Pulmonary hypertension secondary to partial pulmonary venous obstruction in a child with Cantu syndrome.
We report on an African-American male with Cantu syndrome who required a pericardial window for a significant pericardial effusion in infancy and was subsequently found to have partial pulmonary venous obstruction (PVO) leading to pulmonary hypertension. Measurement of bilateral pulmonary capillary wedge pressures is important to uncover partial PVO.
Kobayashi
Daisuke
D
Department of Pediatrics, Wake Forest University School of Medicine, Winston-Salem, NC, USA. dkobayas@wfubmc.edu
Cook
Amanda L
AL
Williams
Derek A
DA
D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D006332:Cardiomegaly / Q000150:complications / Q000000981:diagnostic imaging; D002648:Child; D002675:Child, Preschool; D040181:Genetic Diseases, X-Linked / Q000150:complications / Q000000981:diagnostic imaging; D006801:Humans; D006976:Hypertension, Pulmonary / Q000000981:diagnostic imaging / Q000209:etiology*; D006983:Hypertrichosis / Q000150:complications / Q000000981:diagnostic imaging; D008297:Male; D010009:Osteochondrodysplasias / Q000150:complications / Q000000981:diagnostic imaging; D010490:Pericardial Effusion / Q000000981:diagnostic imaging; D010493:Pericarditis / Q000188:drug therapy; D011668:Pulmonary Veno-Occlusive Disease / Q000150:complications*; D011669:Pulmonary Wedge Pressure; D011859:Radiography; D013577:Syndrome
D000900:Anti-Bacterial Agents