Wegener s granulomatosis with granulomatous liver involvement.
We report on a patient with biopsy proven systemic Wegener's granulomatosis (WG) with a granulomatous necrotising manifestation of WG in the liver, lung, parotid gland and skin with subsequent death of liver failure. Liver involvement in WG is an exceedingly rare, though potentially fatal, organ manifestation of WG.
Holl-Ulrich
Konstanze
K
Institute of Pathology, University Hospital Schleswig-Holstein, Campus Lubeck, Germany. holl-ulrich@patho.uni-luebeck.de
Klass
Monika
M
D000368:Aged; D019268:Antibodies, Antineutrophil Cytoplasmic / Q000097:blood; D001706:Biopsy; D017809:Fatal Outcome; D005260:Female; D014890:Granulomatosis with Polyangiitis / Q000150:complications* / Q000276:immunology / Q000473:pathology; D006505:Hepatitis / Q000209:etiology* / Q000276:immunology / Q000473:pathology; D006801:Humans; D008099:Liver / Q000473:pathology; D017093:Liver Failure / Q000209:etiology* / Q000276:immunology / Q000473:pathology; D008168:Lung / Q000473:pathology; D009336:Necrosis; D010306:Parotid Gland / Q000473:pathology; D010309:Parotitis / Q000209:etiology / Q000276:immunology / Q000473:pathology; D012867:Skin / Q000473:pathology
D019268:Antibodies, Antineutrophil Cytoplasmic