title: The hypoplastic left heart syndrome is not a risk factor for Fontan operation.
abstract: OBJECTIVE
  To show the mortality rate of children undergoing to Fontan operation and determine whether the hypoplastic left heart syndrome (HLHS) is a risk factor for hospital mortality.
  
  
  METHODS
  From August 2001 to June 2008, 76 patients underwent Fontan operation and were divided into two groups: group A with 54 patients, 31 (40.7%) patients with tricuspid atresia and variants, six (7.8%) of double-inlet left ventricle, four (5.3%) and atrioventricular septal defect and total 13 (17.1%) of other complex congenital heart disease and group B all patients with HLHS a total of 22 (28.9%) patients.
  
  
  RESULTS
  Group A patients had a mean age of 6.47 years ± 4.83 and group B of 2.08 years ± 0.24 P <0.001, the average weight was 22.42 ± 11.04 against 12.99 ± 1.2 P = 0.016, the mean CPB time was 119.5 min versus 113.3 min P = 0.0, with a mean clamping time of 74.8 min and 73.5 min p = 0.75. The mean ICU stay was 4.1 days for group A versus 7.52 days for group B p = 0.0003. In total (group A + B) three patients died, with hospital mortality of 3.9%, and one patient with HLHS (4.54%) (P <0.001, 95% CI 0.001 to 0.228).
  
  
  CONCLUSIONS
  Our study shows that despite higher morbidity in HLHS is not a risk factor for hospital mortality.
authors.affiliation: arturhso@hotmail.com
authors.forename: Artur Henrique de
authors.initials: AH
authors.lastname: Souza
authors.forename: Luciana da
authors.initials: Ld
authors.lastname: Fonseca
authors.forename: Sônia Meiken
authors.initials: SM
authors.lastname: Franchi
authors.forename: Alessandro Cavalcante
authors.initials: AC
authors.lastname: Lianza
authors.forename: José Francisco
authors.initials: JF
authors.lastname: Baumgratz
authors.forename: José Pedro da
authors.initials: JP
authors.lastname: Silva
mesh_terms: D002648:Child; D002675:Child, Preschool; D005260:Female; D018729:Fontan Procedure / Q000401:mortality*; D006330:Heart Defects, Congenital / Q000150:complications; D017052:Hospital Mortality; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000150:complications* / Q000401:mortality; D008297:Male; D012307:Risk Factors