Sudden infant death syndrome and left ventricular hypertrabeculation-hidden arrhythmogenic entity?
Left ventricular noncompaction/hypertrabeculation is a condition which is characterized by a highly trabeculated, "spongy" myocardium.It can present at any age with heart failure, arrhythmia and/or thromboembolic events.A wide variety of mutations have been found to be a cause of hypertrabeculation and it is possible that there is a continuum of hypertrophic cardiomyopathy, dilated cardiomyopathy and hypertrabeculation/noncompaction.We present a case of left ventricular hypertrabeculation which presented as sudden infant death syndrome and we propose that this entity may be a hidden cause of arrhythmic death in some infants presenting as sudden infant death syndrome.
Ker
J
J
Department of Physiology, University of Pretoria, Pretoria, South Africa.
Toit-Prinsloo
L Du
LD
van Heerden
W F P
WF
Saayman
G
G