Lowe's syndrome with Fanconi syndrome for ocular surgery: perioperative anesthetic considerations.
Lowe's syndrome is a rare inherited metabolic disorder characterized by mental retardation, kidney malfunction, and abnormalities of the eyes and bones. A 4 month-old child with Lowe's and Fanconi's syndrome, undergoing bilateral congenital cataract surgery, is presented. Preoperative electrolyte imbalance was corrected by potassium, calcium, magnesium, phosphate, and bicarbonate supplementation. Anesthesia was administered uneventfully using appropriate anesthetic agents and monitoring. Adequate preoperative evaluation and optimization, along with selection of anesthetic agents and fluid and electrolyte management with appropriate perioperative monitoring, is key to a successful outcome.
Department of Anaesthesiology and Intensive Care, All India Institute ofMedical Sciences, Ansari Nagar, NewDelhi 110029, India. trips22003@yahoo.co.in
Ravindra
R
Pandey
Rakesh
R
Garg
Chandrashish
C
Chakravarty
Vanlal
V
Darlong
Jyotsna
J
Punj
Chandralekha
D000758:Anesthesia / Q000379:methods*; D002387:Cataract Extraction; D005198:Fanconi Syndrome / Q000378:metabolism*; D006801:Humans; D007223:Infant; D008297:Male; D009800:Oculocerebrorenal Syndrome / Q000150:complications / Q000601:surgery*; D019990:Perioperative Care