Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report.
Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.
Geetha
Lakshminarsimhaiah
L
Department of Neuroanesthesia, National Institute of Mental Health and Neurosciences, Bangalore, 560 029, India.
Radhakrishnan
Muthuchellappan
M
Raghavendra
Biligiri Sridhar
BS
Rao
G S Umamaheswara
GS
Indira Devi
Bhagavatula
B
D000328:Adult; D000758:Anesthesia / Q000379:methods*; D019299:Decompression, Surgical; D005260:Female; D005539:Foramen Magnum / Q000601:surgery*; D006801:Humans; D008168:Lung / Q000503:physiopathology; D009085:Mucopolysaccharidosis IV / Q000150:complications* / Q000503:physiopathology