Two-stage total aortic replacement for Loeys-Dietz syndrome.
Loeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.
Williams
Matthew L
ML
Division of Thoracic and Cardiovascular Surgery, Department of Surgery, Duke University, Durham, North Carolina 27710, USA.
Wechsler
Stephanie Burns
SB
Hughes
G Chad
GC
D000328:Adult; D000784:Aortic Dissection / Q000601:surgery*; D001011:Aorta / Q000601:surgery*; D001014:Aortic Aneurysm / Q000601:surgery*; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods; D006801:Humans; D055947:Loeys-Dietz Syndrome / Q000601:surgery*; D008297:Male; D016896:Treatment Outcome