Epitheloid hemangioendothelioma in patient with liver transplantation.
Malignant hepatic epithelioid hemangioendothelioma (HEH) is a rare malignant tumor of vascular origin with unknown aetiology and a variable natural course. At the time of diagnosis, most patients present with multifocal tumours lesions that involve both liver lobes. From the therapeutic aspect, liver resection (LRx), liver transplantation (LTx), chemotherapy, radiotherapy, and/or immunotherapy have been used in the treatment of patients with HEH. However, because of the rarity of this tumor and its unpredictable natural history, it is impossible to assess the effectiveness of these respective therapies. In this report, our objective was to present clinical aspects, diagnostic options, therapeutic modalities, and the clinical outcome of single patient with LTx because of this rare tumor.
Kanizaj
Tajana Filipec
TF
Department of Medicine, University Hospital "Merkur", Zagreb, Croatia. tajana_filipec@yahoo.com
Cvrlje
Vesna Colić
VC
Mrzljak
Anna
A
Kardum-Skelin
Ika
I
Sustercić
Dunja
D
Segro
Dinko
D
Gustin
Denis
D
Kocman
Branislav
B
D018952:Antigens, CD34 / Q000378:metabolism; D044963:Biopsy, Fine-Needle; D004801:Eosine Yellowish-(YS); D005260:Female; D018323:Hemangioendothelioma, Epithelioid / Q000378:metabolism / Q000473:pathology* / Q000601:surgery*; D006801:Humans; D008113:Liver Neoplasms / Q000378:metabolism / Q000473:pathology* / Q000601:surgery*; D016031:Liver Transplantation; D008751:Methylene Blue; D008875:Middle Aged; D019408:Platelet Endothelial Cell Adhesion Molecule-1 / Q000378:metabolism
D018952:Antigens, CD34; C043260:May-Grunwald Giemsa; D019408:Platelet Endothelial Cell Adhesion Molecule-1; D008751:Methylene Blue; D004801:Eosine Yellowish-(YS)