title: Hypoplastic left heart syndrome with restrictive atrial septum and advanced heart block documented with a novel fetal electrocardiographic monitor.
abstract: Hypoplastic left ventricle with congenital heart block has been reported previously in a fetus with concurrent left atrial isomerism and levo-transposition of the great arteries. We present the unusual case of an infant diagnosed in utero with hypoplastic left heart syndrome, a restrictive atrial septum and advanced heart block but with D-looping of the ventricles and no atrial isomerism. In addition, fetal heart rhythm was documented with the assistance of a new fetal electrocardiographic monitor.
authors.affiliation: Department of Pediatrics, Division of Pediatric Cardiology, Columbia University Medical Center, New York, NY 10032, USA.
authors.forename: H K
authors.initials: HK
authors.lastname: Narayan
authors.forename: W
authors.initials: W
authors.lastname: Fifer
authors.forename: S
authors.initials: S
authors.lastname: Carroll
authors.forename: J
authors.initials: J
authors.lastname: Kern
authors.forename: E
authors.initials: E
authors.lastname: Silver
authors.forename: I A
authors.initials: IA
authors.lastname: Williams
mesh_terms: D000328:Adult; D054087:Atrial Septum / Q000196:embryology / Q000503:physiopathology*; D004562:Electrocardiography / Q000295:instrumentation*; D017809:Fatal Outcome; D005260:Female; D006327:Heart Block / Q000151:congenital* / Q000175:diagnosis / Q000196:embryology / Q000601:surgery; D006344:Heart Septal Defects, Atrial / Q000175:diagnosis* / Q000196:embryology / Q000601:surgery; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis* / Q000196:embryology / Q000503:physiopathology / Q000601:surgery; D011247:Pregnancy