title: Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy.
abstract: We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide and sunitinib with a very good response after 12 months of follow-up.
authors.affiliation: Serviço de Medicina Interna 3, Hospital Santo António dos Capuchos.
authors.forename: Angela
authors.initials: A
authors.lastname: Simas
authors.forename: Catarina
authors.initials: C
authors.lastname: Matos
authors.forename: Rodrigo
authors.initials: R
authors.lastname: Lopes da Silva
authors.forename: Vítor
authors.initials: V
authors.lastname: Brotas
authors.forename: Eugénio
authors.initials: E
authors.lastname: Teófilo
authors.forename: José Pereira
authors.initials: JP
authors.lastname: Albino