title: Pachydermoperiostosis accompanied by heart failure.
abstract: Pachydermoperiostosis or primary hypertrophic osteoarthropathy is an uncommon disease of acromegaloid facial feature, but characterized by unique phenotype (digital clubbing and pachydermia) and distinctive radiographic appearances like periostosis. We experienced a case with complete form of pachydermoperiostosis accompanied by heart failure. He presented with typical features consisting of clubbing with enlargement of the hand, thickening of facial skin and periosteal new bone formation involving lower leg. Echocardiography revealed severely decreased left ventricular systolic function. Treatment with medications resulted in an improvement of cardiac function and symptom. There is no previous report documenting pachydermoperiostosis accompanied by heart failure. We report that case for the first time.
authors.affiliation: Division of Cardiology, Department of Internal Medicine, Gachon University Gil Hospital, Incheon, Korea.
authors.forename: Kwen-Chul
authors.initials: KC
authors.lastname: Shin
authors.forename: Wook-Jin
authors.initials: WJ
authors.lastname: Chung
authors.forename: Ki Young
authors.initials: KY
authors.lastname: Lee
authors.forename: Mi-Seung
authors.initials: MS
authors.lastname: Shin
authors.forename: Sei-Hyun
authors.initials: SH
authors.lastname: Kim
authors.forename: Yun Jeong
authors.initials: YJ
authors.lastname: Jo
authors.forename: Yae Min
authors.initials: YM
authors.lastname: Park
authors.forename: Tae Hoon
authors.initials: TH
authors.lastname: Ahn
authors.forename: In Suk
authors.initials: IS
authors.lastname: Choi
authors.forename: Eak Kyun
authors.initials: EK
authors.lastname: Shin