title: Mondini malformation associated with diastematomyelia and presenting with recurrent meningitis.
abstract: The authors report the case of 5-year-old girl who presented with 4 episodes of recurrent meningitis. Her initial workup revealed a lumbosacral dermoid sinus associated with diastematomyelia and a tethered cord. Therefore, a surgical repair to correct the anomaly was performed. However, another episode of meningitis occurred after surgery, and a subsequent temporal bone scan revealed the presence of left Mondini dysplasia. To the authors' knowledge, this is the first report of Mondini dysplasia in association with diastematomyelia.
authors.affiliation: Department of Pediatrics, Division of Child Neurology, Jordan University Hospital, Amman, Jordan. amasri@ju.edu.jo
authors.forename: Amira
authors.initials: A
authors.lastname: Masri
authors.forename: Faris G
authors.initials: FG
authors.lastname: Bakri
authors.forename: Ralf
authors.initials: R
authors.lastname: Birkenhäger
authors.forename: Abeer
authors.initials: A
authors.lastname: Alassaf
authors.forename: Awni F
authors.initials: AF
authors.lastname: Musharbash
authors.forename: Azmy
authors.initials: A
authors.lastname: Haroun
authors.forename: Imad
authors.initials: I
authors.lastname: Zak
mesh_terms: D002675:Child, Preschool; D007758:Ear, Inner / Q000002:abnormalities*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000209:etiology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D026901:Membrane Transport Proteins / Q000235:genetics; D008581:Meningitis / Q000150:complications*; D009436:Neural Tube Defects / Q000150:complications*; D000076988:Sulfate Transporters
chemical_list: D026901:Membrane Transport Proteins; C085609:SLC26A4 protein, human; D000076988:Sulfate Transporters