Intrathecal baclofen pump implantation in a case of stiff person syndrome.
Stiff person syndrome (SPS) is a rare disorder characterized by severe axial and/or limb rigidity, spasms and continuous motor unit activity on EMG. Symptomatically these patients are usually treated with GABAergic medications. We present a 45-year-old woman with SPS, who failed high dose of GABAergic medication. With intrathecal baclofen by intrathecal baclofen pump she had a significant improvement in her symptoms and quality of life.
Department of Neurology, Lourdes Heart Institute and Neuro Centre, Kochi, Kerala, India. bobvarkey@gmail.com
Bobby Varkey
BV
Maramattom
D001418:Baclofen / Q000627:therapeutic use*; D005260:Female; D018755:GABA Agonists / Q000627:therapeutic use*; D006801:Humans; D015918:Infusion Pumps, Implantable; D007278:Injections, Spinal / Q000379:methods; D008875:Middle Aged; D016750:Stiff-Person Syndrome / Q000188:drug therapy* / Q000473:pathology
D018755:GABA Agonists; D001418:Baclofen