Case report: Clinical, histological and ultrastructural characterization of type II dentinogenesis imperfecta.
BACKGROUND
Type II dentinogenesis imperfecta (DGIII) is an autosomal dominant dental development anomaly that affects both the primary and permanent dentition.


METHODS
This case report describes the clinical, radiographic and morphological characteristics of the teeth of a seven-year-old child with DGI-II determined by optical microscopy and scanning electron microscopy.


METHODS
This consisted of extraction of the primary teeth with periapical lesions due to the advanced state of tooth resorption. Aesthetic restorations were performed on the mandibular anterior teeth and occlusal fissure sealants were applied to erupting teeth. A removable partial upper denture was made in order to return anterior aesthetic function and to aid mastication and speech.


RESULTS
The child was examined at 3 month intervals. Over the following 3 years the prosthesis was replaced due to facial growth and fluoride was applied at each follow-up visit to all teeth. The patient remains in follow up and management.


CONCLUSIONS
Individuals with DGI-II must not neglect their dental health. Early diagnosis, professional advice and treatment with periodic follow-up can help improve the quality of life of such patients.
Department of Paediatric Dentistry, Dental School, UFVJM, Brazil.
C T
CT
Leal
L D
LD
Martins
F D
FD
Verli
M A L
MA
de Souza
M L
ML
Ramos-Jorge
D002648:Child; D003481:Cuspid / Q000002:abnormalities; D003743:Dental Enamel / Q000473:pathology / Q000648:ultrastructure; D003804:Dentin / Q000473:pathology / Q000648:ultrastructure; D003811:Dentinogenesis Imperfecta / Q000145:classification* / Q000473:pathology; D003779:Denture Design; D003832:Denture, Partial, Removable; D005500:Follow-Up Studies; D006801:Humans; D007180:Incisor / Q000002:abnormalities; D008297:Male; D008855:Microscopy, Electron, Scanning; D010483:Periapical Diseases / Q000628:therapy; D014081:Tooth Extraction; D014091:Tooth Resorption / Q000628:therapy; D014094:Tooth, Deciduous / Q000002:abnormalities