[Desmoplastic fibroma of the skull in an infant].
Desmoplastic fibromas are uncommon osseous tumors that seldom involve the skull. These tumors are histologically benign but locally aggressive with a propensity for recurrence if resection is partial. To our knowledge, only 16 cases have been reported in the literature, seven of which concerned children. We report a further case of a desmoplastic fibroma of the skull in a 3-year-old boy who presented with a right parietal mass. The CT scan showed a lytic mass with brain compression and cortical destruction. The patient underwent a craniectomy and complete mass resection. Histological diagnosis was desmoplastic fibroma. Postoperative progress was normal without recurrence 6 months later.
Bahri
I
I
Laboratoire d'anatomie et de cytologie pathologiques, CHU Habib Bourguiba, route El Aïn Km 0.5, 3029 Sfax, Tunisia.
Kallel
R
R
Gouiaa
N
N
Boudawara
Z
Z
Boudawara
T S
TS
D001853:Bone Marrow / Q000473:pathology; D002540:Cerebral Cortex / Q000473:pathology; D002675:Child, Preschool; D003399:Craniotomy; D018220:Fibroma, Desmoplastic / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008297:Male; D019635:Neurosurgical Procedures; D010296:Parietal Lobe / Q000473:pathology; D012886:Skull / Q000473:pathology; D012888:Skull Neoplasms / Q000473:pathology / Q000601:surgery*; D014057:Tomography, X-Ray Computed