[Primitive malignant rhabdoid tumor of the central nervous system in an adolescent. A case study].
Primitive malignant rhabdoid tumors of the central nervous system are rare and have a poor prognosis. Adult and adolescent cases are exceptional. We report the case of a 16-year-old girl who presented an intratumoral hemorrhage in a rhabdoid tumor. She was treated with surgery, followed by intravenous and intrathecal chemotherapy. Despite intensive treatment, she died 5 months after diagnosis. We discuss the different therapeutic options for this patient and review the literature on this kind of tumor.
Eap
C
C
Service de neurochirurgie, CHU de Reims, 45, rue Cognacq-Jay, 51092 Reims, France.
Litré
C-F
CF
Noudel
R
R
Theret
E
E
Duntze
J
J
Collin
P
P
Rousseaux
P
P
D000293:Adolescent; D001932:Brain Neoplasms / Q000175:diagnosis / Q000628:therapy; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D018335:Rhabdoid Tumor / Q000175:diagnosis / Q000628:therapy