Endocardial fibroelastosis of the right ventricle and tricuspid valve in a young adult with Behcet's disease.
Endocardial fibroelastosis is characterized by massive proliferation of collagenous and elastic tissue, in which the pathological process is restricted to the endocardium. In this report, we present the case of a 20-year-old man with Behcet's disease and endocardial fibroelastosis of the right ventricle involving tricuspid valve resulting in a tumor mass that was resected along with tricuspid valve replacement. The clinical and pathological features of this rare entity are reviewed.
Ucak
Alper
A
Department of Cardiovascular Surgery, GATA Haydarpasa Education Hospital, Istanbul, Turkey.
Onan
Burak
B
Inan
Kaan
K
Ugur
Murat
M
Kucukodaci
Zafer
Z
Yilmaz
Ahmet Turan
AT
D000328:Adult; D001528:Behcet Syndrome / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D004452:Echocardiography; D004695:Endocardial Fibroelastosis / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D006338:Heart Neoplasms / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D006350:Heart Valve Prosthesis; D019918:Heart Valve Prosthesis Implantation; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000473:pathology*; D006801:Humans; D008297:Male; D014261:Tricuspid Valve / Q000000981:diagnostic imaging / Q000473:pathology*