title: Primary cerebellopontine angle craniopharyngioma in a patient with Gardner syndrome.
abstract: Craniopharyngiomas usually involve the sella and suprasellar space. Ectopic craniopharyngiomas have rarely been reported at the cerebellopontine angle (CPA). We report a rare primary craniopharyngioma of the CPA without extension into the sellar region. The lesion was initially detected by MRI during investigation of multiple scalp fibromas. Multiple osteomas of the skull and face were detected 2years later, and colonic adenomatous polyposis was detected 4years later; typical features of Gardner syndrome. This is the third report of a primary CPA craniopharyngioma in a patient with Gardner syndrome.
authors.affiliation: Second Neurosurgery Department, Dr. Lütfi Kirdar Kartal Education and Research Hospital, Kartal, Istanbul, Turkey.
authors.forename: Mustafa
authors.initials: M
authors.lastname: Bozbuga
authors.forename: Hikmet
authors.initials: H
authors.lastname: Turan Suslu
authors.forename: Tufan
authors.initials: T
authors.lastname: Hicdonmez
authors.forename: Cicek
authors.initials: C
authors.lastname: Bayindir
mesh_terms: D000328:Adult; D002528:Cerebellar Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D002530:Cerebellopontine Angle / Q000473:pathology / Q000601:surgery; D003397:Craniopharyngioma / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D005736:Gardner Syndrome / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D008297:Male; D009361:Neoplasm Invasiveness / Q000175:diagnosis / Q000473:pathology; D009464:Neuroma, Acoustic / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D012888:Skull Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery