title: Perioperative management of a child with long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency.
authors.forename: Daniel
authors.initials: D
authors.lastname: Steinmann
authors.forename: Jana
authors.initials: J
authors.lastname: Knab
authors.forename: Hans-Joachim
authors.initials: HJ
authors.lastname: Priebe
mesh_terms: D015094:3-Hydroxyacyl CoA Dehydrogenases / Q000172:deficiency*; D000768:Anesthesia, General / Q000379:methods*; D018686:Anesthetics, Intravenous / Q000008:administration & dosage; D002648:Child; D005260:Female; D005283:Fentanyl / Q000008:administration & dosage; D005947:Glucose / Q000008:administration & dosage; D006801:Humans; D063989:Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase; D008874:Midazolam / Q000008:administration & dosage; D019990:Perioperative Care / Q000379:methods*; D010880:Piperidines / Q000008:administration & dosage; D000077208:Remifentanil; D012965:Sodium Chloride / Q000008:administration & dosage; D013874:Thiopental / Q000008:administration & dosage
chemical_list: D018686:Anesthetics, Intravenous; D010880:Piperidines; D012965:Sodium Chloride; D015094:3-Hydroxyacyl CoA Dehydrogenases; D063989:Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase; D005947:Glucose; D013874:Thiopental; D000077208:Remifentanil; D008874:Midazolam; D005283:Fentanyl