title: Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder.
abstract: BACKGROUND
  Retroperitoneal fibrosis is a fibroinflammatory disease of unknown etiology that can be associated with other fibroinflammatory disorders. Lately, there have been several reports showing that retroperitoneal fibrosis is a manifestation of IgG4-related sclerosing disease, which often presents as autoimmune pancreatitis.
  
  
  METHODS
  This report shows the case of IgG4-related sclerosing cholangitis associated with retroperitoneal fibrosis independent of autoimmune pancreatitis. The patient presented with cholestatic jaundice and picture of sclerosing cholangitis in endoscopic retrograde cholangiography. The combination of endoscopic biliary drainage and steroid therapy was an effective treatment in this case.
  
  
  CONCLUSIONS
  The diagnosis of IgG4-related sclerosing disease should always be taken into consideration in patients with sclerosing cholangitis, especially when it is associated with any fibroinflammatory disorder.
authors.affiliation: Department of Gastroenterology and Hepatology, Medical University of Gdansk, ul. Debinki 7, 80-211 Gdansk, Poland.
authors.forename: Grazyna T
authors.initials: GT
authors.lastname: Rompa
authors.forename: Anna K
authors.initials: AK
authors.lastname: Jablonska
authors.forename: Marek T
authors.initials: MT
authors.lastname: Guzek
authors.forename: Michal M
authors.initials: MM
authors.lastname: Dubowik
authors.forename: Iwona E
authors.initials: IE
authors.lastname: Marek
authors.forename: Marian K
authors.initials: MK
authors.lastname: Smoczynski