[Systemic disease with hepatic and pulmonary involvement].
We discuss the history of a 39 year old woman with multiple patchy consolidations on high - resolution computed tomography in combination with a delayed diagnosis of primary biliary cirrhosis. Further we review the differential diagnostic considerations and step by step diagnostic and therapeutic options. Based on the presentation with symptoms of a mitigated pneumonia at the beginning of the disease, the differential diagnosis of cryptogenic organising pneumonia (CO) is discussed. The diagnosis of COP is often delayed. The theoretic background of primary biliary cirrhosis and the association with pulmonary disease are broadly discussed.
Departement Medizin, Kantonsspital Winterthur, Winterthur.
Ursula
U
Huber
Corina
C
Dommann-Scherrer
Peter E
PE
Ballmer
Thomas
T
Hess
Markus
M
Hofer
D000328:Adult; D001706:Biopsy; D003131:Combined Modality Therapy; D015897:Comorbidity; D018549:Cryptogenic Organizing Pneumonia / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology / Q000628:therapy; D057210:Delayed Diagnosis; D005260:Female; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D008099:Liver / Q000000981:diagnostic imaging / Q000473:pathology; D008105:Liver Cirrhosis, Biliary / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology / Q000628:therapy; D016031:Liver Transplantation; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D016726:Plasma Cell Granuloma, Pulmonary / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D011020:Pneumonia, Pneumocystis / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D020775:Thoracic Surgery, Video-Assisted; D014057:Tomography, X-Ray Computed
D007166:Immunosuppressive Agents