title: Autoimmune pancreatitis with atypical imaging findings that mimicked an endocrine tumor.
abstract: Autoimmune pancreatitis (AIP) is a rare cause of recurrent acute pancreatitis or chronic pancreatitis in middle-aged patients, and is characterised by a marked infiltration of lymphocytes and plasma cells in pancreatic tissue. Diagnosis of focal forms can be difficult as AIP may mimic pancreatic adenocarcinoma. Pediatric cases of AIP are exceptional. We report the case of a 15-year-old girl who had a focal AIP and associated cholangitis, with a very unusual vascularized mass that mimicked a pancreatic endocrine tumor. The diagnosis was obtained by a pancreatic biopsy, thus avoiding surgical resection, and all the clinical, biological and radiological abnormalities resolved after steroid therapy with 6 mo of follow-up.
authors.affiliation: Department of Gastroenterology and Digestive Oncology, Ambroise Paré Hospital, 9, avenue Charles de Gaulle, 92100 Boulogne-Billancourt, France.
authors.forename: Cindy
authors.initials: C
authors.lastname: Neuzillet
authors.forename: Céline
authors.initials: C
authors.lastname: Lepère
authors.forename: Mostafa
authors.initials: M
authors.lastname: El Hajjam
authors.forename: Laurent
authors.initials: L
authors.lastname: Palazzo
authors.forename: Monique
authors.initials: M
authors.lastname: Fabre
authors.forename: Hajer
authors.initials: H
authors.lastname: Turki
authors.forename: Pascal
authors.initials: P
authors.lastname: Hammel
authors.forename: Philippe
authors.initials: P
authors.lastname: Rougier
authors.forename: Emmanuel
authors.initials: E
authors.lastname: Mitry
mesh_terms: D000293:Adolescent; D001327:Autoimmune Diseases / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology; D002761:Cholangitis / Q000175:diagnosis; D003937:Diagnosis, Differential; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D010190:Pancreatic Neoplasms / Q000175:diagnosis; D010195:Pancreatitis / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology; D011241:Prednisone / Q000627:therapeutic use
chemical_list: D005938:Glucocorticoids; D011241:Prednisone