Hemophagocytic syndrome in adult-onset Still's disease (AOSD): a must for biologics?--Case report and brief review of the literature.
A case of adult-onset Still's disease complicated by hemophagocytic lymphohistiocytosis is reported. Its management is being discussed on the background of the latest literature with special regard on the use of high-dose corticosteroids and immunosuppressive agents.
Bürgi
Urs
U
Department of Medicine, Kantonsspital Aarau, Aarau, Switzerland.
Mendez
Adriana
A
Hasler
Paul
P
Hüllstrung
Hans Dieter
HD
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use*; D000328:Adult; D001688:Biological Products / Q000627:therapeutic use*; D001856:Bone Marrow Examination; D005260:Female; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use*; D051359:Lymphohistiocytosis, Hemophagocytic / Q000175:diagnosis / Q000188:drug therapy* / Q000209:etiology; D016706:Still's Disease, Adult-Onset / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy*; D016896:Treatment Outcome
D000305:Adrenal Cortex Hormones; D001688:Biological Products; D007166:Immunosuppressive Agents
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