title: Functional total anomalous pulmonary venous drainage by left atrium-to-superior vena cava shunt.
abstract: Total anomalous pulmonary venous connection is occasionally associated with a functional single ventricle and is thought to be a risk for the staged Fontan approach. We report a patient with a very rare presentation of mitral atresia and intact atrial septum with physiologically total anomalous pulmonary venous drainage by a connecting vein between the left atrium and the superior vena cava. A surgical atrioseptectomy as a functional repair of total anomalous pulmonary venous connection and pulmonary artery banding was successfully performed as the first palliation for Fontan completion.
authors.affiliation: Division of Cardiothoracic, Transplantation, and Vascular Surgery, Hannover Medical School, Hannover, Germany. ono.masamichi@mh-hannover.de
authors.forename: Masamichi
authors.initials: M
authors.lastname: Ono
authors.forename: Heidi
authors.initials: H
authors.lastname: Goerler
authors.forename: Harald
authors.initials: H
authors.lastname: Bertram
authors.forename: Thomas
authors.initials: T
authors.lastname: Breymann
mesh_terms: D000714:Anastomosis, Surgical; D006348:Cardiac Surgical Procedures / Q000379:methods*; D002675:Child, Preschool; D005260:Female; D006325:Heart Atria / Q000002:abnormalities* / Q000601:surgery; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000601:surgery