title: [Desmoid tumor of the breast in a 9 years old little girl].
abstract: Aggressive fibromatosis (desmoid tumour) of the breast is a rare tumour that accounts only for 0.2% of primary breast tumours. This is a benign mesenchymal tumour that develops from muscular fasciae and aponeuroses. It is characterized by its local evolution and its tendency to relapse without metastasizing. Wide radical resection should be attempted whenever possible. Positive margins at resection and reoperation are associated with a high risk of local recurrence. The role of radiotherapy and of medical treatments- especially anti-estrogens - remains unclear. We report here the case of desmoid tumour of the breast arising in a 9-year-old little girl.
authors.affiliation: Service de gynécologie-obstétrique, hôpital Morvan, CHU de Brest, France. matthieu.muller@chu-brest.fr
authors.forename: Matthieu
authors.initials: M
authors.lastname: Muller
authors.forename: Philippe
authors.initials: P
authors.lastname: Dessogne
authors.forename: Marc
authors.initials: M
authors.lastname: Baron
authors.forename: Jean-Michel
authors.initials: JM
authors.lastname: Picquenot
authors.forename: Céline
authors.initials: C
authors.lastname: Riopel
authors.forename: Brigitte
authors.initials: B
authors.lastname: Diologent
authors.forename: Pierre-François
authors.initials: PF
authors.lastname: Dupre
authors.forename: Michel
authors.initials: M
authors.lastname: Collet
mesh_terms: D017668:Age of Onset; D001943:Breast Neoplasms / Q000737:chemistry / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology* / Q000601:surgery; D002277:Carcinoma / Q000175:diagnosis; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D018222:Desmoid Tumors / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D015412:Mastectomy, Segmental; D008572:Menarche; D009363:Neoplasm Proteins / Q000032:analysis; D011379:Prognosis; D011960:Receptors, Estrogen / Q000032:analysis; D011980:Receptors, Progesterone / Q000032:analysis; D012086:Reoperation
chemical_list: D009363:Neoplasm Proteins; D011960:Receptors, Estrogen; D011980:Receptors, Progesterone