title: Long-term evaluation of Cochlear implantation in Cogan syndrome.
abstract: OBJECTIVE
  The evaluation of long-term results of cochlear implantation in patients with typical Cogan syndrome.
  
  
  METHODS
  The medical records of approximately 3,000 patients who underwent cochlear implantation in a tertiary centre within the period 1992-2007 were retrospectively examined.
  
  
  RESULTS
  Four cochlear implant recipients with Cogan syndrome (6 implantations) were identified. One cochlea was found to be partially obliterated; the electrode could, however, be completely inserted. Wound healing disorders and infections in a patient with systemic symptoms were the only postoperative complications. Hearing outcome was favorable, with average HSM and monosyllabic scores of 96.7 and 82.5%, respectively, in an average follow-up time of 9.25 years.
  
  
  CONCLUSIONS
  Cochlear implantation is the appropriate hearing rehabilitation method in Cogan syndrome patients. Although the basic illness does not affect the long-term hearing outcome, skin-atrophy-related complications in cases with systemic symptoms may occur. Finally, the cochlear implant surgeon should be aware of the possible cochlea obliteration.
authors.affiliation: Otorhinolaryngology Department, Hannover Medical University, Hannover, Germany. Kontorinis.Georgios @ mh-hannover.de
authors.forename: Georgios
authors.initials: G
authors.lastname: Kontorinis
authors.forename: Alexandros
authors.initials: A
authors.lastname: Giourgas
authors.forename: Juergen
authors.initials: J
authors.lastname: Neuburger
authors.forename: Anke
authors.initials: A
authors.lastname: Lesinski-Schiedat
authors.forename: Thomas
authors.initials: T
authors.lastname: Lenarz
mesh_terms: D000328:Adult; D002648:Child; D019929:Cochlear Implantation / Q000534:rehabilitation*; D055952:Cogan Syndrome / Q000534:rehabilitation* / Q000601:surgery*; D003638:Deafness / Q000534:rehabilitation / Q000601:surgery; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D012189:Retrospective Studies; D013997:Time Factors; D016896:Treatment Outcome; D055815:Young Adult