Ewing's sarcoma/PNET of kidney in 13-year-old girl.
Ewing's sarcoma is the second most common primary tumour of bone in childhood. Less frequently it occurs in soft tissues. Ewing's sarcoma/primitive neuroectodermal tumour (ES/PNET) is an extra ordinarily rare primary tumour in the kidney. Only very few cases of primary renal Ewing's sarcoma have been reported in the literature to date. We present a case of primary right renal Ewing's sarcoma in a 13-year-old girl who was diagnosed as a case of stage IV ES/PNET of kidney with metastases to lung and liver. Right nephrectomy was done followed by adjuvant radiotherapy and chemotherapy with complete response to local and distant area.
Badar
Quratulain
Q
Department of Radiation Oncology, the Aga Khan University Hospital, Pakistan.
Ali
Nasir
N
Abbasi
Nadeem
N
Ashraf
Shamvil
S
Karsan
Farrok
F
Hashmi
Raheel
R
D000293:Adolescent; D001706:Biopsy; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000000981:diagnostic imaging* / Q000628:therapy; D018242:Neuroectodermal Tumors, Primitive / Q000000981:diagnostic imaging* / Q000628:therapy; D012512:Sarcoma, Ewing / Q000000981:diagnostic imaging* / Q000628:therapy; D014057:Tomography, X-Ray Computed; D018084:Ultrasonography, Interventional