Polysplenia/heterotaxy syndrome associated with aortic coarctation and multiple venous anomalies: multidetector computed tomography findings.
Polysplenia/heterotaxy syndrome is a rare condition involving multiple gastrointestinal, vascular, and cardiac malformations. We present a previously unreported association of aortic coarctation, double superior vena cava, a left-hand side inferior vena cava with hemiazygos vein continuation and a right retroaortic renal vein with polysplenia/heterotaxy syndrome. Multidetector computed tomography with multiplanar reconstruction images were useful in the detection of these abnormalities.
Karadeniz
Aysegul
A
Department of Radiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey.
Semiz Oysu
Aslihan
A
Sahin
Sinan
S
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000328:Adult; D001017:Aortic Coarctation / Q000000981:diagnostic imaging*; D001401:Azygos Vein / Q000002:abnormalities / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D012082:Renal Veins / Q000002:abnormalities / Q000000981:diagnostic imaging; D013154:Spleen / Q000002:abnormalities / Q000000981:diagnostic imaging*; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D014680:Veins / Q000002:abnormalities*; D014682:Vena Cava, Inferior / Q000002:abnormalities / Q000000981:diagnostic imaging; D014683:Vena Cava, Superior / Q000002:abnormalities / Q000000981:diagnostic imaging