A case of retiform-hemangioendothelioma with unusual presentation and aggressive clinical features.
Retiform hemangioendothelioma (RH) is an extremely rare low-grade angiosarcoma mainly involving the skin and subcutaneous tissue. Clinically patients often present with an asymptomatic slow-growing solitary nodular or plaque-like lesion. RH is characterized by frequent local recurrences but a very low metastatic rate. Here we reported a case of RH in a 61-year-old Chinese woman who presented with a rapid growing cutaneous plaque-like lesion on her right scalp, followed by another lesion behind the right ear. The lesions were associated with paroxysmal sharp needle-stabbing like headache. She underwent wide excision and skin engraftment. Three months post surgery, she experienced tumor recurrence, and died 9 months after the initial diagnosis.
Zhang
Guiying
G
Department of Dermatology , the Second Xiangya Hospital, Central South University, Changsha, Hunan, China.
Lu
Qianjin
Q
Yin
Heng
H
Wen
Haiquan
H
Su
Yuwen
Y
Li
Daiqiang
D
Xiao
Rong
R
D005260:Female; D006390:Hemangioendothelioma / Q000473:pathology* / Q000601:surgery; D006394:Hemangiosarcoma / Q000473:pathology* / Q000601:surgery; D006801:Humans; D007150:Immunohistochemistry; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local / Q000473:pathology; D012535:Scalp / Q000473:pathology* / Q000601:surgery; D012878:Skin Neoplasms / Q000473:pathology* / Q000601:surgery