title: Malignant atrophic papulosis with severe gastrointestinal perforation and omental necrosis: a case report.
abstract: Malignant atrophic papulosis (MAP) is a rare disease with an extremely grim prognosis, death being due to gastrointestinal perforation and neurological disorders. We report a severe case of MAP in a 37-year old woman. The patient had three emergent laparotomies in 3 months for recurrent acute peritonitis due to omental thrombosis resulting in necrosis, multiple intestinal and mesenteric lesions, and severe gastrointestinal perforations. Multiple papular skin lesions were present for 1 year prior to surgery. Pathological findings revealed MAP. Surgical intervention was successful and the patient recovered smoothly but later died of malnutrition and septicaemia.
authors.affiliation: Department of General Surgery, Affiliated Sir Run Run Shaw Hospital, School of Medicine, Zhejiang University, Hangzhou, China.
authors.forename: X Y
authors.initials: XY
authors.lastname: Zheng
authors.forename: D Y
authors.initials: DY
authors.lastname: Huang
authors.forename: Y
authors.initials: Y
authors.lastname: Xin
authors.forename: X F
authors.initials: XF
authors.lastname: Wang
mesh_terms: D000208:Acute Disease; D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007416:Intestinal Perforation / Q000209:etiology / Q000473:pathology* / Q000601:surgery; D054853:Malignant Atrophic Papulosis / Q000150:complications / Q000473:pathology* / Q000601:surgery; D009336:Necrosis; D009852:Omentum / Q000473:pathology*; D010538:Peritonitis / Q000209:etiology / Q000473:pathology* / Q000601:surgery