title: Complete atrioventricular block as the first manifestation of noncompaction of the ventricular myocardium.
abstract: Noncompaction of ventricular myocardium (NVM) is a rare cardiomyopathy, most probably caused by disturbances in embryonic morphogenesis of the myocytes, resulting in prominent trabeculations in the ventricular myocardium. Several diagnostic criteria have been proposed by echocardiography, and its association with other heart diseases is common. Its mortality is closely related to ventricular dysfunction, cardiac arrhythmias, and cardioembolic events. We report here a case of occurrence of atrioventricular block with syncope as the clinical manifestation of NVM. A brief review of the literature on morphological features, diagnosis, prognosis, and treatment will also be discussed.
authors.affiliation: Serviço de Cardiologia e Cirurgia Cardiovascular do Hospital das Clínicas da Universidade Federal de Minas Gerais, Belo Horizonte, Minas Gerais, Brazil. ramosnas@gmail.com
authors.forename: Bruno Ramos
authors.initials: BR
authors.lastname: Nascimento
authors.forename: Daniel Furtado
authors.initials: DF
authors.lastname: Vidigal
authors.forename: Renata
authors.initials: R
authors.lastname: De Carvalho Bicalho Carneiro
authors.forename: Warley Cristiano
authors.initials: WC
authors.lastname: De Souza
authors.forename: Walkiria Monteiro
authors.initials: WM
authors.lastname: Lopes
authors.forename: Antonio Luiz Pinho
authors.initials: AL
authors.lastname: Ribeiro
authors.forename: E Maria
authors.initials: EM
authors.lastname: Do Carmo Pereira Nunes
mesh_terms: D000328:Adult; D054537:Atrioventricular Block / Q000175:diagnosis* / Q000503:physiopathology* / Q000601:surgery; D003937:Diagnosis, Differential; D004452:Echocardiography; D015716:Electrocardiography, Ambulatory; D005260:Female; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis* / Q000503:physiopathology* / Q000601:surgery; D010138:Pacemaker, Artificial