Anaesthetic management of a newborn with galactosaemia for congenital heart surgery.
Galactosaemia is an autosomal recessive metabolic disorder that occurs due to galactose-1-phosphate uridyl transferase enzyme deficiency that leads to hepatic, ophthalmic, neural and renal derangements. Association of cyanotic congenital heart disease with galactosaemia is a rare occurence and a matter of great concern for the anaesthesiologist during open heart surgery. In this case report, the perioperative management of a newborn with galactosaemia operated for correction of transposition of great arteries (TGA) is discussed.
Choudhury
Arindam
A
Senior resident, Department of Cardiac Anaesthesiology, Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi 110029.
Das
Sambhunath
S
Kiran
Usha
U