Composite adrenal phaeochromocytoma-ganglioneuroma causing watery diarrhoea, hypokalaemia and achlorhydria syndrome.
The watery diarrhoea, hypokalaemia and achlorhydria syndrome is a rare cause of secretory diarrhoea. In this case report, we highlight a young female with watery diarrhoea, hypokalaemia and achlorhydria syndrome as a consequence of a vasoactive intestinal peptide producing composite adrenal phaeochromocytoma-ganglioneuroma. She made a complete recovery after curative surgical resection.
George
Deepu J
DJ
Division of Gastroenterology, Department of Medicine, Groote Schuur Hospital, Cape Town, South Africa.
Watermeyer
Gill A
GA
Levin
Dion
D
Epstein
David
D
Ross
Ian L
IL
Scholz
Barbara U
BU
Setshedi
Matshiko
M
Locketz
Michael
M
Dittrich
Cornelli
C
Shaw
John
J
Krige
Jake E
JE
D000126:Achlorhydria / Q000209:etiology*; D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000378:metabolism / Q000601:surgery; D003967:Diarrhea / Q000209:etiology*; D005260:Female; D005729:Ganglioneuroma / Q000150:complications* / Q000601:surgery; D006801:Humans; D007008:Hypokalemia / Q000209:etiology*; D010673:Pheochromocytoma / Q000150:complications* / Q000378:metabolism / Q000601:surgery; D014660:Vasoactive Intestinal Peptide / Q000378:metabolism; D055815:Young Adult
D014660:Vasoactive Intestinal Peptide