Nutritional considerations in patients with cystic fibrosis.
Nutritional status is strongly associated with pulmonary function and survival in cystic fibrosis patients. Attainment of a normal growth pattern in childhood and maintenance of adequate nutritional status in adulthood represent major goals of multidisciplinary cystic fibrosis centers. International guidelines on energy intake requirements, pancreatic enzyme-replacement therapy and fat-soluble vitamin supplementation are of utmost importance in daily practice. The present review summarizes the most up-to-date information on early nutritional management in newly diagnosed patients and evaluates the benefits of aggressive nutritional support, assessment of nutritional status, recommendations for nutrition-related management in pancreatic-insufficient patients and the possible therapeutic impact of fat intake modulation upon inflammatory status.
Munck
Anne
A
CF Center, University Hospital Robert Debré, AP-HP 48, bd Serurier 75019 Paris, France. anne.munck@rdb.aphp.fr
D003550:Cystic Fibrosis / Q000178:diet therapy / Q000503:physiopathology*; D018450:Disease Progression; D004734:Energy Metabolism; D057487:Enzyme Therapy; D006801:Humans; D007249:Inflammation / Q000517:prevention & control; D008286:Malabsorption Syndromes / Q000503:physiopathology / Q000517:prevention & control; D009748:Nutrition Disorders / Q000503:physiopathology* / Q000517:prevention & control*; D009751:Nutritional Requirements; D009752:Nutritional Status; D018529:Nutritional Support / Q000379:methods*; D011379:Prognosis; D012129:Respiratory Function Tests; D014815:Vitamins / Q000627:therapeutic use
D014815:Vitamins