title: Anesthetic experience of a patient with Ohtahara syndrome -A case report-.
abstract: Ohtahara syndrome (OS) is a rare epileptic encephalopathy that is characterized by an abnormal electroencephalogram (EEG) and intractable seizures in the neonatal and early infantile period. The patient of this reported case was delivered normally at 39 weeks of gestation without any complication. One week after birth, seizures that were refractory to anticonvulsants started with repetitive clustered tonic spasms. The child had no abnormal findings on the initial laboratory investigations. But he was diagnosed with OS according to the frequent tonic spasms, an abnormal EEG pattern of suppression-burst and magnetic resonance imaging of cortical dysplasia. He was planned to undergo an operation for brain lesion. This report describes our experience with the general anesthetic management when we performed craniotomy and right hemispherotomy for a patient with OS.
authors.affiliation: Department of Anesthesiology and Pain Medicine, Hallym University College of Medicine, Chuncheon, Korea.
authors.forename: Eun Mi
authors.initials: EM
authors.lastname: Choi
authors.forename: Kyeong Tae
authors.initials: KT
authors.lastname: Min
authors.forename: Jin Sun
authors.initials: JS
authors.lastname: Cho
authors.forename: Seung Ho
authors.initials: SH
authors.lastname: Choi