Desmoplastic small round cell tumor of the mandible in a child with unusual plantar metastasis.
Desmoplastic small round-cell tumor (DSRCT) is a rare and aggressive tumor that usually affects young males. Abdominal or pelvic disease is generally present in patients with DSRCT. Despite multimodality treatment, it still remains highly aggressive and has poor prognosis. We report a 16-year-old male with DSRCT in the mandible, an unusual site of the disease, treated with chemo-radiotherapy but recurred in an unexpected site 5 months after the completion of treatment.
Küpeli
Serhan
S
Department of Pediatric Oncology, Institute of Oncology, Hacettepe University Faculty of Medicine, Sihhiye/Ankara, Turkey. serkupeli@yahoo.com
Cağlar
Kudret
K
Birgen
Dilek
D
Sungur
Arzu
A
Varan
Ali
A
D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D001859:Bone Neoplasms / Q000556:secondary* / Q000628:therapy; D018288:Carcinoma, Small Cell / Q000188:drug therapy / Q000532:radiotherapy / Q000556:secondary*; D003131:Combined Modality Therapy; D017809:Fatal Outcome; D005534:Foot Diseases / Q000209:etiology*; D006801:Humans; D008207:Lymphatic Metastasis; D008279:Magnetic Resonance Imaging; D008297:Male; D008339:Mandibular Neoplasms / Q000188:drug therapy / Q000473:pathology* / Q000532:radiotherapy; D011879:Radiotherapy Dosage