title: Severe pulmonary hypertension in histiocytosis X: long-term improvement with bosentan.
authors.forename: L
authors.initials: L
authors.lastname: Kiakouama
authors.forename: V
authors.initials: V
authors.lastname: Cottin
authors.forename: B
authors.initials: B
authors.lastname: Etienne-Mastroïanni
authors.forename: C
authors.initials: C
authors.lastname: Khouatra
authors.forename: M
authors.initials: M
authors.lastname: Humbert
authors.forename: J F
authors.initials: JF
authors.lastname: Cordier
mesh_terms: D000959:Antihypertensive Agents / Q000627:therapeutic use*; D000077300:Bosentan; D004417:Dyspnea / Q000188:drug therapy; D006439:Hemodynamics / Q000187:drug effects; D006646:Histiocytosis, Langerhans-Cell / Q000188:drug therapy*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy* / Q000503:physiopathology; D008297:Male; D008875:Middle Aged; D010879:Piperazines / Q000627:therapeutic use; D011687:Purines / Q000627:therapeutic use; D012720:Severity of Illness Index; D000068677:Sildenafil Citrate; D013449:Sulfonamides / Q000627:therapeutic use*; D013450:Sulfones / Q000627:therapeutic use
chemical_list: D000959:Antihypertensive Agents; D010879:Piperazines; D011687:Purines; D013449:Sulfonamides; D013450:Sulfones; D000068677:Sildenafil Citrate; D000077300:Bosentan