[Sweet's syndrome as the presenting manifestation of relapsing polychondritis].
Relapsing polychondritis (RP) is a rare disorder characterized by recurrent inflammatory episodes involving various cartilages. The clinical course of RP is variable, and dermatologic manifestations are uncommon. We report a 73-year-old patient who presented with a neutrophilic dermatosis (Sweet's syndrome) as the initial manifestation of RP. There was no evidence for a myelodysplastic syndrome, as it has been previously reported with RP, but the patient was followed-up for an indolent and untreated chronic lymphocytic leukaemia. Complete remission was obtained with oral corticosteroids. This report highlights the clinical spectrum of the RP.
Wastiaux
H
H
Clinique dermatologique, CHU de Nantes, Hôtel Dieu, 44093 Nantes cedex, France.
Hervier
B
B
Durant
C
C
Gagey-Caron
V
V
Masseau
A
A
Barbarot
S
S
Hamidou
M
M
D000368:Aged; D003937:Diagnosis, Differential; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D015451:Leukemia, Lymphocytic, Chronic, B-Cell / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D008297:Male; D011081:Polychondritis, Relapsing / Q000150:complications* / Q000175:diagnosis* / Q000188:drug therapy; D016463:Sweet Syndrome / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D016896:Treatment Outcome
D005938:Glucocorticoids