Osteogenesis imperfecta in pregnancy. Case report.
OBJECTIVE
Osteogenesis Imperfecta is a rare condition, especially in obstetric patients. It has an estimated prevalence of 1/10,000 in the general population, and 1/25,000 to 30,000 in obstetric patients. The objective of this report was to present a rare case of a pregnant woman with Osteogenesis Imperfecta undergoing cesarean section.


METHODS
This is a 23 years old gravida on the 38th week, admitted to the maternity ward with loss of amniotic fluid and contractions for four hours, associated with the absence of fetal movements for four days. The patient had a mild form of Osteogenesis Imperfecta without other comorbidities. She was not taking any medication, and she did not have prenatal follow-up. The patient underwent spinal anesthesia in the L(3)-L(4) space, median approach, with a single puncture with a 27G Quincke needle and the administration of hyperbaric 0.5% bupivacaine (10 mg) and morphine (60 microg). She was discharged in the second postoperative day without complaints.


CONCLUSIONS
Fertility is preserved, especially in those patients with type I of the disease, and pregnancy can be carried to term. Delivery is usually surgical due to pelvic deformities in the gravida, cephalopelvic disproportion, and increased incidence of abnormal fetal presentation. The importance of the anesthesiologist in the surgical team relies on the perioperative management and the choice of the most appropriate anesthetic technique for each patient.
Lyra
Ticiana Goyanna
TG
Maternidade de Referência Professor José Maria de Magalhães Netto, CET/SBA of the Santa Casa de Misericórdia da Bahia, Salvador, BA. ticig@yahoo.com.br
Pinto
Vanessa Alves Fernandes
VA
Ivo
Fábio André Barbosa
FA
Nascimento
Jedson dos Santos
Jdos S
D000773:Anesthesia, Obstetrical; D002585:Cesarean Section; D005260:Female; D006801:Humans; D010013:Osteogenesis Imperfecta; D011247:Pregnancy; D011248:Pregnancy Complications; D055815:Young Adult