Primary hypertrophic osteoarthropathy.
Pachydermoperiostosis PDP (idiopathic or primary hypertrophic osteoarthropathy) is a rare congenital disease that inherited in an autosomal fashion. The disease is more common in males and develops gradually from adulthood. The disease is characterized by coarse facial features, clubbing of the fingers and radiographic periostitis of the distal long bones. The patient was a 37-year-old man with acroosteolysis and digital clubbing of hands and feet fingers and lion facies.
F. Sodagari University of Medical Sciences and Health Care Services, Tehran, Iran. hpoormoghim@iums.ac.ir
Hadi
H
Poormoghim
Aref
A
Hosseynian
Aryan
A
Javadi
D000172:Acromegaly / Q000175:diagnosis; D000328:Adult; D003937:Diagnosis, Differential; D019066:Facies; D006801:Humans; D008297:Male; D010000:Osteitis / Q000150:complications / Q000473:pathology; D010004:Osteoarthropathy, Primary Hypertrophic / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging; D010005:Osteoarthropathy, Secondary Hypertrophic / Q000150:complications / Q000175:diagnosis / Q000473:pathology; D010014:Osteolysis / Q000150:complications / Q000473:pathology; D011859:Radiography; D013587:Syphilis / Q000150:complications / Q000175:diagnosis