title: A long-term survival case of tracheal agenesis: management for tracheoesophageal fistula and esophageal reconstruction.
abstract: Tracheal agenesis is a very rare disorder which leads to severe respiratory disorders immediately after birth. Reports are very limited on long-term survival cases. We report here a long-term survival case with Floyd's type I tracheal agenesis. During the neonatal stage, the patient underwent abdominal esophageal banding to substitute esophagus for trachea and transection at the cervical esophagus with esophagostomy. Subsequently, airway management was difficult due to a fragile tracheoesophageal fistula, but the fistula was conservatively treated and stabilized with the patient's growth. This patient is a very rare case in whom oral feeding was achieved after esophageal reconstruction using a gastric tube. For this case, we describe mainly (1) the management method of the tracheoesophageal fistula and (2) esophageal reconstruction without thoracotomy.
authors.affiliation: Department of Pediatric Surgery, School of Medicine, Keio University, Shinjuku-ku, Tokyo, 160-8582, Japan. yfuchimo@sc.itc.keio.ac.jp
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Fuchimoto
authors.forename: Masaharu
authors.initials: M
authors.lastname: Mori
authors.forename: Fumika
authors.initials: F
authors.lastname: Takasato
authors.forename: Hirofumi
authors.initials: H
authors.lastname: Tomita
authors.forename: Yuki
authors.initials: Y
authors.lastname: Yamamoto
authors.forename: Naoki
authors.initials: N
authors.lastname: Shimojima
authors.forename: Ken
authors.initials: K
authors.lastname: Hoshino
authors.forename: Goro
authors.initials: G
authors.lastname: Koinuma
authors.forename: Yasuhide
authors.initials: Y
authors.lastname: Morikawa
mesh_terms: D058109:Airway Management / Q000379:methods*; D003251:Constriction, Pathologic / Q000150:complications / Q000601:surgery; D004947:Esophagus / Q000601:surgery*; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011175:Positive-Pressure Respiration / Q000379:methods; D017741:Survivors; D014132:Trachea / Q000002:abnormalities / Q000601:surgery; D014138:Tracheoesophageal Fistula / Q000150:complications / Q000628:therapy*; D016896:Treatment Outcome