Severe headache complicated by vertical atlantoaxial subluxation in diffuse systemic sclerosis with crowned dens pattern calcification.
We report a 34-year-old female case of diffuse systemic sclerosis (SSc) with generalized ectopic calcification, who developed severe headache with vertical atlantoaxial subluxation (AAS) complicated by calcification around the odontoid process (crowned dens pattern calcification). Although a rare complication, AAS should be considered as a differential diagnosis of severe headache in SSc patients with extensive calcification.
Department of Rheumatology, Tokyo Medical University Hospital, Tokyo, Japan.
Aki
A
Shoji
Koichiro
K
Tahara
Haeru
H
Hayashi
Soichiro
S
Tsuji
Eri
E
Kimura
Kengo
K
Yamamoto
Masato
M
Odawara
Tetsuji
T
Sawada
D000328:Adult; D001268:Atlanto-Axial Joint / Q000000981:diagnostic imaging* / Q000293:injuries; D002114:Calcinosis / Q000000981:diagnostic imaging; D002574:Cervical Vertebrae / Q000000981:diagnostic imaging / Q000601:surgery; D005260:Female; D006261:Headache / Q000000981:diagnostic imaging* / Q000209:etiology; D006801:Humans; D004204:Joint Dislocations / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000209:etiology; D008171:Lung Diseases / Q000000981:diagnostic imaging; D009809:Odontoid Process / Q000000981:diagnostic imaging* / Q000601:surgery; D011859:Radiography; D045743:Scleroderma, Diffuse / Q000150:complications / Q000000981:diagnostic imaging*; D012720:Severity of Illness Index; D014143:Traction; D016896:Treatment Outcome