[Primary pulmonary sarcoma-a study of 8 cases].
OBJECTIVE
To summarize the diagnosis, pathology, treatment and prognosis of 8 cases of primary pulmonary sarcoma.


METHODS
The clinical data of 8 patients with primary pulmonary sarcoma in the PUMC Hospital from 1986 to 2009 were retrospectively analyzed.


RESULTS
The clinical manifestations included cough (n=5), chest pain (n=2), hemoptysis (n=2), short of breath (n=2), and hoarseness due to the oppression of the recurrent laryngeal nerve (n=1). The pathological diagnoses included leiomyosarcoma (n=1), synovial sarcoma (n=1), malignant fibrous histiocytoma (n=1), and unknown tumors due to poor differentiation (n=5). The 1- and 5-year survival rate was 37.5 % and 12.5%, respectively.


CONCLUSIONS
The primary pulmonary sarcoma is a rare disease with non-specific clinical manifestations. The early diagnosis is difficult and the prognosis is poor. Currently no satisfactory therapy is available for this disease.
Zou
Bao-hua
BH
Department of Internal Medicine, PUMC Hospital, CAMS and PUMC, Beijing 100730, China.
Zhang
Li
L
D000328:Adult; D000368:Aged; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D008297:Male; D008875:Middle Aged; D012189:Retrospective Studies; D012509:Sarcoma / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D055815:Young Adult