Pachydermoperiostosis accompanied by heart failure.
Pachydermoperiostosis or primary hypertrophic osteoarthropathy is an uncommon disease of acromegaloid facial feature, but characterized by unique phenotype (digital clubbing and pachydermia) and distinctive radiographic appearances like periostosis. We experienced a case with complete form of pachydermoperiostosis accompanied by heart failure. He presented with typical features consisting of clubbing with enlargement of the hand, thickening of facial skin and periosteal new bone formation involving lower leg. Echocardiography revealed severely decreased left ventricular systolic function. Treatment with medications resulted in an improvement of cardiac function and symptom. There is no previous report documenting pachydermoperiostosis accompanied by heart failure. We report that case for the first time.
Shin
Kwen-Chul
KC
Division of Cardiology, Department of Internal Medicine, Gachon University Gil Hospital, Incheon, Korea.
Chung
Wook-Jin
WJ
Lee
Ki Young
KY
Shin
Mi-Seung
MS
Kim
Sei-Hyun
SH
Jo
Yun Jeong
YJ
Park
Yae Min
YM
Ahn
Tae Hoon
TH
Choi
In Suk
IS
Shin
Eak Kyun
EK