Case report: Sanjad--Sakati syndrome: dental findings and treatment.
BACKGROUND
Sanjad--Sakati syndrome (SSS) is a genetic disease confined to Arab populations in the Middle- East countries and characterized by hypoparathyroidism, hypocalcaemia and hyperphosphataemia, severe intrauterine and postnatal growth failure, respiratory infection susceptibility prone, dwarfism, mental retardation, seizures, craniofacial dysmorphic features as retromicrognathia and abnormal dentition.


METHODS
A 12 year-old child was referred who needed dental treatment because of his oral and systemic condition. Radiographic findings showed agenesis of 12 permanent teeth (all canines and premolars).


METHODS
Because of the child's physical limitations and cooperation, treatment was under general anaesthesia. Plaque removal, restorations and extractions of infected teeth were performed.


RESULTS
The child was observed after one year, plaque removal was carried out and fluoride varnish was placed on all teeth. However, the patient died 18 months later as a result of pulmonary complications.


CONCLUSIONS
People with poor systemic conditions and physical limitations are prone to dental health neglect. Early professional advice and treatment, and periodical follow-up can improve quality of life of these patients.
Wasersprung
D
D
Department of Paediatric Dentistry, The Maurice and Gabriela Goldschleger School of Dental Medicine, Tel Aviv University, Tel Aviv, Israel.
Platis
C M
CM
Cohen
S
S
Kaczko
L
L
Zunser
I
I
Peretz
B
B
Katz
J
J
D000015:Abnormalities, Multiple; D002648:Child; D003241:Consanguinity; D019465:Craniofacial Abnormalities / Q000150:complications; D017742:Dental Care for Chronically Ill; D003730:Dental Care for Persons with Disabilities; D003773:Dental Plaque / Q000628:therapy; D003777:Dental Prophylaxis / Q000379:methods*; D003793:Dental Restoration, Permanent / Q000379:methods; D019988:Children with Disabilities; D004392:Dwarfism; D019066:Facies; D017809:Fatal Outcome; D006801:Humans; D007011:Hypoparathyroidism / Q000150:complications / Q000151:congenital; D008607:Intellectual Disability; D008297:Male; D013577:Syndrome; D014071:Tooth Abnormalities / Q000150:complications*; D014081:Tooth Extraction / Q000379:methods