Delayed enhancement cardiac magnetic resonance imaging in propionic acidemia.
We report on cardiomyopathy in propionic acidemia (PA) diagnosed using delayed-enhancement cardiac magnetic imaging (DECM) in a 27-year-old woman. DECM demonstrated hyperenhancement at the lateral wall of the left ventricle, suggesting myocardial changes occurring after a metabolic crisis, which improved during the convalescent period. DECM was useful for the diagnosis of cardiomyopathy in PA.
Iwashima
Satoru
S
Department of Pediatrics, Hamamatsu University School of Medicine, Hamamatsu 431-3192, Japan. iwashima@hama-med.ac.jp
Ishikawa
Takamichi
T
Ohzeki
Takehiko
T
Endou
Yusaku
Y
D000328:Adult; D003937:Diagnosis, Differential; D018450:Disease Progression; D005260:Female; D006331:Heart Diseases / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D007091:Image Processing, Computer-Assisted / Q000379:methods*; D008279:Magnetic Resonance Imaging / Q000379:methods*; D009206:Myocardium / Q000473:pathology*; D056693:Propionic Acidemia / Q000150:complications / Q000175:diagnosis*; D013997:Time Factors