Desmoplastic small round cell tumor in the ovary: Report of two cases and literature review.
Desmoplastic small round cell tumor (DSRCT) is a rare intra-abdominal tumor of uncertain histogenesis that occurs predominantly in young males. We report two cases of DSRCT in young women that presented clinically as ovarian tumor with extensive pelvic and abdominal dissemination. Both patients underwent debulking surgery and combined chemotherapy. After primary therapy, the tumors recurred and both women died of the disease. The clinical presentation and differential diagnosis, as well as the treatment, including surgical debulking and combined chemotherapy are discussed.
Ota
Shunichiro
S
Department of Obstetrics and Gynecology, Kurume University School of Medicine, Fukuoka, Japan. otsir@med.kurume-u.ac.jp
Ushijima
Kimio
K
Fujiyoshi
Naoki
N
Fujimoto
Takefumi
T
Hayashi
Ryunosuke
R
Murakami
Fumihiro
F
Komai
Kan
K
Fujiyoshi
Keizo
K
Hori
Daizo
D
Kamura
Toshiharu
T
D000328:Adult; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D010051:Ovarian Neoplasms / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D010053:Ovary / Q000473:pathology; D018228:Sarcoma, Small Cell / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D016896:Treatment Outcome