title: Minimizing joint damage: the role of nurses in promoting adherence to hemophilia treatment.
abstract: Hemophilia is a genetic disorder characterized by spontaneous or excessive bleeding predominantly into the weight-bearing joints or muscles. Synovial bleeding can lead to joint damage and disability. Recent studies have shown that prophylactic therapy may prevent joint damage in children with severe hemophilia. However, adherence to these regimens is often suboptimal. Barriers to adherence include lack of understanding of the disease and the time-consuming nature of infusions. Nurses play a critical role in promoting adherence to prophylactic regimens, particularly for adolescent patients. By providing individualized education and support, nurses can help promote joint therapies and minimize disability in patients with severe hemophilia.
authors.affiliation: Haemophilia Centre, Great Ormond Street Hospital for Children NHS Trust, Great Ormond Street, London, United Kingdom.
authors.forename: Kate
authors.initials: K
authors.lastname: Khair
mesh_terms: D000293:Adolescent; D001779:Blood Coagulation Factors / Q000627:therapeutic use*; D002648:Child; D004496:Education, Continuing; D006467:Hemophilia A / Q000150:complications / Q000188:drug therapy* / Q000451:nursing; D006470:Hemorrhage / Q000150:complications*; D006801:Humans; D007592:Joint Diseases / Q000209:etiology / Q000517:prevention & control*; D024802:Nurse's Role; D010349:Patient Compliance
chemical_list: D001779:Blood Coagulation Factors