Refractory heart failure in a patient with non-compacted myocardium.
The non-compacted myocardium is characterized by excessive trabeculation and ventricular recesses (usually of the left ventricle) due to the interruption of the myocardial fiber compaction during embryogenesis. This abnormality usually courses with heart failure, thromboembolic phenomena and cardiac arrhythmia, predicting a bad prognosis. We report the case of a 26-year-old male individual with refractory heart failure due to isolated left ventricular non-compacted myocardium that needed a heart transplant.
Villacorta
Humberto
H
Hospital Quinta D'Or, Rio de Janeiro, RJ, Brasil. hvillacorta@quintador.com.br
Sampaio
Jacqueline Miranda
JM
Santos
Fernanda Beatriz Amador Dos
FB
Carrera
Valdo
V
Pereira
Carlos Cleverson
CC
Mesquita
Evandro Tinoco
ET
D000328:Adult; D006333:Heart Failure / Q000209:etiology*; D016027:Heart Transplantation; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000150:complications* / Q000473:pathology / Q000601:surgery; D008297:Male