A 21-year-old man with systemic-onset juvenile rheumatoid arthritis, cough and progressive dyspnea.
Primary or nonobstructive, endogenous lipoid pneumonia is a rare clinical entity usually associated with an underlying systemic disease. The present report describes a case involving a 21-year-old man with systemic-onset juvenile rheumatoid arthritis who developed primary endogenous lipoid pneumonia. Multiple treatment regimens were attempted; however, definitive management was only achieved through double-lung transplantation.
Leber
A
A
Department of Medicine, University Health Network, University of Toronto, Toronto, Ontario, Canada.
Carette
S
S
Chapman
K R
KR
Hwang
D M
DM
Singer
L G
LG
Marras
T K
TK
D001171:Arthritis, Juvenile / Q000150:complications*; D003371:Cough / Q000209:etiology; D004417:Dyspnea / Q000209:etiology; D006801:Humans; D016040:Lung Transplantation; D008297:Male; D011014:Pneumonia / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D055815:Young Adult