title: One and a half ventricular repair as an alternative for hypoplastic right ventricle.
abstract: OBJECTIVE
  Patients with complex congenital heart disease, characterized by right ventricle hypoplasia, had a palliative surgical option with one and a half ventricular repair.
  
  
  METHODS
  From July 2001 to March 2009, nine patients (mean age 5.2 years, range 3 to 9 years) with hypoplastic right ventricle, underwent correction with one and a half ventricle technique. Preoperative diagnoses included: pulmonary atresia with intact ventricular septum, in six and Ebstein's anomaly, in three cases. Six patients had bidirectional cavo-pulmonary shunt (Glenn operation) previously. The surgical approach was performed with cardiopulmonary bypass to correct intracardiac defects: atrial septal defect closure (nine cases); right ventricle outlet tract reconstruction with porcine pulmonary prosthesis (seven cases); tricuspid valvuloplasty (three cases).
  
  
  RESULTS
  There was one (11.1%) hospital death. All the patients left the hospital in good clinical conditions. One patient presented pulmonary stenosis at distal prosthesis anastomosis and needed surgical correction. There was one (12.5%) late deaths after reoperation. At mean follow-up of 39.8 months (range 16 months to 8.4 years) seven patients are alive in functional class I (NYHA).
  
  
  CONCLUSIONS
  Surgical treatment of congenital cardiac anomalies in the presence of a hypoplastic right ventricle by means of one and a half ventricle repair has the advantages of reducing the surgical risk of biventricular repair compared to the Fontan circulation; it maintains a low right atrium pressure, a pulsatile pulmonary blood flow and improves the systemic oxygen saturation with short and medium-term promising results. Longer follow-up is needed to prove the efficacy of such a repair in the long term.
authors.affiliation: miguelmaluf@gmail.com
authors.forename: Miguel Angel
authors.initials: MA
authors.lastname: Maluf
authors.forename: Antonio Carlos
authors.initials: AC
authors.lastname: Carvalho
authors.forename: Werther Brunow
authors.initials: WB
authors.lastname: Carvalho
mesh_terms: D000714:Anastomosis, Surgical / Q000379:methods; D006348:Cardiac Surgical Procedures / Q000009:adverse effects* / Q000379:methods / Q000401:mortality; D002648:Child; D002675:Child, Preschool; D005260:Female; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000473:pathology / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology / Q000601:surgery; D006801:Humans; D008297:Male; D010166:Palliative Care / Q000379:methods*; D016896:Treatment Outcome