title: Absent pulmonary valve, imperforate tricuspid valve, and dysplastic right ventricle.
abstract: We report a very rare case involving an absent pulmonary valve, an imperforate tricuspid valve, a ventricular septal defect (VSD), and a dysplastic right ventricle in a patient who underwent a Fontan operation successfully. Upon performing a bidirectional cavopulmonary anastomosis, we closed the VSD and coronary artery-to-right ventricle fistulae, and plicated the right ventricular free wall in order to obliterate the right ventricular cavity.
authors.affiliation: Department of Cardiovascular Surgery, Chiba Children Hospital, 579-1 Heta, Midori, Chiba 266-0007, Japan. finitoyuki@msn.com
authors.forename: Yuki
authors.initials: Y
authors.lastname: Nakamura
authors.forename: Mitsuru
authors.initials: M
authors.lastname: Aoki
authors.forename: Noboru
authors.initials: N
authors.lastname: Yamamoto
authors.forename: Tadashi
authors.initials: T
authors.lastname: Fujiwara
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D003330:Coronary Vessel Anomalies / Q000150:complications / Q000601:surgery; D018729:Fontan Procedure; D006345:Heart Septal Defects, Ventricular / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D010166:Palliative Care; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery; D016896:Treatment Outcome; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000601:surgery; D016157:Vascular Fistula / Q000151:congenital / Q000601:surgery