title: Ewing's sarcoma/PNET of kidney in 13-year-old girl.
abstract: Ewing's sarcoma is the second most common primary tumour of bone in childhood. Less frequently it occurs in soft tissues. Ewing's sarcoma/primitive neuroectodermal tumour (ES/PNET) is an extra ordinarily rare primary tumour in the kidney. Only very few cases of primary renal Ewing's sarcoma have been reported in the literature to date. We present a case of primary right renal Ewing's sarcoma in a 13-year-old girl who was diagnosed as a case of stage IV ES/PNET of kidney with metastases to lung and liver. Right nephrectomy was done followed by adjuvant radiotherapy and chemotherapy with complete response to local and distant area.
authors.affiliation: Department of Radiation Oncology, the Aga Khan University Hospital, Pakistan.
authors.forename: Quratulain
authors.initials: Q
authors.lastname: Badar
authors.forename: Nasir
authors.initials: N
authors.lastname: Ali
authors.forename: Nadeem
authors.initials: N
authors.lastname: Abbasi
authors.forename: Shamvil
authors.initials: S
authors.lastname: Ashraf
authors.forename: Farrok
authors.initials: F
authors.lastname: Karsan
authors.forename: Raheel
authors.initials: R
authors.lastname: Hashmi
mesh_terms: D000293:Adolescent; D001706:Biopsy; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000000981:diagnostic imaging* / Q000628:therapy; D018242:Neuroectodermal Tumors, Primitive / Q000000981:diagnostic imaging* / Q000628:therapy; D012512:Sarcoma, Ewing / Q000000981:diagnostic imaging* / Q000628:therapy; D014057:Tomography, X-Ray Computed; D018084:Ultrasonography, Interventional