title: [Stewart-Treves syndrome: report of one case].
abstract: Angiosarcomas are malignant tumors derived from the endothelium of blood vessel (hemangiosarcomas) or lymph vessels (lymphangiosarcomas). Lymph edema of the limbs is considered secondary when extrinsic injuries are observed and primary when these injuries are not present. Stewart-Treves syndrome or a Lymphangiosarcoma, developed over a chronic lymph edema, is a rare complication described in mastectomized patients but it can be observed in lymph edemas located elsewhere. It appears as nodular skin lesions that grow, multiply quickly and frequently metastasize. We report a 40-year-old mole with an angiosarcoma associated with primary chronic lower limb lymph edema. The patient consulted for a history of weight loss and malaise and appearance of violaceous lesions over the zone of lymph edema and inguinal lymph node involvement. A CT scan showed bilateral lung lesions and enlargement of inguinal and iliac lymph nodes. A biopsy of one of the skin lesions disclosed an angiosarcoma, diagnosis that was confirmed with immuno-histochemistry Chemotherapy was started but the patient died five months after the diagnosis.
authors.affiliation: Departamento Clínico de Medicina, Hospital de Clínicas, Universidad de la República, Montevideo, Uruguay. rsilvarino@gmail.com
authors.forename: Ricardo
authors.initials: R
authors.lastname: Silvariño
authors.forename: Valentina
authors.initials: V
authors.lastname: Mérola
authors.forename: Luis
authors.initials: L
authors.lastname: Fígoli
authors.forename: Cecilia
authors.initials: C
authors.lastname: Romero
authors.forename: Jimena
authors.initials: J
authors.lastname: Lapiedra
authors.forename: Juan
authors.initials: J
authors.lastname: Alonso
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D006801:Humans; D035002:Lower Extremity / Q000473:pathology*; D008175:Lung Neoplasms / Q000556:secondary*; D008204:Lymphangiosarcoma / Q000556:secondary*; D008209:Lymphedema / Q000473:pathology*; D008297:Male