title: Delayed enhancement cardiac magnetic resonance imaging in propionic acidemia.
abstract: We report on cardiomyopathy in propionic acidemia (PA) diagnosed using delayed-enhancement cardiac magnetic imaging (DECM) in a 27-year-old woman. DECM demonstrated hyperenhancement at the lateral wall of the left ventricle, suggesting myocardial changes occurring after a metabolic crisis, which improved during the convalescent period. DECM was useful for the diagnosis of cardiomyopathy in PA.
authors.affiliation: Department of Pediatrics, Hamamatsu University School of Medicine, Hamamatsu 431-3192, Japan. iwashima@hama-med.ac.jp
authors.forename: Satoru
authors.initials: S
authors.lastname: Iwashima
authors.forename: Takamichi
authors.initials: T
authors.lastname: Ishikawa
authors.forename: Takehiko
authors.initials: T
authors.lastname: Ohzeki
authors.forename: Yusaku
authors.initials: Y
authors.lastname: Endou
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D018450:Disease Progression; D005260:Female; D006331:Heart Diseases / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D007091:Image Processing, Computer-Assisted / Q000379:methods*; D008279:Magnetic Resonance Imaging / Q000379:methods*; D009206:Myocardium / Q000473:pathology*; D056693:Propionic Acidemia / Q000150:complications / Q000175:diagnosis*; D013997:Time Factors