Complete atrioventricular block and reversible systolic dysfunction in left ventricular hypertrabeculation/non-compaction with metabolic myopathy.
A 32-year-old female patient presented with cardiac failure because of systolic dysfunction. Five years before, a DDD pacemaker had been implanted because of complete atrioventricular block. Echocardiographic examination disclosed left ventricular hypertrabeculation/non-compaction. Because of sinus tachycardia, ivabradine was started and the patient's left ventricular function returned to normal within 4 months. Recurrent creatine-kinase elevation and reduced nicotinamide adenine dinucleotide staining on muscle biopsy suggested metabolic myopathy.
Medical Department, Krankenanstalt Rudolfstiftung, Juchgasse, Wien, Österreich. claudia.stöllberger@chello.at
Claudia
C
Stöllberger
Josef
J
Finsterer
Gottfried H
GH
Sodeck
Franz
F
Weidinger
D000328:Adult; D054537:Atrioventricular Block / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D001706:Biopsy; D003937:Diagnosis, Differential; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D015637:Gated Blood-Pool Imaging; D006330:Heart Defects, Congenital / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D024821:Metabolic Syndrome / Q000150:complications* / Q000175:diagnosis; D018908:Muscle Weakness / Q000150:complications* / Q000175:diagnosis; D009200:Myocardial Contraction / Q000502:physiology*; D013599:Systole; D018487:Ventricular Dysfunction, Left / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology