title: Meningioangiomatosis: clinical-radiological features and surgical outcome.
abstract: Meningioangiomatosis (MA) is a rare, benign neoplastic disorder involving the cortex and leptomeninges, the sporadic form, commonly presents as refractory localization-related epilepsy, but could be asymptomatic especially in older patients. The imaging features may be entirely non-specific. Magnetic Resonance Imaging (MRI) erroneously suggests meningioma, lowgrade tumour or vascular malformations. The pathological findings are characterised by proliferation of meningothelial cells and leptomeningeal vessels and calcifications within the mass. Macroscopically there is dense thickening in the underlying cortex, often in a sharply defined area. In this article we report 3 cases of MA, neither of whom had a familiary history or stigmata of Neurofibromatosis (NF). We discuss and place particular emphasis on the clinical presentation and diagnosis imaging, as well as on the outcome. We also review the literature concerning about the aetiology, pathology findings and imaging features of MA.
authors.affiliation: Departments of Neurosurgery, University of Santiago de Compostela, Spain. socrandrea@hotmail.com
authors.forename: A
authors.initials: A
authors.lastname: Arcos
authors.forename: R
authors.initials: R
authors.lastname: Serramito
authors.forename: J M
authors.initials: JM
authors.lastname: Santín
authors.forename: A
authors.initials: A
authors.lastname: Prieto
authors.forename: M
authors.initials: M
authors.lastname: Gelabert
authors.forename: X
authors.initials: X
authors.lastname: Rodriguez-Osorio
authors.forename: R
authors.initials: R
authors.lastname: Reyes
mesh_terms: D000798:Angiomatosis / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D002540:Cerebral Cortex / Q000000981:diagnostic imaging / Q000473:pathology; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D008577:Meningeal Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D008875:Middle Aged; D011859:Radiography; D016896:Treatment Outcome; D055815:Young Adult