[A systemic amyloidosis presenting as a tracheobronchial amyloidosis].
Amyloidosis is a spectrum of disease characterized by the abnormal deposition of fibril amyloid-related proteins in the extracellular space. The most common types of amyloidosis are AL and AA amyloidosis. Amyloidosis is also classified according to the extent of the deposition as systemic or localized. Respiratory amyloidosis is classified as laryngeal, tracheobronchial or parenchymal amyloidosis. Tracheobronchial amyloidosis is classically known as a rare manifestation of the localized disease. A few cases only of systemic amyloidosis presenting as a tracheobronchial disease have been reported. We here report a 26-year-old man who presented with hemoptysis related to a systemic tracheal primary amyloidosis.
Haddad
F
F
Département de médecine interne, Hôtel-Dieu de France, Achrafieh, rue Adib Ishac, Beyrouth, Liban.
Jammal
M
M
Azar
H
H
Mallat
S
S
Nasr
F
F
Dabar
G
G
Ghorra
C
C
D000328:Adult; D000686:Amyloidosis / Q000150:complications*; D001982:Bronchial Diseases / Q000209:etiology*; D006801:Humans; D008297:Male; D014133:Tracheal Diseases / Q000209:etiology*