Extended cardiac resection for obstructing pseudotumor due to Ormond disease.
A 60-year-old man presented with symptoms from an intracardiac mass. His medical history included retroperitoneal fibrosis (Ormond disease). Magnetic resonance imaging revealed an obstructing bilobular mass in the right atrium, located at the caval junction and extending intramurally into the atria, septum, and right ventricle. En bloc resection of the right atrium, interatrial septum, dome of the left atrium, vena cava, anterior tricuspid annulus, right coronary artery, and partial right ventriculectomy was completed with right ventricular repair, tricuspid valve replacement, and left and right atrial replacement with bovine pericardium. This lesion was a myofibroblastic tumor with the same histologic features as his retroperitoneal fibrosis.
Solomon
Brian
B
Department of Cardiothoracic Surgery, New York University School of Medicine, and New York Harbor Veterans Healthcare System, New York, NY, USA.
Grossi
Eugene A
EA
Monteith
Duane
D
Donnino
Robert M
RM
Srichai
Barbara
B
Dellis
Sophie L
SL
Galloway
Aubrey C
AC
D006348:Cardiac Surgical Procedures / Q000379:methods; D006104:Granuloma, Plasma Cell / Q000209:etiology* / Q000601:surgery*; D006331:Heart Diseases / Q000209:etiology* / Q000601:surgery*; D006801:Humans; D008297:Male; D008875:Middle Aged; D012185:Retroperitoneal Fibrosis / Q000150:complications*