Approach to incidentally diagnosed isolated ventricular noncompaction of myocardium.
Isolated ventricular noncompaction (IVNC) is a congenital cardiomyopathy characterized by a distinctive ("spongy") morphological appearance of the left ventricular (LV) myocardium. It is rare but, with improved imaging modalities and awareness, it is being reported more frequently. Clinical manifestations may range from being asymptomatic to heart failure, arrhythmias, sudden cardiac death, and systemic thromboembolism. With the increasing reporting frequency, the implications of incidentally diagnosed noncompaction need to be addressed. We came across two cases at our medical center which raised important practical questions.
Mid America Cardiology and Section of Cardiovascular Diseases, The University of Kansas Hospital and Medical Center, Kansas City, KS 66160, USA. jlvacek@mac.md
Sravanthi
S
Nagavalli
James L
JL
Vacek
D000368:Aged; D003937:Diagnosis, Differential; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006801:Humans; D033162:Incidental Findings; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis* / Q000235:genetics / Q000503:physiopathology / Q000628:therapy; D008297:Male; D008875:Middle Aged; D011379:Prognosis