The pediatric renal clear cell "sugar" tumor: pseudo-alveolar structure mimicking clear cell renal carcinoma.
The primary extrapulmonary sugar tumor (PEST) is rare. Up to now, only 16 cases of PEST have been reported, including 5 pediatric cases. We report a renal benign PEST in a 16-year-old boy, which is the first such case to be reported in the pediatric kidney. The tumor was composed of clear and eosinophilic epithelioid cells, growing with nest and pseudoalveolar structure, which can be confused with renal clear cell carcinoma. The tumor cells were positive for melanocytic and negative for epithelial markers. The tumor was enucleated, and the patient was well without recurrence 21 months after surgery.
Shu
Hong
H
Department of Pathology, Shengjing Hospital of China Medical University, Shenyang, Liaoning, China. shuhong0302@hotmail.com
Gao
Ai-Feng
AF
Yang
Xiang-Hong
XH
Lu
Qing-Jie
QJ
D000293:Adolescent; D002292:Carcinoma, Renal Cell / Q000473:pathology*; D003937:Diagnosis, Differential; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology*; D008297:Male; D054973:Perivascular Epithelioid Cell Neoplasms / Q000473:pathology*