title: [Tumour of the endolymphatic sac in a 12-year-old child].
abstract: We present the case of a 12-year-old boy with right-sided pantonal sensorineural hearing loss. With the help of imaging diagnostics a tumour of the right temporal bone was detected. It was resected using a transmastoid approach. Histopathological study showed a low-grade adenocarcinoma of the endolymphatic sac, known as Heffner tumour. An association with the von-Hippel-Lindau complex - as often reported in the medical literature - could not be proven.
authors.affiliation: HNO-Klinik, Universität Regensburg, Franz-Josef-Strauss-Allee 11, 93053, Regensburg, Deutschland.
authors.forename: V
authors.initials: V
authors.lastname: Vielsmeier
authors.forename: P
authors.initials: P
authors.lastname: Kwok
authors.forename: M
authors.initials: M
authors.lastname: Jakob
authors.forename: C
authors.initials: C
authors.lastname: Vogel
authors.forename: J
authors.initials: J
authors.lastname: Strutz
authors.forename: M
authors.initials: M
authors.lastname: Huber
mesh_terms: D000230:Adenocarcinoma / Q000150:complications / Q000175:diagnosis* / Q000601:surgery*; D002648:Child; D004428:Ear Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000601:surgery*; D004712:Endolymphatic Sac / Q000473:pathology* / Q000601:surgery*; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology / Q000517:prevention & control*; D006801:Humans; D008297:Male