title: Management of monophasic synovial sarcoma of the small intestine.
abstract: BACKGROUND
  Reports of primary intraabdominal synovial sarcomas are extremely rare.
  
  
  METHODS
  A literature review using PubMed was performed. A retrospective review of the one known case at our institution was completed.
  
  
  RESULTS
  Even the most experienced pathologists report that synovial sarcomas can be very difficult to diagnose correctly. One cytogenic abnormality that is common (> 90%) and pathognomonic for synovial sarcoma is a characteristic chromosomal translocation resulting in the SYT/SSX fusion gene. Wide regional excision has been performed for intraabdominal sarcoma, with improved results. Our patient is more than 24 months with no evidence of recurrent or metastatic disease.
  
  
  CONCLUSIONS
  The prognosis for patients with intraabdominal synovial sarcoma remains poor. However, wide regional excision may allow for prolonged disease-free survival.
authors.affiliation: Departments of Surgery and Pathology, Tulane University School of Medicine, New Orleans, Louisiana, USA.
authors.forename: Calvin
authors.initials: C
authors.lastname: Eriksen
authors.forename: Lance
authors.initials: L
authors.lastname: Burns
authors.forename: Angela
authors.initials: A
authors.lastname: Bohlke
authors.forename: Salima
authors.initials: S
authors.lastname: Haque
authors.forename: Douglas P
authors.initials: DP
authors.lastname: Slakey
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007078:Ileal Neoplasms / Q000175:diagnosis / Q000601:surgery*; D010535:Laparoscopy / Q000379:methods*; D013584:Sarcoma, Synovial / Q000175:diagnosis / Q000601:surgery*; D014057:Tomography, X-Ray Computed