title: Isolated cranio-spinal involvement of Rosai-Dorfman disease: case report.
abstract: Rosai-Dorfman disease is a rare non-neoplastic lymphoproliferative condition. It commonly affects individuals between third and fifth decades, most common presentation being in the form of massive painless cervical lymphadenopathy with fever, weight loss and malaise. Isolated intracranial involvement is rare seen in less than 5% of patients with extranodal involvement. We present a patient with isolated contiguous cranio-spinal involvement who presented to us with remitting symptoms.
authors.affiliation: Department of Neurosurgery, National Institute of Mental Health and Neurosciences, Bangalore, India.
authors.forename: Sudheer
authors.initials: S
authors.lastname: Ambekar
authors.forename: Sampath
authors.initials: S
authors.lastname: Somanna
authors.forename: Dhananjaya Ishwar
authors.initials: DI
authors.lastname: Bhat
authors.forename: Manish
authors.initials: M
authors.lastname: Ranjan
mesh_terms: D000328:Adult; D056424:Decompressive Craniectomy; D005260:Female; D005539:Foramen Magnum; D015618:Histiocytosis, Sinus / Q000150:complications / Q000473:pathology*; D006801:Humans; D011782:Quadriplegia / Q000209:etiology / Q000473:pathology*; D016896:Treatment Outcome; D014786:Vision Disorders / Q000209:etiology / Q000473:pathology*