title: Leukocyte adhesion deficiency type 1 presenting with recurrent pyoderma gangrenosum and flaccid scarring.
abstract: We report an 11-year-old boy with a longstanding history of recurrent pyoderma gangrenosum and abnormal wound healing who eventually developed a fatal invasive fungal infection. This article emphasizes the importance to consider leukocyte adhesion deficiency type 1 in the differential diagnosis of patients with recurrent skin ulcers.
authors.affiliation: Division of Rheumatology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229-3039, USA. claas.hinze@gmail.com
authors.forename: Claas H
authors.initials: CH
authors.lastname: Hinze
authors.forename: Anne W
authors.initials: AW
authors.lastname: Lucky
authors.forename: Kevin E
authors.initials: KE
authors.lastname: Bove
authors.forename: Rebecca A
authors.initials: RA
authors.lastname: Marsh
authors.forename: Jack H
authors.initials: JH
authors.lastname: Bleesing
authors.forename: Murray H
authors.initials: MH
authors.lastname: Passo
mesh_terms: D001706:Biopsy; D002648:Child; D002921:Cicatrix / Q000209:etiology / Q000276:immunology / Q000473:pathology*; D017809:Fatal Outcome; D006801:Humans; D018370:Leukocyte-Adhesion Deficiency Syndrome / Q000150:complications / Q000276:immunology / Q000473:pathology; D008297:Male; D017511:Pyoderma Gangrenosum / Q000150:complications* / Q000276:immunology / Q000473:pathology*; D012008:Recurrence; D012867:Skin / Q000276:immunology / Q000473:pathology