A case of Degos disease successfully treated with corticosteroid combined with cyclophosphamide.
Degos disease is a rare disorder characterized by systemic vasculitis involving various organs. There is no established, effective treatment for the disorder, and its prognosis is still poor. Combination therapy with corticosteroid and cyclophosphamide is considered effective for vasculitides involving the small arteries such as ANCA-associated vasculitis. We present here a 42-year-old man who developed Degos disease over several months, and was successfully treated using combined treatment with corticosteroid and cyclophosphamide.
Kameda
Tomohiro
T
Department of Internal Medicine Division of Endocrinology and Metabolism, Hematology, Rheumatology and Respiratory Medicine Faculty of Medicine, Kagawa University, Takamatsu, Japan.
Dobashi
Hiroaki
H
Yoneda
Kozo
K
Susaki
Kentaro
K
Kuno
Toshiya
T
Murao
Koji
K
Ishida
Toshihiko
T
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use*; D000328:Adult; D003520:Cyclophosphamide / Q000627:therapeutic use*; D004359:Drug Therapy, Combination; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use*; D008297:Male; D054853:Malignant Atrophic Papulosis / Q000188:drug therapy*; D016896:Treatment Outcome
D000305:Adrenal Cortex Hormones; D007166:Immunosuppressive Agents; D003520:Cyclophosphamide