Stiff heart syndrome.
Isolated cardiac amyloidosis, or "Stiff Heart Syndrome," is a rare manifestation of amyloidosis. Some degree of cardiac amyloid deposition is common in elderly patients, as reported in prior post-mortem studies; however, isolated cardiac involvement with predominantly cardiac symptoms and no evidence of systemic disease is a rare presentation. Establishing the correct diagnosis, even with the use of extensive testing including amyloid typing, understanding the clinical significance, and management can be challenging in such cases.
Bhupathi
Satya S
SS
Department of Internal Medicine, Marshfield Clinic, WI 54449, USA.
Chalasani
Sreelatha
S
Rokey
Roxann
R
D000368:Aged; D000682:Amyloid / Q000378:metabolism; D000686:Amyloidosis / Q000175:diagnosis* / Q000378:metabolism / Q000473:pathology / Q000628:therapy*; D006331:Heart Diseases / Q000175:diagnosis* / Q000378:metabolism / Q000473:pathology / Q000628:therapy*; D006801:Humans; D008297:Male; D013577:Syndrome
D000682:Amyloid