[Recurrent ovarian fibromas in condition of Gorlin syndrome].
Gorlin syndrome also known as basal cell nevus syndrome is a rare autosomal dominant condition with variable expression. This syndrome is characterized by many anomalies of development and by the propensity of developing multiple neoplasms. We report a case of a 20-years-old French patient who has relapsing ovarian bilateral fibromas in condition of Gorlin syndrome. These fibromas are present in 25 % of Gorlin syndrome cases, which often are bilateral. The economic resection of these fibromas is recommended in spite of the risk of recurrence to preserve the fertility.
Omrani
H
H
Service de gynécologie, hôpital d'Haguenau, université de Strasbourg, 64, avenue du Professeur-René-Leriche, 67504 Haguenau cedex, France. omranihind@yahoo.fr
Hui Bon Hoa
I
I
Bennis
H
H
Lehmann
M
M
Zerr
V
V
D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000150:complications*; D005260:Female; D005350:Fibroma / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D009364:Neoplasm Recurrence, Local; D010051:Ovarian Neoplasms / Q000175:diagnosis* / Q000601:surgery