Infantile fibromatosis: a case report and review of the literature.
Desmoid tumours are benign fibrous neoplasms originating from musculoaponeurotic structures throughout the body. These tumours are rare in the mandible and the literature is limited to case reports and retrospective reviews and to date there is no agreed protocol for the management of these lesions in the paediatric mandible. The definition, diagnosis and management of juvenile fibromatosis still presents a challenge to the modern surgeon, radiologist and pathologist. We describe a case of paediatric mandibular infantile fibromatosis which presented a diagnostic dilemma, and review the currently available literature.
Ruparelia
Meera Satish
MS
John Radcliffe Hospital, Headley Way, Headington, Oxford, OX3 9DU, UK. meerarup@btinternet.com
Dhariwal
Daljit K
DK
D000199:Actins / Q000032:analysis; D001706:Biopsy; D002675:Child, Preschool; D003937:Diagnosis, Differential; D018222:Desmoid Tumors / Q000175:diagnosis*; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008339:Mandibular Neoplasms / Q000175:diagnosis*; D011862:Radiography, Panoramic; D051176:beta Catenin / Q000032:analysis
D000199:Actins; D051176:beta Catenin