient required a Kawashima procedure with augmentation of the central pulmonary arteries for definitive palliation 1 year later. Cyanosis, respiratory distress, and ventricular function improved.
Ban
Yukiko
Y
Department of Cardiovascular Surgery, University of Tsukuba, Tsukuba, Japan.
Noma
Mio
M
Horigome
Hitoshi
H
Kato
Hideyuki
H
Tokunaga
Chiho
C
Sakakibara
Yuzuru
Y
Hiramatsu
Yuji
Y
D001013:Aorta, Thoracic / Q000002:abnormalities; D013504:Cardiovascular Surgical Procedures / Q000379:methods; D002648:Child; D003097:Collateral Circulation; D005260:Female; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D011651:Pulmonary Artery / Q000601:surgery*; D018633:Pulmonary Atresia / Q000601:surgery*; D011652:Pulmonary Circulation; D013154:Spleen / Q000002:abnormalities*