title: Is celiac artery compression syndrome genetically inherited?: a case series from a family and review of the literature.
abstract: The median arcuate ligament is a tendinous arch joining the two medial borders of the diaphragm crura together. In 13-50% of asymptomatic subjects it is responsible for significant angiographic celiac trunk compression. The significance of median arcuate ligament-associated celiac artery compression has been a source of some controversy in the past literature, and the etiology remains unclear. We report here a case series from a family that was diagnosed by the use of multidetector computed tomography. The observation of this syndrome in a family suggests that the responsible anatomic relationships are congenital and may be genetically inherited.
authors.affiliation: Turkiye Yuksek Ihtisas Training and Research Hospital, Department of Radiology, Kizilay sokak No. 4, 06100 Sihhiye, Ankara, Turkey. sarperokten@yahoo.com
authors.forename: Rıza S
authors.initials: RS
authors.lastname: Okten
authors.forename: Fahrettin
authors.initials: F
authors.lastname: Kucukay
authors.forename: Muharrem
authors.initials: M
authors.lastname: Tola
authors.forename: Birol
authors.initials: B
authors.lastname: Bostanci
authors.forename: Turhan
authors.initials: T
authors.lastname: Cumhur
mesh_terms: D000328:Adult; D001157:Arterial Occlusive Diseases / Q000000981:diagnostic imaging* / Q000235:genetics*; D002445:Celiac Artery / Q000000981:diagnostic imaging* / Q000473:pathology*; D005260:Female; D020022:Genetic Predisposition to Disease; D006801:Humans; D008297:Male; D008875:Middle Aged; D061330:Multidetector Computed Tomography / Q000379:methods*; D011857:Radiographic Image Interpretation, Computer-Assisted; D013577:Syndrome