Kindler syndrome causing severe cicatricial ectropion.
A 32-year-old female with Kindler syndrome presented with a 5-year history of lower eyelid malposition, corneal exposure, and recurrent erosions. Severe anterior lamellar cicatricial changes were noted bilaterally, with bilateral lower eyelid ectropion and retraction. Tarsal eversion was noted on the left lower eyelid. The patient had repeatedly failed conservative treatments for keratopathy and was treated surgically, with resolution of corneal disease and improved lower eyelid position. A review of Kindler syndrome is provided, geared toward the oculoplastic surgeon who may participate in the care of these patients.
Lelli
Gary J
GJ
Division of Oculoplastic Surgery, Department of Ophthalmology, Weill Cornell Medical College, New York, NY 10021, USA. gjl9003@med.cornell.edu
D000328:Adult; D001768:Blister / Q000150:complications / Q000601:surgery; D017439:Cicatrix, Hypertrophic / Q000209:etiology* / Q000601:surgery; D004483:Ectropion / Q000209:etiology* / Q000601:surgery; D004820:Epidermolysis Bullosa / Q000150:complications / Q000601:surgery; D005260:Female; D006801:Humans; D013508:Ophthalmologic Surgical Procedures; D010510:Periodontal Diseases / Q000150:complications / Q000601:surgery; D010787:Photosensitivity Disorders / Q000150:complications / Q000601:surgery