Erythropoietic protoporphyria (Report of three cases).
Three Libyan patients developing clinical manifestations of erythropoietic protoporphyria (EPP) at 5 years, 7 years and 3 years of age are reported. All of them had variable degree of photosensitivity leading to pitted scarring. Red blood cells in peripheral blood smear revealed positive pink fluorescence in all. First patient responded well with chloroquine therapy and the 3rd patient showed improvement with oral beta-carotene therapy, but the second patient did not show significant response to either.
Department of Dermatology, Central Hosptlal and Faculty of Medicine, Al-Fateh University of Medical Science, Tripoli, Libya.
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Shafi
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Khatri