title: [Isolated non-compaction of the right ventricular myocardium: two cases report].
abstract: BACKGROUND
  The noncompaction of myocardium is a rare myocardiopathy. The isolated right ventricular involvement is exceptional. We report two cases of isolated noncompaction of the right ventricular myocardium. CASE 1: I., 2 years old, investigated for a congenital cyanosis with severe functional repercussion. Her echocardiography revealed a complex congenital heart disease associated with isolate noncompaction of the right ventricle. CASE 2: A., 5 years old, was referred for history of syncope for the 2 last years. The echocardiography showed a severe pulmonary hypertension and an isolate noncompaction of the right ventricle.
  
  
  CONCLUSIONS
  Due to the rarity of the isolate non-compaction of the right ventricle, it diagnosis remains difficult. The treatment and the outcomes of this disease are still unclear. An early diagnosis may help to reduce its complication.
authors.affiliation: Équipe de recherche pour l'enfance, la santé et le développement, faculté de médecine et de pharmacie de Marrakech, CHU Mohamed VI, Marrakech, Maroc. lahmiti@gmail.com
authors.forename: S
authors.initials: S
authors.lastname: Lahmiti
authors.forename: A
authors.initials: A
authors.lastname: Aboussad
mesh_terms: D009202:Cardiomyopathies / Q000150:complications / Q000000981:diagnostic imaging; D002675:Child, Preschool; D003490:Cyanosis / Q000209:etiology; D003937:Diagnosis, Differential; D042241:Early Diagnosis; D004452:Echocardiography; D006330:Heart Defects, Congenital / Q000150:complications / Q000000981:diagnostic imaging; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications / Q000000981:diagnostic imaging*; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000150:complications / Q000000981:diagnostic imaging; D008297:Male; D011379:Prognosis; D013575:Syncope / Q000209:etiology