A young patient with Danon disease receives two ICD shocks: why?
We report the case of an 18-year-old man with Danon disease, a genetic disorder inclunding a severe hypertrophic cardiomyopathy with very broad QRS, who had an implantable cardioverter defibrillator for primary prevention. Nine months after implantation, he received two inappropriate shocks due to R-wave double counting during sinus tachycardia. We discuss how to avoid such inappropriate therapy.
Hôpital Trousseau, Cardiology, Tours, France. nourazannad@sfr.fr
Noura
N
Zannad
Bertrand
B
Pierre
Pierre
P
Cosnay
Dominique
D
Babuty
D000293:Adolescent; D017147:Defibrillators, Implantable; D052120:Glycogen Storage Disease Type IIb / Q000628:therapy*; D006801:Humans; D008297:Male; D011475:Prosthesis Failure; D013616:Tachycardia, Sinus / Q000628:therapy