Dropped head syndrome as a presenting sign of scleromyositis.
The isolated or prominent weakness of cervical extensor muscles is a relatively rare clinical sign known as "dropped head syndrome". It occurs in a variety of neuromuscular diseases. Here, we report the case of a 53 year old woman whose main symptom was a dropped head syndrome that led to the diagnosis of scleromyositis. Scleromyositis is a rare idiopathic inflammatory myopathy, which combines polymyositis and scleroderma symptoms. Although idiopathic inflammatory myopathies are listed as causes of dropped head syndrome, very few cases are reported in the literature. Furthermore, scleromyositis revealed by a dropped head syndrome has never been described. As this condition was totally reversed by a regiment of corticosteroids, it is thus of a diagnostic interest for neurologists to be aware of idiopathic inflammatory myopathies, including scleromyositis, as a potentially treatable aetiology of dropped head syndrome.
Garcin
Beatrice
B
AP-HP, service de neurologie, Hôpital Saint-Antoine, 184 rue de Faubourg Saint-Antoine, 75012 Paris, France. beagarcin@msn.com
Lenglet
Timothée
T
Dubourg
Odile
O
Mesnage
Valérie
V
Levy
Richard
R
D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D008875:Middle Aged; D018908:Muscle Weakness / Q000209:etiology*; D009334:Neck Muscles / Q000473:pathology*; D017285:Polymyositis / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use; D020127:Recovery of Function; D012595:Scleroderma, Systemic / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D016896:Treatment Outcome
D005938:Glucocorticoids; D011241:Prednisone