title: Successful initiation and maintenance of hemodialysis in an adult patient with complete transposition of the great arteries.
abstract: Cyanotic congenital heart disease (CCHD) is a life-threatening cardiac defect that requires palliative or corrective surgery in early life. Major advances in medical and surgical management have resulted in the survival of CCHD patients to adulthood with or without corrective surgery, though some are at risk of development of end-stage renal disease (ESRD) due to cyanotic nephropathy (CN). There is little or no information on the initiation and maintenance of hemodialysis (HD) in such patients. We present here a case of a 44-year-old man with complete transposition of the great arteries and CN-related ESRD. He had only received a bi-directional Glenn's operation and still suffered persistent severe hypoxemia and impaired cardiac function. ESRD was successfully treated with HD over more than 4 years. The case emphasizes the need for special attention in the selection and initiation of renal replacement therapy.
authors.affiliation: Department of Medicine and Clinical Science, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.
authors.forename: Shunsuke
authors.initials: S
authors.lastname: Yamada
authors.forename: Hideki
authors.initials: H
authors.lastname: Yotsueda
authors.forename: Masatomo
authors.initials: M
authors.lastname: Taniguchi
authors.forename: Kazuhiko
authors.initials: K
authors.lastname: Tsuruya
authors.forename: Hideki
authors.initials: H
authors.lastname: Hirakata
authors.forename: Mitsuo
authors.initials: M
authors.lastname: Iida
mesh_terms: D000328:Adult; D003490:Cyanosis / Q000150:complications* / Q000601:surgery; D006330:Heart Defects, Congenital / Q000150:complications* / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D007674:Kidney Diseases / Q000209:etiology / Q000473:pathology / Q000628:therapy; D007676:Kidney Failure, Chronic / Q000209:etiology / Q000473:pathology / Q000628:therapy; D008297:Male; D006435:Renal Dialysis; D014188:Transposition of Great Vessels / Q000150:complications / Q000601:surgery