title: Evolution of Cellular Inclusions in Bietti's Crystalline Dystrophy.
abstract: Bietti's crystalline dystrophy (BCD) consists of small, yellow-white, glistening intraretinal crystals in the posterior pole, tapetoretinal degeneration with atrophy of the retinal pigment epithelium (RPE) and "sclerosis" of the choroid; in addition, sparking yellow crystals in the superficial marginal cornea are also found in many patients. BCD is inherited as an autosomal-recessive trait (4q35-tel) and usually has its onset in the third decade of life. This review focuses on the ultrastructure of cellular crystals and lipid inclusions of BCD.
authors.affiliation: Immunopathology Section, Laboratory of Immunology, National Eye Institute, National Institutes of Health, Bethesda, MD.
authors.forename: Emiko
authors.initials: E
authors.lastname: Furusato
authors.forename: J Douglas
authors.initials: JD
authors.lastname: Cameron
authors.forename: Chi-Chao
authors.initials: CC
authors.lastname: Chan