title: [Myocardial noncompaction in a patient with kyphoscoliosis].
abstract: Myocardial noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy characterized by excessively protrusive trabeculae and deep trabecular recesses in one or more segments of the ventricle. A 37-year-old male patient with prominent kyphoscoliosis presented with dyspnea. Transthoracic echocardiography showed trabeculations and deep intratrabecular recesses along the ventricular cavity in the apical and lateral segments of the left ventricle. Color Doppler imaging showed blood flow in these recesses. Diameters of the left ventricle and atrium were increased, with global hypokinesis of the left ventricle (ejection fraction 30%). Severe aortic valve stenosis was noted. Pulmonary function test showed moderate restriction. Due to high perioperative mortality, the patient was scheduled to medical treatment.
authors.affiliation: Dr. Siyami Ersek Göğüs Kalp ve Damar Cerrahisi Eğitim ve Araştırma Hastanesi Kardiyoloji Kliniği, İstanbul. yalchinveliyev@gmail.com
authors.forename: Yalçın
authors.initials: Y
authors.lastname: Velibey
authors.forename: Servet
authors.initials: S
authors.lastname: Altay
authors.forename: Mehmet
authors.initials: M
authors.lastname: Eren
authors.forename: Neşe
authors.initials: N
authors.lastname: Cam
mesh_terms: D000328:Adult; D001024:Aortic Valve Stenosis / Q000000981:diagnostic imaging / Q000209:etiology; D009202:Cardiomyopathies / Q000150:complications* / Q000151:congenital* / Q000000981:diagnostic imaging / Q000628:therapy; D004452:Echocardiography; D018618:Echocardiography, Doppler, Color; D006801:Humans; D007738:Kyphosis / Q000150:complications* / Q000151:congenital / Q000000981:diagnostic imaging; D008297:Male; D011859:Radiography; D012129:Respiratory Function Tests; D012600:Scoliosis / Q000150:complications* / Q000151:congenital / Q000000981:diagnostic imaging; D018487:Ventricular Dysfunction, Left / Q000000981:diagnostic imaging / Q000209:etiology