Heart transplantation in an adult patient with isolated noncompaction of the left ventricular myocardium.
Isolated noncompaction of the ventricular myocardium is defined as a rare cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibers and meshwork, an important process in myocardial development, in absence of any coexisting congenital heart lesions. A lot of controversies exist about diagnostic criteria, nomenclature, origin, pathogenesis, and prognosis of this disease. Here, we describe an adult patient with isolated left ventricular noncompaction who presented with worsening congestive heart failure and was successfully treated with heart transplantation.
Clinic of Heart and Vascular Medicine, Vilnius University, Lithuania. sigita.glaveckaite@santa.lt
Sigita
S
Glaveckaite
Kestutis
K
Rucinskas
Jelena
J
Celutkiene
Vyte
V
Maneikiene
Diana
D
Zakarkaite
Sigita
S
Aidietiene
Nomeda
N
Valeviciene
Mindaugas
M
Mataciūnas
Edvardas
E
Zurauskas
Pranas
P
Serpytis
Aleksandras
A
Laucevicius
D000328:Adult; D002312:Cardiomyopathy, Hypertrophic / Q000175:diagnosis; D004452:Echocardiography; D004562:Electrocardiography; D005500:Follow-Up Studies; D016027:Heart Transplantation; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis / Q000000981:diagnostic imaging; D008279:Magnetic Resonance Imaging; D008297:Male; D013902:Radiography, Thoracic; D013318:Stroke Volume; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D018615:Ultrasonography, Doppler, Color