title: Cutaneous Rosai-Dorfman disease: a case report.
abstract: Rosai-Dorfman disease, otherwise known as sinus histiocytosis with massive lymphadenopathy, is a non-Langerhans cell histiocytosis with a benign course and unknown etiology. It was described in 1969 as a painless cervical lymph node enlargement in association with fever, weight loss and sweating. Extranodal disease has been reported in 43% of cases, with involvement of multiple organs. Purely extranodal Rosai-Dorfman disease has been already reported, including forms restricted to the skin. This paper reports a case of purely cutaneous Rosai-Dorfman disease, which is of interest in view of the rarity of this condition.
authors.affiliation: Alfredo da Matta Foundation, Manaus, AM, Brazil.
authors.forename: Josie da Costa
authors.initials: Jda C
authors.lastname: Eiras
authors.forename: Antônio Pedro Mendes
authors.initials: AP
authors.lastname: Schettini
authors.forename: Livia Lima de
authors.initials: LL
authors.lastname: Lima
authors.forename: Liana Hortência Miranda
authors.initials: LH
authors.lastname: Tubilla
authors.forename: Rosa Maria Libório de
authors.initials: RM
authors.lastname: Oliveira
mesh_terms: D000328:Adult; D001706:Biopsy; D005260:Female; D015618:Histiocytosis, Sinus / Q000473:pathology* / Q000601:surgery; D006801:Humans; D007150:Immunohistochemistry; D012867:Skin / Q000473:pathology