Metachronous Multiplicity of Spinal Cord Arteriovenous Fistula and Spinal Dural AVF in a Patient with Hereditary Haemorrhagic Telangiectasia.
HHT (Hereditary Haemorrhagic Telangiectasia or Rendu Osler Weber disease) is a known autosomal dominant dysplasia. The first clinical presentation of HHT in a child may be a cerebral or spinal AVM. We present the case of a young boy with HHT who had a previous spinal cord AVF treated by surgical obliteration and then presented with a spinal dural AVF nine months later. This patient had surgical obliteration of a spinal cord perimedullary AVF and subsequently developed a new spinal dural AVF at a different level. The diagnosis was made by spinal MR imaging and spinal angiography.
Ling
J C M
JC
Department of Medical Imaging, Buddhist Tzu Chi Medical Center, Hualien; Taiwan - tkkim@kumc.or.kr.
Agid
R
R
Nakano
S
S
Souza
M P S
MP
Reintamm
G
G
Terbrugge
K G
KG