Circumflex right aortic arch with associated hypoplasia and coarctation: repair by aortic arch advancement and end-to-side anastomosis.
Right aortic arch with associated arch hypoplasia, coarctation, and an aberrant isolated left subclavian artery is a very uncommon variant of vascular rings, which itself accounts for fewer than 1% of all congenital cardiac defects. Several cases have been reported, and most commonly, extraanatomic grafts have been used for repair. We present a unique technique that involves the resection of the circumflex arch, aortic arch advancement, and end-to-side anastomosis to repair this rare aortic arch malformation.
Congenital Heart Surgery, Texas Children's Hospital, Houston, Texas.
Craig A
CA
Bleakney
Farhan
F
Zafar
Charles D
CD
Fraser
D000015:Abnormalities, Multiple / Q000601:surgery*; D000714:Anastomosis, Surgical / Q000379:methods; D000792:Angiography; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D001017:Aortic Coarctation / Q000175:diagnosis / Q000601:surgery*; D002675:Child, Preschool; D004452:Echocardiography; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D056346:Sternotomy; D025321:Surgery, Computer-Assisted / Q000379:methods; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome