title: Systemic juvenile xanthogranuloma with fatal outcome.
abstract: Juvenile xanthogranuloma is a benign and self-limited disease which usually appears in the skin of children. Visceral involvement has been rarely reported, as has fatal outcome in some affected individuals. We report a case of systemic juvenile xanthogranuloma in a female newborn with mainly skin, bone marrow, and liver involvement, leading to death at the age of 2 months.
authors.affiliation: Department of Pathology, Hospital del Niño Jesús, 28009 Madrid, Spain.
authors.forename: Daniel
authors.initials: D
authors.lastname: Azorín
authors.forename: Antonio
authors.initials: A
authors.lastname: Torrelo
authors.forename: Alvaro
authors.initials: A
authors.lastname: Lassaletta
authors.forename: Inmaculada
authors.initials: I
authors.lastname: de Prada
authors.forename: Isabel
authors.initials: I
authors.lastname: Colmenero
authors.forename: Trinidad
authors.initials: T
authors.lastname: Contra
authors.forename: Imelda
authors.initials: I
authors.lastname: González-Mediero
mesh_terms: D001706:Biopsy; D017809:Fatal Outcome; D005260:Female; D006644:Histiocytes / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008099:Liver / Q000473:pathology; D017093:Liver Failure / Q000473:pathology*; D010198:Pancytopenia / Q000473:pathology*; D012867:Skin / Q000473:pathology*; D014972:Xanthogranuloma, Juvenile / Q000473:pathology*