A case of adult periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome associated with endocapillary proliferative glomerulonephritis.
PFAPA is an acronym for periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis. This syndrome has been usually described in pediatric patients and it generally resolves spontaneously. The endocapillary proliferative glomerulonephritis (EPG) is a glomerular injury characterized by hypercellularity in glomerular lumen and is caused by post-infectious or autoimmune diseases. In this paper, we describe the case of a 35-year-old man affected by PFAPA and EPG. To our knowledge this association has never been reported in the literature before.
Department of Rheumatology, University of Pisa, Via Roma 67, 56100 Pisa, Italy. m_cazzato@virgilio.it
Massimiliano
M
Cazzato
Rossella
R
Neri
Niccolo
N
Possemato
Rodolfo
R
Puccini
Stefano
S
Bombardieri
D000328:Adult; D004305:Dose-Response Relationship, Drug; D005334:Fever / Q000175:diagnosis*; D015432:Glomerulonephritis, Membranoproliferative / Q000175:diagnosis* / Q000188:drug therapy; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D008198:Lymph Nodes / Q000473:pathology; D008199:Lymphadenitis / Q000175:diagnosis*; D008297:Male; D008775:Methylprednisolone / Q000627:therapeutic use; D009333:Neck; D010507:Periodicity; D010612:Pharyngitis / Q000175:diagnosis*; D020551:Pulse Therapy, Drug; D013281:Stomatitis, Aphthous / Q000175:diagnosis*; D013577:Syndrome; D016896:Treatment Outcome
D005938:Glucocorticoids; D008775:Methylprednisolone