Massive craniofacial intraosseous vascular malformation resembling cystic angiomatosis: report of 2 cases and review of the literature.
Cystic angiomatosis of bone is a rare condition of multifocal angiomas of the skeleton. The condition is believed to be congenital, grows slowly and starts in first decades of life. Two cases of progressive bimaxillary enlargement, presented here with a history of slowly enlargement of facial bones when they were 9 and 6 year old, respectively. Radiographic evaluation of the craniofacial bones revealed aggressive hypertrophy with severe displacement of the teeth. The histopathological evaluation of the gross specimen showed vital bone containing capillary and cavernous spaces with endothelial lining. Aggressive cystic angiomatosis of the facial bones was described here as the most probable diagnosis.
Department of Oral and Maxillofacial Surgery, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Seyed
S
Hossein Mortazavi
Abbas
A
Khodayari
Arash
A
Khojasteh
Fatemeh Mashhadi
FM
Abbas
Leili
L
Mehrdad
Mohammad Taghi
MT
Kiani
Allan G
AG
Farman
D000293:Adolescent; D000539:Alveolar Process / Q000098:blood supply / Q000473:pathology; D000798:Angiomatosis / Q000175:diagnosis*; D001847:Bone Diseases / Q000175:diagnosis*; D001853:Bone Marrow / Q000473:pathology; D002196:Capillaries / Q000002:abnormalities; D002636:Cherubism / Q000175:diagnosis; D003937:Diagnosis, Differential; D042783:Endothelial Cells / Q000473:pathology; D005147:Facial Bones / Q000473:pathology*; D005260:Female; D005624:Frontal Bone / Q000473:pathology; D006801:Humans; D006984:Hypertrophy; D008297:Male; D008336:Mandibular Diseases / Q000175:diagnosis; D008439:Maxillary Diseases / Q000175:diagnosis; D009777:Occipital Bone / Q000473:pathology; D054079:Vascular Malformations / Q000175:diagnosis; D015050:Zygoma / Q000473:pathology