title: The right sided syndrome, congenital absence of kidney and testis.
abstract: Unilateral renal agenesis (URA) is a developmental defect associated with ano-malies of the genitourinary system. The associations vary from absence of testis alone to high anorectal anomalies in other patients. We present two interesting patients with URA, encountered recently. Our first case was diagnosed with URA at the age of 11 years, which was detected on sonography, when he presented with pain abdomen. The presence of an epididymal cyst masked the absence of ipsilateral testes leading to delay in the diagnosis. Our second case was diagnosed with URA during the neonatal period when he presented with anorectal agenesis. He underwent abdomino-anal pull-through operation and later clinical course was complicated by recurrent cystitis, secondary vesicoureteral reflux and hydroureteronephrosis of solitary kidney, progressing to chronic kidney disease.
authors.affiliation: Department of Endocrinology, Medwin Hospitals, Chirag Ali Lane, Nampally, Hyderabad, AP, India. hariendo@rediffmail.com
authors.forename: K V S Hari
authors.initials: KV
authors.lastname: Kumar
authors.forename: B Srinivas
authors.initials: BS
authors.lastname: Rao
authors.forename: Shekhar
authors.initials: S
authors.lastname: Shiradhonkar
authors.forename: Ratan
authors.initials: R
authors.lastname: Jha
authors.forename: Girish
authors.initials: G
authors.lastname: Narayan
authors.forename: K D
authors.initials: KD
authors.lastname: Modi
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D000015:Abnormalities, Multiple; D001006:Anus, Imperforate / Q000150:complications; D002648:Child; D000013:Congenital Abnormalities / Q000000981:diagnostic imaging / Q000628:therapy; D003456:Cryptorchidism / Q000150:complications* / Q000000981:diagnostic imaging / Q000628:therapy; D003556:Cystitis / Q000209:etiology; D018450:Disease Progression; D006801:Humans; D006869:Hydronephrosis / Q000209:etiology; D007231:Infant, Newborn; D007668:Kidney / Q000002:abnormalities / Q000000981:diagnostic imaging; D007674:Kidney Diseases / Q000151:congenital; D008297:Male; D018529:Nutritional Support; D012008:Recurrence; D006435:Renal Dialysis; D013088:Spermatocele / Q000150:complications; D016896:Treatment Outcome; D018608:Ultrasonography, Doppler; D014718:Vesico-Ureteral Reflux / Q000209:etiology