Successful aortic reimplantation in a three-year-old child with Marfan syndrome.
Aortic root dilatation is rare in children, and is often secondary to Marfan syndrome (MFS). We experienced a case of a three-year-old boy (92 cm, 12 kg) with MFS presenting with progressive dilatation of aortic root. We electively performed a valve-sparing aortic root replacement using a 24-mm Gelweave Valsalva graft. Although the patient required a mitral valve repair due to infective endocarditis postoperatively, the recovery from the second surgery was uneventful. This case is one of the youngest children of valve-sparing aortic root replacement in the literature.
Miyahara
Yoshinori
Y
Department of Cardiovascular Surgery, Okayama University Graduate School of Medicine, Dentistry, and Pharmaceutical Sciences, 2-5-1 Shikata-cho, Kita-ku, Okayama 700-8558, Japan. giten@fd5.so-net.ne.jp
Kasahara
Shingo
S
Takagaki
Masami
M
Sano
Shunji
S
D001014:Aortic Aneurysm / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001027:Aortography / Q000379:methods; D001807:Blood Vessel Prosthesis; D019917:Blood Vessel Prosthesis Implantation / Q000009:adverse effects / Q000295:instrumentation; D002675:Child, Preschool; D004452:Echocardiography; D004697:Endocarditis, Bacterial / Q000382:microbiology / Q000601:surgery; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D008944:Mitral Valve Insufficiency / Q000382:microbiology / Q000601:surgery; D011474:Prosthesis Design; D012086:Reoperation; D012092:Replantation; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome