title: A case of incontinentia pigmenti associated with multiorgan abnormalities.
abstract: Incontinentia pigmenti is a systemic disorder affecting the skin, teeth, eyes, nervous tissue, hair, nails, musculoskeletal system, and heart. We describe an 11-month-old girl with incontinentia pigmenti associated with a ventricular septal defect, left hemiatrophy, hemangiomas, an abnormal labial frenum, and spastic cerebral palsy manifested as left hemiplegia and developmental delay. We believe this patient illustrates that incontinentia pigmenti is a systemic disorder necessitating a multidisciplinary approach to management.
authors.affiliation: Department of Dermatology, University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea.
authors.forename: Woon-Kyong
authors.initials: WK
authors.lastname: Chung
authors.forename: Deok-Woo
authors.initials: DW
authors.lastname: Lee
authors.forename: Sung-Eun
authors.initials: SE
authors.lastname: Chang
authors.forename: Mi-Woo
authors.initials: MW
authors.lastname: Lee
authors.forename: Jee-Ho
authors.initials: JH
authors.lastname: Choi
authors.forename: Kee-Chan
authors.initials: KC
authors.lastname: Moon