title: Degos cutaneous disease with features of connective tissue disease.
abstract: A 30-year-old woman was referred on April 2002 for a plaque that involved the internal aspect of the right leg, an erythema nodosum-like lesion on the lower extremities, and periarthritis on her left ankle. Subsequently, the patient developed anular, atrophic, growing, porcelain-white papules, with a thin rim of erythema and telangiectases over her upper and lower extremities. Clinically and histologically, these lesions were the characteristics of Degos disease. Despite arthritis and myositis that required treatment, low level C3 and C4, positive antinuclear antibodies, and elevated anticardiolipin antibodies only once, in a follow-up of 6 years the patient never developed a specific connective tissue disease or other systemic involvement. In conclusion, because clinical and histological findings of Degos disease might mimic connective tissue diseases, rheumatologists must be aware that this reaction pattern can be seen in a wide clinical spectrum of diseases.
authors.affiliation: Rheumatology Section, Hospital José M. Cullen, Santa Fe, Argentina.
authors.forename: Alberto
authors.initials: A
authors.lastname: Ortiz
authors.forename: Federico
authors.initials: F
authors.lastname: Ceccato
authors.forename: Adriana
authors.initials: A
authors.lastname: Albertengo
authors.forename: Susana
authors.initials: S
authors.lastname: Roverano
authors.forename: José
authors.initials: J
authors.lastname: Iribas
authors.forename: Sergio
authors.initials: S
authors.lastname: Paira
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D054853:Malignant Atrophic Papulosis / Q000473:pathology*