title: Chiari 1 malformation and holocord syringomyelia presenting as abrupt onset foot drop.
abstract: We present two patients with a Chiari 1 malformation and holocord syringomyelia who presented with abrupt onset unilateral foot drop. Neurophysiologic testing was consistent with a proximal nerve root lesion. This assisted with localization and directed magnetic resonance (MR) imaging to lumbosacral spine and nerve roots. Each child underwent a suboccipital craniectomy and laminectomy with duroplasty to decompress the foramen magnum. Each child also showed rapid and complete clinical recovery despite the significant electromyographic and MRI abnormalities on initial study.
authors.affiliation: Division of Neurology, Children's Hospital of Eastern Ontario, University of Ottawa, 401 Smyth Road, Ottawa, Ontario, Canada. hmcmillan@cheo.on.ca
authors.forename: Hugh J
authors.initials: HJ
authors.lastname: McMillan
authors.forename: Erick
authors.initials: E
authors.lastname: Sell
authors.forename: Munyao
authors.initials: M
authors.lastname: Nzau
authors.forename: Enrique C G
authors.initials: EC
authors.lastname: Ventureyra
mesh_terms: D001139:Arnold-Chiari Malformation / Q000150:complications* / Q000503:physiopathology / Q000601:surgery; D002675:Child, Preschool; D019299:Decompression, Surgical; D005260:Female; D020233:Gait Disorders, Neurologic / Q000209:etiology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D019635:Neurosurgical Procedures; D013595:Syringomyelia / Q000209:etiology* / Q000473:pathology / Q000503:physiopathology
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