Heart transplantation in an adult patient with isolated noncompaction of the left ventricular myocardium.
Isolated noncompaction of the ventricular myocardium is defined as a rare cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibers and meshwork, an important process in myocardial development, in absence of any coexisting congenital heart lesions. A lot of controversies exist about diagnostic criteria, nomenclature, origin, pathogenesis, and prognosis of this disease. Here, we describe an adult patient with isolated left ventricular noncompaction who presented with worsening congestive heart failure and was successfully treated with heart transplantation.
Glaveckaite
Sigita
S
Clinic of Heart and Vascular Medicine, Vilnius University, Lithuania. sigita.glaveckaite@santa.lt
Rucinskas
Kestutis
K
Celutkiene
Jelena
J
Maneikiene
Vyte
V
Zakarkaite
Diana
D
Aidietiene
Sigita
S
Valeviciene
Nomeda
N
Mataciūnas
Mindaugas
M
Zurauskas
Edvardas
E
Serpytis
Pranas
P
Laucevicius
Aleksandras
A
D000328:Adult; D002312:Cardiomyopathy, Hypertrophic / Q000175:diagnosis; D004452:Echocardiography; D004562:Electrocardiography; D005500:Follow-Up Studies; D016027:Heart Transplantation; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis / Q000000981:diagnostic imaging; D008279:Magnetic Resonance Imaging; D008297:Male; D013902:Radiography, Thoracic; D013318:Stroke Volume; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D018615:Ultrasonography, Doppler, Color