title: Noncompaction cardiomyopathy--a review of eight cases.
abstract: Left ventricular noncompaction is a genetic disorder that is thought to be related to an arrest in endomyocardial development. It is characterized by the presence of a prominent trabecular meshwork and deep recesses. In order to better characterize this recently described disorder, whose prognosis remains unclear, we review eight cases diagnosed at our hospital, describing their clinical, electrocardiographic and echocardiographic features as well as therapy and follow-up. We also discuss the most relevant data from the literature concerning pathogenesis, clinical presentation, diagnostic criteria, therapy and prognosis.
authors.affiliation: Serviço de Cardiologia, Hospital de Santa Marta, Lisboa, Portugal. alexandra_toste@hotmail.com
authors.forename: Alexandra
authors.initials: A
authors.lastname: Toste
authors.forename: Luísa Moura
authors.initials: LM
authors.lastname: Branco
authors.forename: Ana
authors.initials: A
authors.lastname: Galrinho
authors.forename: Ana
authors.initials: A
authors.lastname: Lousinha
authors.forename: António
authors.initials: A
authors.lastname: Fiarresga
authors.forename: Mário M
authors.initials: MM
authors.lastname: Oliveira
authors.forename: João
authors.initials: J
authors.lastname: Abreu
authors.forename: João João
authors.initials: JJ
authors.lastname: Mendes
authors.forename: Lurdes
authors.initials: L
authors.lastname: Ferreira
authors.forename: Ana
authors.initials: A
authors.lastname: Leal
authors.forename: Rui Cruz
authors.initials: RC
authors.lastname: Ferreira
mesh_terms: D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D004562:Electrocardiography; D005260:Female; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis* / Q000000981:diagnostic imaging; D008297:Male; D008875:Middle Aged; D012189:Retrospective Studies; D014463:Ultrasonography