title: Biventricular repair of right atrial isomerism with complex congenital anomalies.
abstract: Biventricular repair is usually difficult to achieve in patients who have right atrial isomerism, which is typically associated with other complex cardiac anomalies. The procedure can be used in patients who have balanced ventricular structures. Herein, we report a successful surgical reconstruction, including biventricular repair, in a 4-year-old boy. The child's right atrial isomerism was associated with double-outlet right ventricle, a large atrial septal defect, a subaortic ventricular septal defect, valvular and infundibular pulmonary stenosis, left persistent superior vena cava, and hemiazygos continuation of an interrupted inferior vena cava. Balanced ventricles enabled biventricular repair, which we consider to be preferable to the Fontan procedure in such circumstances.
authors.affiliation: Department of Cardiac Surgery, Kartal Kosuyolu Heart & Research Center, Kartal, 34846 Istanbul, Turkey.
authors.forename: Kaan
authors.initials: K
authors.lastname: Kirali
authors.forename: Ahmet
authors.initials: A
authors.lastname: Sasmazel
authors.forename: Ilker
authors.initials: I
authors.lastname: Mataraci
authors.forename: Hasan
authors.initials: H
authors.lastname: Erdem
authors.forename: Fusun
authors.initials: F
authors.lastname: Guzelmeric
mesh_terms: D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures; D002675:Child, Preschool; D004310:Double Outlet Right Ventricle / Q000601:surgery; D006325:Heart Atria / Q000002:abnormalities / Q000601:surgery; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D008297:Male; D011666:Pulmonary Valve Stenosis / Q000601:surgery; D056346:Sternotomy; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014682:Vena Cava, Inferior / Q000002:abnormalities / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities / Q000601:surgery
references.citation: Ann Thorac Surg. 1999 May;67(5):1403-11
references.pmid: 10355421
references.citation: Ann Thorac Surg. 2006 May;81(5):1808-16; discussion 1816
references.pmid: 16631677
references.citation: Circulation. 1990 May;81(5):1520-36
references.pmid: 2331765
references.citation: Ann Thorac Surg. 1998 Aug;66(2):641-3
references.pmid: 9725444