Pulmonary atresia and ventricular septal defect with collaterals to right lung associated with anomalous left pulmonary artery from the ascending aorta.
We present a 10-month-old boy with cyanosis. This is a rare case of pulmonary atresia, ventricular septal defect (VSD), major aorto-pulmonary collateral arteries (MAPCAs) to the right lung with absent native right pulmonary artery (RPA) in association with anomalous left pulmonary artery (LPA) from the ascending aorta (AAo). Echocardiography was unable to identify all of the cardiovascular abnormalities. Multidetector CT demonstrated all of these abnormalities and is the investigation of choice instead of cardiac catheterization.
Khositseth
Anant
A
Department of Pediatrics, Faculty of Medicine, Ramathibodi Hospital, Mahidol University, Bangkok, 10400, Thailand. alaks@diamond.mahidol.ac.th
Siripornpitak
Suvipaporn
S
Pornkul
Ratanaporn
R
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D001011:Aorta / Q000002:abnormalities*; D001027:Aortography; D001159:Arterio-Arterial Fistula / Q000000981:diagnostic imaging*; D002648:Child; D003097:Collateral Circulation; D003490:Cyanosis / Q000175:diagnosis / Q000209:etiology; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D011651:Pulmonary Artery / Q000000981:diagnostic imaging*; D018633:Pulmonary Atresia / Q000000981:diagnostic imaging*