title: Micrographic surgery (Tubingen torte technique) for the treatment of an invasive dermatofibrosarcoma protuberans with muscular involvement.
abstract: Dermatofibrosarcoma protuberans (DFSP) is an uncommon skin tumour characterized by a slow, infiltrative growth and marked tendency towards local recurrences. Wide surgical excision of 3-5 cm from the margins including the fascia is the recommended treatment. Mohs Micrographic Surgery has been shown to afford lower rates of recurrence. The Mohs-Tübingen technique is a variant indicated for very large excisions that allows a complete eradication of the tumour, preserving healthy tissues. We report the case of a 45 year-old man affected by DFSP of the right shoulder deeply infiltrating the muscles, referred to us for a recurrence after a large excision. We submitted the patient to Mohs-Tübingen surgery in collaboration with an orthopaedic surgeon due to the presence of muscular involvement of DFSP. Two surgical operations were necessary to obtain negative histology as the tumor was deeply infiltrating the prescapular muscles. After three years of follow-up, the patient did not have any recurrence and the normal mobility of the shoulder was preserved. Precocious diagnosis and adequate therapy are necessary for DFSP as not only the margins, but also the deep invasion of the tumor have to be carefully controlled.
authors.affiliation: Orthopaedics and Traumatology Unit, Maggiore della Carità Hospital, Novara, Italy.
authors.forename: M
authors.initials: M
authors.lastname: Leigheb
authors.forename: E
authors.initials: E
authors.lastname: Zavattaro
authors.forename: F
authors.initials: F
authors.lastname: Bellinzona
authors.forename: G
authors.initials: G
authors.lastname: Furlan
authors.forename: G
authors.initials: G
authors.lastname: Leigheb
mesh_terms: D018223:Dermatofibrosarcoma / Q000150:complications / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008297:Male; D008875:Middle Aged; D015580:Mohs Surgery / Q000379:methods*; D019042:Muscle Neoplasms / Q000473:pathology / Q000601:surgery*; D009361:Neoplasm Invasiveness; D012782:Shoulder; D012878:Skin Neoplasms / Q000150:complications / Q000473:pathology / Q000601:surgery*