Simultaneous occurrence of pancreatoblastoma and neuroblastoma in a newborn with beckwith-wiedemann syndrome.
Beckwith-Wiedemann syndrome is associated with an increased risk of tumors in the pediatric age. We report the case of a newborn with Beckwith-Wiedemann syndrome presenting the simultaneous occurrence of a cystic pancreatoblastoma and an adrenal neuroblastoma. Surgery was required to treat the pancreatoblastoma, and a "wait and see" policy was adopted for the neuroblastoma, which spontaneously regressed within a few months.
Sorrentino
Stefania
S
Department of Hematology-Oncology, Gaslini Children's Hospital, Genoa, Italy. sorryste@fastwebnet.it
Conte
Massimo
M
Nozza
Paolo
P
Granata
Claudio
C
Capra
Valeria
V
Avanzini
Stefano
S
Garaventa
Alberto
A
D000328:Adult; D001506:Beckwith-Wiedemann Syndrome / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D009447:Neuroblastoma / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D010181:Pancreatic Cyst / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D010190:Pancreatic Neoplasms / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D011247:Pregnancy; D011379:Prognosis; D014057:Tomography, X-Ray Computed; D016216:Ultrasonography, Prenatal