Muir-Torre syndrome.
Muir-Torre syndrome (MTS) is an autosomal dominant genodermatosis that consists of unusual cutaneous sebaceous neoplasm, with or without kerathoacantomas and one or more low-grade visceral malignancies, with or without colonic polyps, in the absence of other predisposing factors. This chapter presents a review of the principal clinical and genetic findings in this syndrome and discusses its relation with Lynch syndrome.
Mercader
Pedro
P
Dermatology Service, Hospital General Universitario Morales Meseguer, Murcia, Spain. pedromercader@hotmail.com
D000818:Animals; D006801:Humans; D055653:Muir-Torre Syndrome / Q000235:genetics / Q000378:metabolism / Q000473:pathology / Q000628:therapy