Biventricular repair of right atrial isomerism with complex congenital anomalies.
Biventricular repair is usually difficult to achieve in patients who have right atrial isomerism, which is typically associated with other complex cardiac anomalies. The procedure can be used in patients who have balanced ventricular structures. Herein, we report a successful surgical reconstruction, including biventricular repair, in a 4-year-old boy. The child's right atrial isomerism was associated with double-outlet right ventricle, a large atrial septal defect, a subaortic ventricular septal defect, valvular and infundibular pulmonary stenosis, left persistent superior vena cava, and hemiazygos continuation of an interrupted inferior vena cava. Balanced ventricles enabled biventricular repair, which we consider to be preferable to the Fontan procedure in such circumstances.
Kirali
Kaan
K
Department of Cardiac Surgery, Kartal Kosuyolu Heart & Research Center, Kartal, 34846 Istanbul, Turkey.
Sasmazel
Ahmet
A
Mataraci
Ilker
I
Erdem
Hasan
H
Guzelmeric
Fusun
F
D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures; D002675:Child, Preschool; D004310:Double Outlet Right Ventricle / Q000601:surgery; D006325:Heart Atria / Q000002:abnormalities / Q000601:surgery; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D008297:Male; D011666:Pulmonary Valve Stenosis / Q000601:surgery; D056346:Sternotomy; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014682:Vena Cava, Inferior / Q000002:abnormalities / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities / Q000601:surgery
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