title: Maternal parenting stress in families with a child with Angelman syndrome or Prader-Willi syndrome.
abstract: BACKGROUND
  Parenting stress was investigated in mothers with a child with Angelman syndrome (AS) or Prader-Willi syndrome (PWS), which are genetically related.
  
  
  METHODS
  Mothers of 24 children with AS and 23 children with PWS (2-12 years) completed the Nijmegen Parenting Stress Index-Short, Developmental Behaviour Checklist, and Vineland Screener 0-12.
  
  
  RESULTS
  Parenting stress was high for 58% of AS and 26% of PWS cases. For both syndromes, no relationship existed with the child's gender, age, or behavioural problems. In PWS there was no effect on level of functioning. Overall, more mothers with a child with AS perceived high parenting stress. When children showed low levels of behavioural problems this difference was contained. However, when children exhibited severe behavioural problems, parenting stress was the same for both syndromes.
  
  
  CONCLUSIONS
  In AS professional family support is essential, since parenting is stressful for many mothers. In PWS, this is especially the case when behavioural problems are present.
authors.affiliation: Department of Clinical Child and Adolescent Studies, Leiden University, the Netherlands. josettewulffaert@hotmail.com
authors.forename: Josette
authors.initials: J
authors.lastname: Wulffaert
authors.forename: Evert M
authors.initials: EM
authors.lastname: Scholte
authors.forename: Ina A
authors.initials: IA
authors.lastname: Van Berckelaer-Onnes
mesh_terms: D000223:Adaptation, Psychological; D017204:Angelman Syndrome / Q000175:diagnosis / Q000235:genetics / Q000523:psychology*; D002648:Child; D002653:Child Behavior Disorders / Q000175:diagnosis / Q000523:psychology; D002675:Child, Preschool; D005190:Family; D005260:Female; D005838:Genotype; D006801:Humans; D008297:Male; D009035:Mothers / Q000523:psychology*; D009426:Netherlands; D016487:Parenting / Q000523:psychology*; D010865:Pilot Projects; D011218:Prader-Willi Syndrome / Q000175:diagnosis / Q000235:genetics / Q000523:psychology*; D011569:Psychiatric Status Rating Scales; D012944:Social Support; D013315:Stress, Psychological / Q000523:psychology; D011795:Surveys and Questionnaires