title: Absent pulmonary valve syndrome with ascending aortic aneurysm.
abstract: Absent pulmonary valve syndrome is rare. We report the case of a child with absent pulmonary valve syndrome noted after birth. Progressive dilatation of the main pulmonary artery and ascending aorta were noted by echocardiography and confirmed by heart computed tomography. He underwent ascending aorta graft replacement and pulmonary artery reduction angioplasty at the age of 6. Good outcome was achieved at 18-month follow-up where subsequent computed tomography revealed a normal size ascending aorta and main pulmonary artery.
authors.affiliation: Department of Pediatrics, Chang Gung Memorial Hospital, Kaohsiung Medical Center, Chang Gung University College of Medicine, 123 Ta Pei Road, Niao Sung Hsiang, Kaohsiung 833, Taiwan. cdliang@adm.cgmh.org.tw
authors.forename: Chi-Di
authors.initials: CD
authors.lastname: Liang
authors.forename: Sheung-Fat
authors.initials: SF
authors.lastname: Ko
authors.forename: Jen-Ping
authors.initials: JP
authors.lastname: Chang
authors.forename: Shun-Chen
authors.initials: SC
authors.lastname: Huang
mesh_terms: D017130:Angioplasty; D001014:Aortic Aneurysm / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation; D004108:Dilatation, Pathologic; D006330:Heart Defects, Congenital / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000000981:diagnostic imaging / Q000601:surgery; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014463:Ultrasonography