[Association of plastic bronchitis to protein-losing enteropathy after fontan operation].
We report an unusual case of association of plastic bronchitis (PB) to protein-losing enteropathy (PLE) in a girl of 4 years and 9 months of age with double inlet single left ventricle and ventriculoarterial concordance. submitted to total cavopulmonary surgery. with an intracardiac lateral tunnel at the age of three. The elimination of the 10 cm fibrin bronchial mold (PB) and the alpha-1-antitrypsin elevation of 52 mg/g in feces had both become outstanding. Using sildenafil. the thoracic duct ligature and the cardiac transplant were programmed in case of continuity of the process.
Guimarães
Vanessa Alves
VA
Instituto do Coração (InCor), Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo, São Paulo, SP, Brasil.
Atik
Edmar
E
Castelli
Jussara Bianchi
JB
Ikari
Nana Miura
NM
Thomaz
Ana Maria
AM
Lopes
Antonio Augusto Barbosa
AA
D001991:Bronchitis / Q000209:etiology*; D002675:Child, Preschool; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D011504:Protein-Losing Enteropathies / Q000209:etiology*