title: Kaposiform hemangioendothelioma of the kidney: an unusual presentation of a rare vascular neoplasm.
abstract: Kaposiform hemangioendothelioma (KHE) is a rare, locally aggressive, vascular spindle-cell proliferation, with resemblance to Kaposi sarcoma. Usually, this tumor occurs in the skin and the retroperitoneum. We described a girl with a kidney localization and extension into the inferior vena cava and even into the right atrium. The case presented here is unique in 2 ways. First, kidney involvement of KHE has never been described in the literature until now. Second, and most remarkably, extensive tumor thrombosis suggests surgical excision even with cardiopulmonary bypass. The KHE of the kidney is a rare tumor but should be taken into account in the differential diagnosis with other pediatric renal neoplasms.
authors.affiliation: Pediatric Department, Pediatric Oncology Service, Second University of Naples, Naples, Italy. paolo.indolfi@unina2.it
authors.forename: Paolo
authors.initials: P
authors.lastname: Indolfi
authors.forename: Vittoria
authors.initials: V
authors.lastname: Donofrio
authors.forename: Claudia
authors.initials: C
authors.lastname: Fusco
authors.forename: Martina
authors.initials: M
authors.lastname: Di Martino
authors.forename: Daniela
authors.initials: D
authors.lastname: Di Pinto
authors.forename: Cristiana
authors.initials: C
authors.lastname: Indolfi
authors.forename: Agostino Maioli Castriota
authors.initials: AM
authors.lastname: Scanderbech
authors.forename: Fiorina
authors.initials: F
authors.lastname: Casale
mesh_terms: D002675:Child, Preschool; D005260:Female; D006390:Hemangioendothelioma / Q000175:diagnosis* / Q000378:metabolism / Q000628:therapy; D006801:Humans; D007124:Immunoenzyme Techniques; D007680:Kidney Neoplasms / Q000175:diagnosis* / Q000378:metabolism / Q000628:therapy; D012514:Sarcoma, Kaposi / Q000175:diagnosis* / Q000378:metabolism / Q000628:therapy; D019043:Vascular Neoplasms / Q000175:diagnosis* / Q000378:metabolism / Q000628:therapy