title: Deep anterior lamellar keratoplasty for Maroteaux-Lamy syndrome.
abstract: OBJECTIVE
  To present a case of Maroteaux-Lamy syndrome (MLS), which underwent deep anterior lamellar keratoplasty (DALK) for visual rehabilitation.
  
  
  METHODS
  A 15-year-old girl with MLS was admitted with severe corneal opacity. We performed DALK on her left eye for visual rehabilitation. Big-bubble technique was used to perform lamellar separation.
  
  
  RESULTS
  Corneal graft was clear 24 months after surgery. Best spectacle-corrected visual acuity of left eye was 20/25 with the correction of +0.75/-0.50 diopters × 170. At the last follow-up, in vivo confocal microscopy revealed mild haze in the posterior stroma at the graft interface level. Endothelial cell count was 2473.4 cells per square millimeter using a noncontact specular microscope.
  
  
  CONCLUSIONS
  Given systemic problems in patients with MLS and less postoperative complications of DALK in comparison with penetrating keratoplasty, it seems DALK is the better choice for these patients.
authors.affiliation: Labbafinejad Medical Center, Shahid Beheshti University (MC), Tehran, Iran.
authors.forename: Mohsen
authors.initials: M
authors.lastname: Rahmati-Kamel
authors.forename: Mohammadali
authors.initials: M
authors.lastname: Javadi
authors.forename: Ahmad
authors.initials: A
authors.lastname: Shojaei
authors.forename: Medi
authors.initials: M
authors.lastname: Eslani
authors.forename: Farid
authors.initials: F
authors.lastname: Karimian
mesh_terms: D000293:Adolescent; D002452:Cell Count; D003316:Corneal Diseases / Q000473:pathology / Q000601:surgery*; D016039:Corneal Transplantation; D004728:Endothelium, Corneal / Q000473:pathology; D005260:Female; D006801:Humans; D009087:Mucopolysaccharidosis VI / Q000473:pathology / Q000601:surgery*; D014786:Vision Disorders / Q000534:rehabilitation*; D014792:Visual Acuity / Q000502:physiology