Giant renal angiomyolipomas and pulmonary lymphangiomyomatosis.
Renal angiomyolipomas (AML) are benign tumors, which can acquire huge size and when bilateral, they are diagnostic of tuberous sclerosis (TS). Pulmonary lymphangiomyomatosis (LAM) is more common in female patients with TS and mostly diagnosed in patients with renal AMLs. We report a case of giant bilateral AMLs and pulmonary LAM in a 48-year-old female patient, who required nephrectomy for life-threatening hemorrhage.
Department of Nephrology, The Kidney Centre, Karachi, Pakistan. neph.kiran@gmail.com
Kiran
K
Nasir
Aasim
A
Ahmad
D018207:Angiomyolipoma / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D001803:Blood Transfusion; D005260:Female; D006470:Hemorrhage / Q000209:etiology; D006801:Humans; D007680:Kidney Neoplasms / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D008175:Lung Neoplasms / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D018192:Lymphangioleiomyomatosis / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary; D009392:Nephrectomy; D006435:Renal Dialysis; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014402:Tuberous Sclerosis / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000628:therapy