Auditory steady state response in auditory neuropathy.
METHODS
Auditory neuropathy is a disorder characterised by preservation of outer hair cell function, with normal otoacoustic emissions and/or cochlear microphonics, but an absent or distorted auditory brainstem response.


OBJECTIVE
This study aimed to objectively assess hearing thresholds in patients with auditory neuropathy, using the auditory steady state response.


METHODS
Thirteen patients with auditory neuropathy and 15 normal hearing subjects were examined. Audiological evaluation included basic audiological tests, otoacoustic emissions, auditory brainstem response and auditory steady state response.


RESULTS
In the auditory neuropathy patients, the auditory brainstem response was absent in 11 patients, while the auditory steady state response was absent in only three.


CONCLUSIONS
The auditory steady state response may serve as a valuable objective measure for assessing the hearing threshold across different frequencies in patients with auditory neuropathy. We recommend that auditory steady state response be used to complete the evaluation of patients with auditory neuropathy.
Emara
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AA
MD Audiology Unit, ENT Department, Tanta University, Cairo, Egypt. Afaf_emara@hotmail.com
Gabr
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TA
D000161:Acoustic Stimulation / Q000379:methods; D000293:Adolescent; D000328:Adult; D001299:Audiometry / Q000379:methods*; D001309:Auditory Threshold / Q000502:physiology*; D016022:Case-Control Studies; D002648:Child; D005072:Evoked Potentials, Auditory / Q000502:physiology; D005260:Female; D034381:Hearing Loss / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology*; D006313:Hearing Loss, Central / Q000175:diagnosis / Q000503:physiopathology; D006801:Humans; D008297:Male; D017084:Otoacoustic Emissions, Spontaneous / Q000502:physiology; D011237:Predictive Value of Tests; D000160:Vestibulocochlear Nerve Diseases / Q000175:diagnosis / Q000503:physiopathology*; D055815:Young Adult