title: An alternative surgical approach for the combined treatment of pectus excavatum and acute aortic dissection type-A in Marfan syndrome.
abstract: Acute aortic dissection type-A (AADA) is a life-threatening condition especially in patients with Marfan syndrome (MFS) simultaneously suffering from severe pectus excavatum (PE). We report on emergency surgery for combined treatment of PE and AADA in a patient with MFS using an alternative approach. It leads to excellent exposure of the dislocated heart and great vessels enabling Bentall procedure followed by funnel chest repair with modified technique of Adkins and Blades. We achieved favorable functional and cosmetic results. Therefore, we conclude the surgical approach presented is feasible for standard treatment of AADA and consecutive repair of PE.
authors.affiliation: Department of Cardiac Surgery, University Hospital Heidelberg, INF 110, D-69120 Heidelberg, Germany.
authors.forename: Simon
authors.initials: S
authors.lastname: Schwill
authors.forename: Klaus
authors.initials: K
authors.lastname: Kallenbach
authors.forename: Carsten J
authors.initials: CJ
authors.lastname: Beller
authors.forename: Matthias
authors.initials: M
authors.lastname: Karck
mesh_terms: D000208:Acute Disease; D000328:Adult; D000784:Aortic Dissection / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D001014:Aortic Aneurysm / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D019917:Blood Vessel Prosthesis Implantation; D005260:Female; D005660:Funnel Chest / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D008382:Marfan Syndrome / Q000150:complications* / Q000000981:diagnostic imaging; D010027:Osteotomy; D012272:Ribs / Q000002:abnormalities / Q000601:surgery*; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome