Malignant atrophic papulosis with severe gastrointestinal perforation and omental necrosis: a case report.
Malignant atrophic papulosis (MAP) is a rare disease with an extremely grim prognosis, death being due to gastrointestinal perforation and neurological disorders. We report a severe case of MAP in a 37-year old woman. The patient had three emergent laparotomies in 3 months for recurrent acute peritonitis due to omental thrombosis resulting in necrosis, multiple intestinal and mesenteric lesions, and severe gastrointestinal perforations. Multiple papular skin lesions were present for 1 year prior to surgery. Pathological findings revealed MAP. Surgical intervention was successful and the patient recovered smoothly but later died of malnutrition and septicaemia.
Zheng
X Y
XY
Department of General Surgery, Affiliated Sir Run Run Shaw Hospital, School of Medicine, Zhejiang University, Hangzhou, China.
Huang
D Y
DY
Xin
Y
Y
Wang
X F
XF
D000208:Acute Disease; D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007416:Intestinal Perforation / Q000209:etiology / Q000473:pathology* / Q000601:surgery; D054853:Malignant Atrophic Papulosis / Q000150:complications / Q000473:pathology* / Q000601:surgery; D009336:Necrosis; D009852:Omentum / Q000473:pathology*; D010538:Peritonitis / Q000209:etiology / Q000473:pathology* / Q000601:surgery