Partial Klüver-Bucy syndrome in a patient with acute disseminated encephalomyelitis.
The symptoms of Klüver-Bucy syndrome (KBS) include hyperorality, hypersexuality, visual agnosia, hypermetamorphosis and decreased motor or vocal reaction to fear- or anger-provoking stimuli. This syndrome has been associated with a wide variety of neurodegenerative disorders, as well as traumatic, non-traumatic and infectious brain injuries. We report an 11-year-old boy who developed a fairly classical presentation of KBS, presumably in the setting of post-infectious acute disseminated encephalomyelitis (ADEM). This patient's presentation is a reminder of this rare syndrome and extends the clinical manifestations of ADEM, which is a relatively more common condition.
Jha
Sanjeev
S
Department of Neurology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Raebareli Road, Lucknow 226 014, Uttar Pradesh, India. sjha@sgpgi.ac.in
Ansari
M K
MK
D002648:Child; D003937:Diagnosis, Differential; D018450:Disease Progression; D004673:Encephalomyelitis, Acute Disseminated / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D020232:Kluver-Bucy Syndrome / Q000175:diagnosis* / Q000209:etiology* / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D012920:Social Behavior Disorders / Q000175:diagnosis* / Q000209:etiology / Q000473:pathology