A myxoid chondrosarcoma associated with an anti-Hu-positive paraneoplastic encephalomyelitis.
Extraskeletal myxoid chondrosarcoma is a rare tumor with less than 100 cases reported in the literature. The prevalence of anti-Hu positive myxoid chondrosarcoma-associated paraneoplastic subacute cerebellar degeneration is exceedingly rare. We present a report of a patient with confirmed myxoid chondrosarcoma-associated paraneoplastic subacute cerebellar degeneration, who exhibited marked improvement within 1 week of receiving chemotherapy, intravenous immunoglobulin (IVIG), and hydrocortisone treatment.
Hoosien
Michael
M
University of Miami, Miami, FL, 33136, USA. mhoosien@med.miami.edu
Vredenburgh
James
J
Lanfranco
Julio
J
Ochoa
Roberto
R
Robinson
Philip
P
Martinez
Robert
R
Singer
Carlos
C
Silva
Orlando
O
D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002813:Chondrosarcoma / Q000150:complications* / Q000188:drug therapy / Q000601:surgery; D051959:ELAV Proteins / Q000276:immunology; D006801:Humans; D016756:Immunoglobulins, Intravenous / Q000627:therapeutic use; D008297:Male; D008875:Middle Aged; D020361:Paraneoplastic Syndromes, Nervous System / Q000188:drug therapy / Q000209:etiology* / Q000503:physiopathology*; D012983:Soft Tissue Neoplasms / Q000150:complications* / Q000188:drug therapy / Q000601:surgery; D013848:Thigh
D051959:ELAV Proteins; D016756:Immunoglobulins, Intravenous