title: [Aortic valve preservation and root reconstruction in Marfan syndrome].
abstract: OBJECTIVE
  To explore the experiences of aortic valve preservation and root reconstruction in patients with Marfan syndrome.
  
  
  METHODS
  From July 2003 to Dec 2007, 22 patients with Marfan syndrome were treated by aortic valve preservation and root reconstruction. There were 12 male and 10 female, the age ranged from 10 to 57 years old with a mean of (28 +/- 10) years. The operation procedures included reimplantation technique in 9 patients, remodeling technique in 8 patients, and patch technique in 2 patients. In addition, reimplantation technique + total aorta replacement in 1 patient, remodeling technique + "aortic arch replacement + stent-elephant trunk" in 1 patient, patch technique + "aortic arch replacement + stent-elephant trunk" in 1 patient. The patients were followed-up by 17 to 64 months with a mean of (46 +/- 16) months.
  
  
  RESULTS
  No in-hospital and follow-up period death occurred. There was one reexploration for bleeding 1 d postoperative. No valve-related complication occurred during the follow-up. At the end of follow-up, no aortic regurgitation was demonstrate in 16 patients, but mild regurgitation in 4 patients, moderate regurgitation in 1 patient and severe regurgitation in 1 patient. Two patients with moderate and severe aortic regurgitation need reoperation 1 year postoperative.
  
  
  CONCLUSIONS
  The early and mid-term results of aortic valve preservation and root reconstruction operations in Marfan syndrome were favorable.
authors.affiliation: Fu Wai Hospital, Peking Union Medical College and Chinese Academy of Medical Science, Beijing, China.
authors.forename: Ren
authors.initials: R
authors.lastname: Wang
authors.forename: Li-zhong
authors.initials: LZ
authors.lastname: Sun
authors.forename: Qian
authors.initials: Q
authors.lastname: Chang
authors.forename: Jun-ming
authors.initials: JM
authors.lastname: Zhu
authors.forename: Yong-min
authors.initials: YM
authors.lastname: Liu
authors.forename: Cun-tao
authors.initials: CT
authors.lastname: Yu
authors.forename: Liang-xin
authors.initials: LX
authors.lastname: Tian
authors.forename: Hui
authors.initials: H
authors.lastname: Xiong
authors.forename: Dian-yuan
authors.initials: DY
authors.lastname: Li
mesh_terms: D000293:Adolescent; D000328:Adult; D001011:Aorta / Q000601:surgery*; D001014:Aortic Aneurysm / Q000209:etiology / Q000601:surgery*; D001021:Aortic Valve / Q000601:surgery; D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D008875:Middle Aged; D012189:Retrospective Studies; D016896:Treatment Outcome; D055815:Young Adult