title: Generalised lymphangiomatosis in an 8-year-old girl who presented with cardiomegaly.
abstract: Generalised lymphangiomatosis is a rare disease that is characterized by widespread bony and soft tissue involvement of lymphangioma. Radiological evaluation is crucial because the site and extent of the lymphangioma are important prognostic factors. The computed tomography, ultrasonography and magnetic resonance images showed sharply defined, non-enhanced cystic lesions involving the mediastinum, bones, spleen, lung, and lower neck. We report here a case that was referred to us for investigation of marked cardiomegaly.
authors.affiliation: Department of Pediatric Cardiology, Istanbul University, Istanbul, Turkey.
authors.forename: Funda
authors.initials: F
authors.lastname: Oztunç
authors.forename: Bülent
authors.initials: B
authors.lastname: Koca
authors.forename: Ibrahim
authors.initials: I
authors.lastname: Adaletli
mesh_terms: D001707:Biopsy, Needle; D001761:Bleomycin / Q000627:therapeutic use; D006332:Cardiomegaly / Q000175:diagnosis* / Q000209:etiology; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D006338:Heart Neoplasms / Q000175:diagnosis* / Q000188:drug therapy; D006801:Humans; D007150:Immunohistochemistry; D008202:Lymphangioma / Q000175:diagnosis* / Q000188:drug therapy; D008279:Magnetic Resonance Imaging / Q000379:methods; D009361:Neoplasm Invasiveness / Q000473:pathology; D009367:Neoplasm Staging; D010166:Palliative Care / Q000379:methods*; D035583:Rare Diseases; D018570:Risk Assessment; D012720:Severity of Illness Index
chemical_list: D001761:Bleomycin