title: Tricuspid atresia with absent pulmonary valve and intact ventricular septum: a rare association.
abstract: The absence of the pulmonary valve in connection with tricuspid atresia and intact ventricular septum is a rare malformation, associated with a poor prognosis. The right ventricle is severely hypertrophied, resembling a cardiac mass protruding into the left ventricular outflow tract. We report such a case that underwent successful palliation with a Blalock-Taussig shunt followed by a superior cavopulmonary anastomosis.
authors.affiliation: Division of Pediatric Cardiology, Arkansas Children's Hospital and University of Arkansas for Medical Sciences, Little Rock, AR, USA. bestthomash@uams.edu
authors.forename: Thomas H
authors.initials: TH
authors.lastname: Best
authors.forename: Himesh V
authors.initials: HV
authors.lastname: Vyas
authors.forename: Robert D B
authors.initials: RD
authors.lastname: Jaquiss
authors.forename: Ritu
authors.initials: R
authors.lastname: Sachdeva
mesh_terms: D000015:Abnormalities, Multiple; D058366:Blalock-Taussig Procedure; D015150:Echocardiography, Doppler; D019560:Echocardiography, Three-Dimensional; D018610:Heart Bypass, Right; D006801:Humans; D017380:Hypertrophy, Right Ventricular / Q000175:diagnosis / Q000209:etiology; D007231:Infant, Newborn; D008297:Male; D010166:Palliative Care; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D016896:Treatment Outcome; D018785:Tricuspid Atresia / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D054088:Ventricular Septum