Ectodermal dysplasia with anodontia: a report of two cases.
Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances in the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. Two case reports illustrating the prosthetic rehabilitation of 2 young boys with anhidrotic ectodermal dysplasia associated with severe anodontia are presented. Since the oral rehabilitation of these cases is often difficult; particularly in pediatric patients, treatment should be administered by a multidisciplinary team involving pediatric dentistry, orthodontics, prosthodontics and oral-maxillofacial surgery.
Bani
Mehmet
M
DDS, Research Assistant, Gazi University, Faculty of Dentistry, Department of Paediatric Dentistry, Ankara, Turkey.
Tezkirecioglu
Ali Melih
AM
Akal
Nese
N
Tuzuner
Tamer
T
Clin Pediatr (Phila). 1966 Jul;5(7):395-402
5944778
Quintessence Int. 1997 Sep;28(9):595-602
9477874
Northwest Dent. 1992 May-Jun;71(3):25-8
1528729
Quintessence Int. 2007 Jan;38(1):75-80
17216912
J Prosthet Dent. 2005 May;93(5):419-24
15867750
Quintessence Int. 2001 Oct;32(9):743-5
11695142
J Am Dent Assoc. 2005 Sep;136(9):1273-6
16196232
J Prosthet Dent. 2002 Dec;88(6):569-72
12488847
J Clin Pediatr Dent. 2002 Fall;27(1):5-8
12413164
Br Dent J. 2003 Mar 8;194(5):245-51
12658298
J Prosthodont. 2007 May-Jun;16(3):209-13
17581183
Pediatr Dermatol. 1997 May-Jun;14(3):180-5
9192408
J Contemp Dent Pract. 2005 Aug 15;6(3):120-6
16127480