Lipoid proteinosis of Urbach and Weithe: case report and a brief review of the literature.
Lipoid proteinosis is a rare disorder involving multiple organ systems. The ocular manifestations are usually trivial, but greatly aid in the diagnosis. We describe a patient who presented to us with typical moniliform blepharosis. A brief description of relevance to the ophthalmologist and review of the literature follows.
Aravind Eye Hospital, Madurai, India.
Monal P
MP
Sainani
R
R
Muralidhar
K
K
Parthiban
P
P
Vijayalakshmi
D002114:Calcinosis / Q000000981:diagnostic imaging / Q000209:etiology; D002648:Child; D005141:Eyelid Diseases / Q000209:etiology* / Q000473:pathology / Q000503:physiopathology; D006801:Humans; D008065:Lipoid Proteinosis of Urbach and Wiethe / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D008297:Male; D013702:Temporal Lobe / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D014792:Visual Acuity
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