Neuroendocrine tumor of vulva: a case report and review of literature.
Neuroendocrine tumor (Merkel cell carcinoma-MCC) of the vulva is a very rare entity with less than 15 cases reported in the English literature. It is known for its aggressive behaviour and propensity for early dissemination. The actual cell of origin and etiology of this disease is controversial. In absence of any definite guidelines for management (due to its rarity), extrapolation of data from extra-vulvar MCC seems logical. We present a case of vulvar neuroendocrine tumor who presented at a locally advanced stage.
Department of Surgical Oncology, Amrita Institute of Medical Sciences and Research Centre, Kochi, Kerala, India. sheikhzahoorahmed@aims.amrita.edu
Zahoor A
ZA
Sheikh
Indu
I
Nair
D K
DK
Vijaykumar
Annie
A
Jojo
M
M
Nandeesh
D015266:Carcinoma, Merkel Cell / Q000175:diagnosis* / Q000473:pathology; D018450:Disease Progression; D005260:Female; D006801:Humans; D008875:Middle Aged; D009362:Neoplasm Metastasis; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000473:pathology; D014846:Vulvar Neoplasms / Q000175:diagnosis* / Q000473:pathology