title: Chronic thromboembolic pulmonary hypertension in Behçet's disease: effectiveness of endarterectomy.
abstract: Behçet's disease is a systemic vasculitis characterised by recurrent mouth and genital ulcers and uveitis. About 25% of patients suffer from vascular involvement. We describe a patient with Behçet's disease who suffered recurrent pulmonary embolism and developed severe chronic thromboembolic pulmonary hypertension. The patient was successfully treated with pulmonary endarterectomy that normalised pulmonary haemodynamics. Chronic thromboembolic pulmonary hypertension is a potential complication of Behçet's disease that may be amenable to pulmonary endarterectomy.
authors.affiliation: Department of Autoimmune Diseases, Hospital Clínic-Institut d'Investigacions Biomèdiques Pi i Sunyer, Universitat de Barcelona, Spain. gespino@clinic.ub.es
authors.forename: Gerard
authors.initials: G
authors.lastname: Espinosa
authors.forename: Isabel
authors.initials: I
authors.lastname: Blanco
authors.forename: Juan Miguel
authors.initials: JM
authors.lastname: Antón
authors.forename: Marcelo
authors.initials: M
authors.lastname: Sánchez
authors.forename: Paolo
authors.initials: P
authors.lastname: Macchiarini
authors.forename: Joan Albert
authors.initials: JA
authors.lastname: Barberà
mesh_terms: D000328:Adult; D001528:Behcet Syndrome / Q000150:complications*; D004691:Endarterectomy; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000601:surgery*; D008297:Male; D011655:Pulmonary Embolism / Q000209:etiology* / Q000601:surgery*; D012008:Recurrence; D016896:Treatment Outcome