Kaposiform hemangioendothelioma arising from the maxillary sinus: a case report.
Kaposiform hemangioendothelioma is a very infrequent, locally aggressive vascular neoplasm, characterized by fascicular spindle cell proliferation. It occurs almost exclusively in infants and adolescents, and is often associated with Kasabach-Merritt phenomenon. The tumor is predominantly located subcutaneously or in the deep soft tissue of the extremities and trunk, peritoneum, or retroperitoneum. However, this tumor can sometimes be located on the head and neck. We report a case of kaposiform hemangioendothelioma of the maxillary sinus in a 4-month-old female infant presenting with cheek swelling, thrombocytopenia, anemia, and disseminated intravascular coagulation. Sinus computed tomography presented an enhancing, bone-destructing tumor. Magnetic resonance images showed an uncommon appearance as mostly low signal intensity on T2-weighted images.
Lee
Chin-Ho
CH
Department of Medical imaging, Kaohsiung Medical University Hospital, Kaohsiung, Taiwan.
Jaw
Twei-Shiun
TS
Yang
Sheau-Fang
SF
Wu
Ding-Kwo
DK
D005260:Female; D006390:Hemangioendothelioma / Q000000981:diagnostic imaging / Q000473:pathology*; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008443:Maxillary Sinus / Q000000981:diagnostic imaging / Q000473:pathology*; D014057:Tomography, X-Ray Computed