Solitary lymphangioleiomyoma of pancreas mimicking pancreatic pseudocyst--a case report.
BACKGROUND
Lymphangioleiomyomatosis (LAM) is a rare disease characterized by proliferation of morphologically distinguishable smooth muscle cells in the lymphatics and lymph nodes of the pulmonary parenchyma in most cases. Extrapulmonary LAM is a rare condition and is found to occur concurrently, before or after pulmonary LAM, and show strong association with tuberous sclerosis.


CONCLUSIONS
The literature regarding extrapulmonary LAM without associated pulmonary LAM is limited due to the extreme rarity of the cases. We hereby describe clinical, pathological and radiological features of primary pancreatic LAM presenting clinicoradiologically as pseudocyst of pancreas in a 43-year-old lady.


CONCLUSIONS
The present case is unique as LAM in pancreas without associated pulmonary LAM has never been reported in the literature before.
Singh
Meeta
M
Maulana Azad Medical College and Lok Nayak Hospital, Bahadur Shah Zafar Marg, New Delhi, 110002, India.
Saroha
Vijay
V
Wadhwa
Rachna
R
Khurana
Nita
N
Kakkar
A K
AK
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D008203:Lymphangiomyoma / Q000473:pathology* / Q000601:surgery; D010190:Pancreatic Neoplasms / Q000473:pathology* / Q000601:surgery; D010192:Pancreatic Pseudocyst / Q000473:pathology*