title: An unusual case of heterotaxy and polysplenia syndrome associated with hemiazygous continuation of the left-sided vena cava inferior, dilated azygous vein and large venous ectasia.
abstract: We report a 13-year-old male patient with heterotaxy and polysplenia syndrome associated with hemiazygous continuation of the left-sided vena cava inferior, dilated azygous vein, and large venous ectasia. This is the first report of heterotaxy and polysplenia syndrome associated with this particular venous arrangement.
authors.affiliation: Kartal Koşuyolu Training and Research Heart Hospital, Istanbul. ayildirimmd@yahoo.com
authors.forename: Ayşe
authors.initials: A
authors.lastname: Yildirim
authors.forename: Deniz
authors.initials: D
authors.lastname: Oğuz
authors.forename: Yusuf
authors.initials: Y
authors.lastname: Öner
authors.forename: Rana
authors.initials: R
authors.lastname: Olguntürk
mesh_terms: D000015:Abnormalities, Multiple; D000293:Adolescent; D001401:Azygos Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D003914:Dextrocardia / Q000150:complications* / Q000175:diagnosis; D004108:Dilatation, Pathologic; D040181:Genetic Diseases, X-Linked / Q000150:complications* / Q000175:diagnosis; D059446:Heterotaxy Syndrome; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D010690:Phlebography; D012857:Situs Inversus / Q000150:complications* / Q000175:diagnosis; D054079:Vascular Malformations / Q000150:complications* / Q000175:diagnosis; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology