Successful weaning of a laryngeal mask airway after a tongue-lip adhesion operation in a case with cerebro-costo-mandibular syndrome.
Cerebro-costo-mandibular syndrome (CCMS) consists of severe micrognathia, glossoptosis, posterior rib-gap defects and developmental delay. It may cause upper airway obstruction andflail chest, resulting in neonatal hypoxia, and possibly death. Early airway management or surgical intervention to maintain a patent airway is critical to avoid hypoxia in CCMS patients. We report a newborn with CCMS who was successfully weaned from a laryngeal mask after undergoing a tongue-lip adhesion operation at 164 days of age.
Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan.
Chi-Yung
CY
So
Yan-Yan
YY
Ng
Chih-Yu
CY
Peng
Jui-Ming
JM
Hu
Suh-Jen
SJ
Chen
Jia-Yuh
JY
Chen
Pen-Hua
PH
Su
D000015:Abnormalities, Multiple / Q000601:surgery*; D002972:Cleft Palate / Q000601:surgery*; D005409:Flail Chest / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D017214:Laryngeal Masks; D008046:Lip / Q000601:surgery*; D008297:Male; D008844:Micrognathism / Q000601:surgery*; D012272:Ribs / Q000002:abnormalities*; D013577:Syndrome; D014059:Tongue / Q000601:surgery*