[Interstitial lung disease in the course of the surfactant protein C deficiency coexisting with the primary humoral immunodeficiency - case study].
The interstitial lung disease in children is a group of disorders heterogeneous in its etiology and pathogenesis. In differential diagnosis infectious, immunological and metabolic factors must be taken into consideration, as well as a genetically determined surfactant protein C deficiency. In the paper a case of interstitial lung disease in the course of the surfactant protein C deficiency coexisting with the primary humoral immunodeficiency is presented, with the discussion concerning clinical manifestation, radiological pattern, and histological findings.
Szczawińska-Popłonyk
Aleksandra
A
Klinika Pneumonologii, Alergologii Dzieciecej i Immunologii Klinicznej III Katedry Pediatrii Uniwersytetu Medycznego im. Karola Marcinkowskiego w Poznaniu. ola@malwa.com.pl
Breborowicz
Anna
A
Langfort
Renata
R
D002648:Child; D004198:Disease Susceptibility / Q000276:immunology; D005260:Female; D006801:Humans; D056724:Immunity, Humoral; D007153:Immunologic Deficiency Syndromes / Q000150:complications*; D017563:Lung Diseases, Interstitial / Q000175:diagnosis* / Q000276:immunology / Q000628:therapy*; D037721:Pulmonary Surfactant-Associated Protein C / Q000172:deficiency*
D037721:Pulmonary Surfactant-Associated Protein C