[Persistent Müllerian ducts syndrome].
Persistent Müllerian ducts syndrome is a rare form of internal male pseudohermaphroditism, characterized by the presence of the uterus, fallopian tubes and upper vagina in an otherwise normally virilised male with a 46 XY karyotype. It is the result of a deficiency in anti-Müllerian hormone or abnormality of this hormone receptor. Often, the diagnosis is made incidentally during surgical exploration for cryptorchidism or herniorrhaphy, and exceptionally during cancer of ectopic testis. We discuss a rare case of this syndrome revealed by a bilateral intra-abdominal gonadal tumor.
Service d'urologie A, hôpital Ibn Sina, CHU de Rabat, Rabat, Maroc. alibarki@hotmail.com
A
A
Barki
F
F
Khalil
R
R
Tahri
M
M
Amrani
M
M
Faik
A
A
El Otmany
D000328:Adult; D003456:Cryptorchidism / Q000150:complications*; D058490:Disorder of Sex Development, 46,XY / Q000150:complications; D006801:Humans; D008297:Male; D013736:Testicular Neoplasms / Q000150:complications*