title: [Recurrent ovarian fibromas in condition of Gorlin syndrome].
abstract: Gorlin syndrome also known as basal cell nevus syndrome is a rare autosomal dominant condition with variable expression. This syndrome is characterized by many anomalies of development and by the propensity of developing multiple neoplasms. We report a case of a 20-years-old French patient who has relapsing ovarian bilateral fibromas in condition of Gorlin syndrome. These fibromas are present in 25 % of Gorlin syndrome cases, which often are bilateral. The economic resection of these fibromas is recommended in spite of the risk of recurrence to preserve the fertility.
authors.affiliation: Service de gynécologie, hôpital d'Haguenau, université de Strasbourg, 64, avenue du Professeur-René-Leriche, 67504 Haguenau cedex, France. omranihind@yahoo.fr
authors.forename: H
authors.initials: H
authors.lastname: Omrani
authors.forename: I
authors.initials: I
authors.lastname: Hui Bon Hoa
authors.forename: H
authors.initials: H
authors.lastname: Bennis
authors.forename: M
authors.initials: M
authors.lastname: Lehmann
authors.forename: V
authors.initials: V
authors.lastname: Zerr
mesh_terms: D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000150:complications*; D005260:Female; D005350:Fibroma / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D009364:Neoplasm Recurrence, Local; D010051:Ovarian Neoplasms / Q000175:diagnosis* / Q000601:surgery