title: Primary pulmonary artery sarcoma extending retrograde into the superior vena cava.
abstract: Primary pulmonary artery sarcoma is a rare tumor that is highly fatal. It can be misdiagnosed as acute or chronic pulmonary thromboembolic disease. Herein, we report the case of a 22-year-old woman with a preoperative diagnosis of pulmonary embolism and superior vena caval thrombosis. Intraoperatively, an extensive sarcoma was seen to extend retrograde from the pulmonary artery, past the right ventricle and right atrium, and into the superior vena cava. Surgical resection of the tumor and reconstruction of the central pulmonary arteries, followed by adjuvant chemotherapy, relieved the clinical symptoms. The patient remained free of cancer at 14 months postoperatively. We believe that this is the 1st report of a primary pulmonary artery sarcoma that extended retrograde into the superior vena cava.
authors.affiliation: Departments of Internal Medicine, Hospital General Ciudad Real, 10034 Ciudad Real, Spain.
authors.forename: José
authors.initials: J
authors.lastname: Portillo-Sanchez
authors.forename: Yasser
authors.initials: Y
authors.lastname: Hessein-Abdou
authors.forename: Eugenio
authors.initials: E
authors.lastname: Puga-Alcalde
authors.forename: Maria Angeles
authors.initials: MA
authors.lastname: Perez-Martinez
authors.forename: Maria
authors.initials: M
authors.lastname: Del Carmen Jimenez-Meneses
authors.forename: Agustín
authors.initials: A
authors.lastname: Camacho-Pedrero
authors.forename: Luís Ruíz
authors.initials: LR
authors.lastname: Valdepeñas-Herrero
mesh_terms: D006348:Cardiac Surgical Procedures; D017024:Chemotherapy, Adjuvant; D003951:Diagnostic Errors; D015150:Echocardiography, Doppler; D017548:Echocardiography, Transesophageal; D005260:Female; D006801:Humans; D009361:Neoplasm Invasiveness; D011651:Pulmonary Artery / Q000473:pathology* / Q000601:surgery; D011655:Pulmonary Embolism / Q000175:diagnosis; D012509:Sarcoma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D013479:Superior Vena Cava Syndrome / Q000175:diagnosis* / Q000209:etiology / Q000628:therapy; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D019043:Vascular Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D014656:Vascular Surgical Procedures; D014683:Vena Cava, Superior / Q000473:pathology* / Q000601:surgery; D055815:Young Adult