Kaposiform hemangioendothelioma of the choledochus.
Kaposiform hemangioendothelioma (KHE) is a rare, locally aggressive vascular neoplasm that mainly occurs during childhood. Although KHE may involve various organs, involvement of the choledochus has not been reported. We report a case of KHE in a 5-month-old male infant. The patient was admitted with icterus and acholic stool. Contrast computed tomography revealed a vascular tumor in the hepatic portal region causing biliary obstruction. Excision of the extrahepatic duct and hepatoportoenterostomy were performed successfully, and he has been well during 3 years of postoperative follow-up.
Terui
Keita
K
Department of Pediatric Surgery, Graduate School of Medicine, Chiba University, Chiba 260-8677, Japan. kta@cc.rim.or.jp
Nakatani
Yukio
Y
Kambe
Michiyo
M
Fukunaga
Masaharu
M
Hishiki
Tomoro
T
Saito
Takeshi
T
Sato
Yoshiharu
Y
Takenouchi
Ayako
A
Saito
Eriko
E
Ono
Sachie
S
Yoshida
Hideo
H
D002779:Cholestasis / Q000209:etiology / Q000601:surgery*; D003138:Common Bile Duct Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D006390:Hemangioendothelioma / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D007223:Infant; D041781:Jaundice, Obstructive / Q000209:etiology / Q000601:surgery*; D008297:Male; D011859:Radiography