Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report.
Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.
Department of Neuroanesthesia, National Institute of Mental Health and Neurosciences, Bangalore, 560 029, India.
Lakshminarsimhaiah
L
Geetha
Muthuchellappan
M
Radhakrishnan
Biligiri Sridhar
BS
Raghavendra
G S Umamaheswara
GS
Rao
Bhagavatula
B
Indira Devi
D000328:Adult; D000758:Anesthesia / Q000379:methods*; D019299:Decompression, Surgical; D005260:Female; D005539:Foramen Magnum / Q000601:surgery*; D006801:Humans; D008168:Lung / Q000503:physiopathology; D009085:Mucopolysaccharidosis IV / Q000150:complications* / Q000503:physiopathology