Pulmonary manifestations of relapsing polychondritis.
Relapsing polychondritis (RP) is a chronic multisystemic disease characterized by recurrent episodes of cartilage inflammation throughout the body. The lower respiratory tract is involved in 20% to 50% of patients and results in significant morbidity. Effective medical therapies and airway interventions are available in experienced centers; however, no single treatment is curative, and the prognosis of RP with airway disease remains overall guarded.
Rafeq
Samaan
S
Beth Israel Deaconess Medical Center, Boston, MA 02215, USA.
Trentham
David
D
Ernst
Armin
A
D004724:Endoscopy; D006801:Humans; D011081:Polychondritis, Relapsing / Q000150:complications*; D011379:Prognosis; D012140:Respiratory Tract Diseases / Q000175:diagnosis* / Q000209:etiology* / Q000503:physiopathology / Q000628:therapy