title: Primary Sjögren's Syndrome with two extraglandular sites involvement - case report.
abstract: Primary Sjögren's Syndrome (pSS) is a chronic, slowly progressive inflammatory autoimmune disorder, characterised by lymphocytic infiltration of the exocrine glands, leading to decrease of glandular secretion. In 40-60% of pSS patients, extraglandular disease develops. We present the case of a patient with two extraglandular sites involvement in the course of pSS manifesting with progressive respiratory and gastrointestinal symptoms.
authors.affiliation: Department of Chest Medicine, National Tuberculosis and Lund Diseases Research Institute, Warsaw, Poland. monika.szturmowicz@gmail.com
authors.forename: Monika
authors.initials: M
authors.lastname: Szturmowicz
authors.forename: Ewelina
authors.initials: E
authors.lastname: Wilińska
authors.forename: Anna
authors.initials: A
authors.lastname: Paczek
authors.forename: Liliana
authors.initials: L
authors.lastname: Wawrzyńska
authors.forename: Lucyna
authors.initials: L
authors.lastname: Opoka
authors.forename: Juliusz
authors.initials: J
authors.lastname: Gątarek
authors.forename: Renata
authors.initials: R
authors.lastname: Langfort
authors.forename: Ewa
authors.initials: E
authors.lastname: Rowińska-Zakrzewska
authors.forename: Adam
authors.initials: A
authors.lastname: Torbicki
mesh_terms: D015746:Abdominal Pain / Q000188:drug therapy / Q000209:etiology*; D000368:Aged; D005260:Female; D005938:Glucocorticoids / Q000008:administration & dosage; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000209:etiology*; D011241:Prednisone / Q000008:administration & dosage; D011859:Radiography; D012859:Sjogren's Syndrome / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy* / Q000473:pathology; D016896:Treatment Outcome
chemical_list: D005938:Glucocorticoids; D011241:Prednisone