title: [Primitive malignant rhabdoid tumor of the central nervous system in an adolescent. A case study].
abstract: Primitive malignant rhabdoid tumors of the central nervous system are rare and have a poor prognosis. Adult and adolescent cases are exceptional. We report the case of a 16-year-old girl who presented an intratumoral hemorrhage in a rhabdoid tumor. She was treated with surgery, followed by intravenous and intrathecal chemotherapy. Despite intensive treatment, she died 5 months after diagnosis. We discuss the different therapeutic options for this patient and review the literature on this kind of tumor.
authors.affiliation: Service de neurochirurgie, CHU de Reims, 45, rue Cognacq-Jay, 51092 Reims, France.
authors.forename: C
authors.initials: C
authors.lastname: Eap
authors.forename: C-F
authors.initials: CF
authors.lastname: Litré
authors.forename: R
authors.initials: R
authors.lastname: Noudel
authors.forename: E
authors.initials: E
authors.lastname: Theret
authors.forename: J
authors.initials: J
authors.lastname: Duntze
authors.forename: P
authors.initials: P
authors.lastname: Collin
authors.forename: P
authors.initials: P
authors.lastname: Rousseaux
mesh_terms: D000293:Adolescent; D001932:Brain Neoplasms / Q000175:diagnosis / Q000628:therapy; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D018335:Rhabdoid Tumor / Q000175:diagnosis / Q000628:therapy