Epidermolysis bullosa: management of esophageal strictures and enteric access by gastrostomy.
Epidermolysis bullosa (EB) is a spectrum of rare, inherited, blistering skin disorders, primarily affecting the skin and pharyngoesophageal mucosa. EB affects approximately 2 to 4 per 100,000 children each year. Blistering and scarring occur in response to even the most minor trauma. In this article, the authors outline the potential management options for patients with EB complicated by feeding difficulties secondary to esophageal strictures as well as those with nutritional deficiencies requiring a gastrostomy tube for supplemental feeding.
Mortell
Alan E
AE
Division of Pediatric and Thoracic Surgery, Cincinnati Children's Hospital Medical Center, University of Cincinnati College of Medicine,Cincinnati, OH 45229-3039, USA.
Azizkhan
Richard G
RG
D004750:Enteral Nutrition; D004820:Epidermolysis Bullosa / Q000150:complications* / Q000178:diet therapy*; D004940:Esophageal Stenosis / Q000178:diet therapy / Q000209:etiology / Q000601:surgery; D005774:Gastrostomy; D006801:Humans