title: Branch retinal artery occlusion with visual field and multifocal erg in Susac syndrome: a case report.
abstract: A 19-year-old woman presented with subacute encephalopathy and subsequently developed hearing loss and occlusions of branches of the central retinal artery. The triad of microangiopathy of the brain, retina and cochlea is typical for Susac syndrome. The etiology of this syndrome is still unknown, but the prognosis is good in most cases. Spontaneous resolution usually occurs, but early treatment minimizes the risk of sequelae. Multifocal ERG may be useful to assess subclinical retinal dysfunction after recovery of subjective symptoms of BRAO in Susac syndrome.
authors.affiliation: Departement Oogheelkunde, UZ Brussel, Vrije Universiteit Brussel, VUB, Laarbeeklaan 101, 1090, Jette, Belgium. mariannevanwinden@telenet.be
authors.forename: Marianne
authors.initials: M
authors.lastname: van Winden
authors.forename: Paul
authors.initials: P
authors.lastname: Salu
mesh_terms: D001158:Arteries; D001379:Azathioprine / Q000008:administration & dosage; D001921:Brain / Q000098:blood supply; D003051:Cochlea / Q000098:blood supply; D003520:Cyclophosphamide / Q000008:administration & dosage; D004334:Drug Administration Schedule; D004359:Drug Therapy, Combination; D004596:Electroretinography / Q000379:methods*; D005260:Female; D005451:Fluorescein Angiography; D005938:Glucocorticoids / Q000008:administration & dosage; D006801:Humans; D007275:Injections, Intravenous; D008775:Methylprednisolone / Q000008:administration & dosage; D055806:Microvessels; D011239:Prednisolone / Q000008:administration & dosage; D015356:Retinal Artery Occlusion / Q000175:diagnosis* / Q000209:etiology / Q000503:physiopathology*; D012171:Retinal Vessels; D055955:Susac Syndrome / Q000150:complications* / Q000188:drug therapy; D014652:Vascular Diseases / Q000209:etiology; D014794:Visual Fields; D055815:Young Adult
chemical_list: D005938:Glucocorticoids; D003520:Cyclophosphamide; D011239:Prednisolone; D001379:Azathioprine; D008775:Methylprednisolone