[A case report of retroperitoneal fibrosis associated with IgG4-related sclerosing disease].
A 67-year-old man had undergone a right ureteronephrectomy because of a right ureter tumor, but the pathological diagnosis was inflammatory tissue with plasma cells, lymphocytes, and fibrosis. About 3 years later, abdominal computed tomography (CT) revealed a solid tumor at the left renal hilus. We resected the tumor and the pathological diagnosis was the same as before. More than 2 years later, because of elevated pancreatic enzymes, immunoglobulin G (IgG) and IgG4, more detailed examinations ware done, and he was diagnosed with IgG4-related autoimmune pancreatitis. We believe that the retroperitoneal tumor was retroperitoneal fibrosis associated with IgG4-related sclerosing disease. Now, he is being treated with steroid therapy. IgG4-related sclerosing disease is a systemic disease whose concept is now being established. Much more work is needed to understand this disease.
Minato
Noriko
N
The Department of Urology, Osaka University Graduate School of Medicine, Osaka, Japan.
Takayama
Hitoshi
H
Mukai
Masatoshi
M
Miyagawa
Yasushi
Y
Tsujihata
Masao
M
Nonomura
Norio
N
Okuyama
Akihiko
A
D000368:Aged; D001327:Autoimmune Diseases / Q000150:complications; D003937:Diagnosis, Differential; D006801:Humans; D007074:Immunoglobulin G / Q000032:analysis*; D008297:Male; D010195:Pancreatitis / Q000150:complications; D011859:Radiography; D012185:Retroperitoneal Fibrosis / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging; D012186:Retroperitoneal Neoplasms / Q000175:diagnosis; D012598:Sclerosis / Q000150:complications*
D007074:Immunoglobulin G