title: Wegener's granulomatosis of the temporal bone and skull base that mimicked an inflammatory myofibroblastic tumour: a case report.
abstract: OBJECTIVE
  To compare two potential diagnoses of a temporal bone pseudotumour: an inflammatory myofibroblastic tumour and Wegener's granulomatosis.
  
  
  METHODS
  A case of Wegener's granulomatosis that mimicked an inflammatory myofibroblastic tumour is reported. The clinical presentation, staging of the disease, histology, and follow-up are analysed.
  
  
  RESULTS
  Histopathology of the temporal bone failed to provide an accurate diagnosis, even after immunocytochemical analyses. The diagnosis of Wegener's granulomatosis was suspected after biopsy of a pulmonary mass and was confirmed by the presence of anti-neutrophil cytoplasmic antibodies in blood samples.
  
  
  CONCLUSIONS
  Irrespective of the aetiology, a pseudotumour of the temporal bone should always be investigated by biology and radiology. Radiological investigations will allow staging of the disease and specific localisation for biopsies.
authors.affiliation: Department of Otorhinolaryngology, CHU Hautepierre, Strasbourg, France.
authors.forename: A-S
authors.initials: AS
authors.lastname: Carpentier
authors.forename: S
authors.initials: S
authors.lastname: Riehm
authors.forename: A
authors.initials: A
authors.lastname: Charpiot
authors.forename: A
authors.initials: A
authors.lastname: Onea
authors.forename: C
authors.initials: C
authors.lastname: Debry
authors.forename: P
authors.initials: P
authors.lastname: Schultz
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D014890:Granulomatosis with Polyangiitis / Q000175:diagnosis*; D006801:Humans; D009379:Neoplasms, Muscle Tissue / Q000175:diagnosis / Q000503:physiopathology; D019291:Skull Base; D013701:Temporal Bone