Obstructed uteri with a cervix and vagina.
OBJECTIVE
To describe a rare anomaly of the female reproductive tract and review the embryology associated with the defect.


METHODS
Case report and review of the literature.


METHODS
Major academic medical center.


METHODS
A 14-year-old girl with two hemiuteri lacking any communication with a single normal midline cervix and vagina.


METHODS
Diagnostic laparoscopy with chromopertubation to identify the anomaly and subsequent bilateral supracervical hemihysterectomies.


METHODS
Incidence, pathogenesis, fertility implications, and treatment options for patients with congenital defects in the upper vagina, cervix, and uterus.


RESULTS
Based on classic embryology, the lower vagina forms from the urogenital sinus while the upper vagina, cervix, and uterus form from the müllerian ducts. If a cervix is present, then the upper vagina and uterus are also usually present and should communicate.


CONCLUSIONS
This anomaly cannot be fully explained by traditional embryologic developmental theory. It is likely that an insult occurred between 9 weeks, when the uterovaginal canal is formed, and 12 weeks, when the müllerian ducts fuse.
Wright
Kelly Nicole
KN
Division of Gynecology, Children's Hospital, Harvard Medical School, Boston, Massachusetts 02115, USA.
Okpala
Ogochukwu
O
Laufer
Marc R
MR
D000293:Adolescent; D002584:Cervix Uteri / Q000002:abnormalities* / Q000473:pathology; D005260:Female; D006801:Humans; D007247:Infertility, Female / Q000473:pathology*; D010535:Laparoscopy; D009095:Mullerian Ducts / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities* / Q000473:pathology