An unusual case of congenitally unguarded tricuspid valve orifice associated with pulmonary valve atresia and intact ventricular septum.
We report on a premature neonate who presented with cyanosis soon after birth. She was found on echocardiography to have an unguarded tricuspid valve orifice associated with pulmonary valve atresia and an intact interventricular septum. Owing to the small-sized pulmonary arteries, she was initially managed conservatively with prostaglandin infusion, and at one year of age underwent a successful bidirectional cavo-pulmonary (Glenn) shunt operation.
Takawira
Farirai F
FF
Department of Paediatric Cardiology, Steve Biko Academic Hospital and University of Pretoria, Pretoria, South Africa. fari.takawira@up.ac.za
Mitchell
Belinda J
BJ
Du Plessis
Dirk J
DJ
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D018633:Pulmonary Atresia / Q000150:complications* / Q000000981:diagnostic imaging*; D035583:Rare Diseases / Q000000981:diagnostic imaging; D018785:Tricuspid Atresia / Q000150:complications* / Q000000981:diagnostic imaging*; D014463:Ultrasonography