title: Newborn with persistent cloaca presenting with accessory phallic urethra and ambiguous genitalia.
abstract: Persistent cloaca is a rare urogenital anomaly that can pose significant challenges for adequate diagnosis and management. We describe the case of an infant girl with a cloacal malformation, having a single perineal orifice and an accessory phallic urethra, who presented with ambiguous genitalia at birth. The distal part of the accessory phallic urethra was used to create a mucosa-lined vestibule as a part of the total urogenital sinus mobilization. This technical maneuver allowed a more natural looking, and possibly functioning, vaginal introitus, improving the final cosmetic result.
authors.affiliation: Division of Pediatric Urology, McMaster Children's Hospital, McMaster University, Hamilton, Ontario, Canada. lhpbraga@gmail.com
authors.forename: Luis H P
authors.initials: LH
authors.lastname: Braga
authors.forename: Kaitlyn
authors.initials: K
authors.lastname: Whelan
authors.forename: Jorge
authors.initials: J
authors.lastname: DeMaria
authors.forename: Joao L
authors.initials: JL
authors.lastname: Pippi-Salle
mesh_terms: D002988:Cloaca / Q000002:abnormalities*; D012734:Disorders of Sex Development / Q000473:pathology / Q000601:surgery*; D005260:Female; D005836:Genitalia, Female / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D019651:Plastic Surgery Procedures / Q000379:methods*; D014521:Urethra / Q000002:abnormalities*; D013519:Urogenital Surgical Procedures